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المؤلفون: Aurélie Tatopoulos, Philippe Reix, Marie Luce Choukroun, Pierre-Régis Burgel, Katia Bessaci-Kabouya, Iulia Ioan, Jennifer Da Silva, Muriel Le Bourgeois, Plamen Bokov, M. Gerardin, Jean-Louis Paillasseur, Stéphanie Bui
المساهمون: Pathologies Pulmonaires et Plasticité Cellulaire - UMR-S 1250 (P3CELL), Université de Reims Champagne-Ardenne (URCA)-Institut National de la Santé et de la Recherche Médicale (INSERM)
المصدر: Journal of Cystic Fibrosis
Journal of Cystic Fibrosis, Elsevier, 2021, ⟨10.1016/j.jcf.2021.06.002⟩مصطلحات موضوعية: 0301 basic medicine, Pulmonary and Respiratory Medicine, Pediatrics, medicine.medical_specialty, Adolescent, Cystic Fibrosis, [SDV]Life Sciences [q-bio], Aminopyridines, Cystic Fibrosis Transmembrane Conductance Regulator, Quinolones, Aminophenols, Cystic fibrosis, Ivacaftor, Cohort Studies, 03 medical and health sciences, chemistry.chemical_compound, 0302 clinical medicine, Daily practice, Medicine, Humans, Benzodioxoles, Young adult, 10. No inequality, Chloride Channel Agonists, ComputingMilieux_MISCELLANEOUS, business.industry, Lumacaftor, medicine.disease, 3. Good health, Respiratory Function Tests, Drug Combinations, 030104 developmental biology, 030228 respiratory system, chemistry, Lung disease, Pediatrics, Perinatology and Child Health, Biomarker (medicine), Observational study, business, medicine.drug
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المؤلفون: Marlène Murris-Espin, Christophe Marguet, Anne Munck, Michel Abely, Harriet Corvol, Philippe Reix, Laurent Mely, Clémence Martin, Tiphaine Biouhee, Julie Macey, Michele Porzio, A. Prevotat, Stéphanie Bui, Dominique Hubert, Isabelle Sermet-Gaudelus, Jennifer Da Silva, Clémence Dehillotte, Isabelle Durieu, Lydie Lemonnier, Raphaël Chiron, Pierre-Régis Burgel, Jean-Louis Paillasseur
المساهمون: Institut Cochin (IC UM3 (UMR 8104 / U1016)), Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS)-Université Paris Cité (UPCité), Hôpital Cochin [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Hospices Civils de Lyon (HCL), Health Service and Performance Research (HESPER), Université Claude Bernard Lyon 1 (UCBL), Université de Lyon-Université de Lyon, Hôpital Arnaud de Villeneuve [CHRU Montpellier], Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier), Université de Montpellier (UM), Hôpital Renée Sabran [CHU - HCL], Hôpital Albert Calmette, Université de Lille, Droit et Santé-Centre Hospitalier Régional Universitaire [Lille] (CHRU Lille), Université de Lille, Centre Hospitalier Universitaire de Toulouse (CHU Toulouse), Fédération de Médecine Translationnelle de Strasbourg (FMTS), Université de Strasbourg (UNISTRA), CHU Strasbourg, American Memorial Hospital (Hôpital des enfants) [Reims], Laboratoire de Biométrie et Biologie Evolutive - UMR 5558 (LBBE), Université de Lyon-Université de Lyon-Institut National de Recherche en Informatique et en Automatique (Inria)-VetAgro Sup - Institut national d'enseignement supérieur et de recherche en alimentation, santé animale, sciences agronomiques et de l'environnement (VAS)-Centre National de la Recherche Scientifique (CNRS), Groupe de Recherche sur les Antimicrobiens et les Micro-Organismes (GRAM 1.0), Université de Rouen Normandie (UNIROUEN), Normandie Université (NU)-Normandie Université (NU), CHU Rouen, Normandie Université (NU), CHU Bordeaux [Bordeaux], CHU Necker - Enfants Malades [AP-HP], Institut Necker Enfants-Malades (INEM - UM 111 (UMR 8253 / U1151)), Mucoviscidose: physiopathologie et phénogénomique [CRSA], Centre de Recherche Saint-Antoine (CRSA), Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU)-Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Sorbonne Université (SU), CHU Trousseau [APHP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP)-Sorbonne Université (SU), Sorbonne Université - Faculté de Médecine (SU FM), Sorbonne Université (SU), CIC Bordeaux, Université Bordeaux Segalen - Bordeaux 2-Institut National de la Santé et de la Recherche Médicale (INSERM), Centre hospitalier universitaire de Nantes (CHU Nantes), Hôpital Robert Debré, Vaincre la Mucoviscidose, Association de lutte contre la Mucoviscidose, EFFI-STAT, Centre Hospitalier Universitaire de Reims (CHU Reims)
المصدر: Journal of Cystic Fibrosis
Journal of Cystic Fibrosis, 2020, 20 (2), pp.220-227. ⟨10.1016/j.jcf.2020.06.012⟩
Journal of Cystic Fibrosis, Elsevier, 2020, ⟨10.1016/j.jcf.2020.06.012⟩مصطلحات موضوعية: 0301 basic medicine, Pulmonary and Respiratory Medicine, Adult, Male, medicine.medical_specialty, Adolescent, Cystic Fibrosis, [SDV]Life Sciences [q-bio], Aminopyridines, Quinolones, Aminophenols, Cystic fibrosis, Ivacaftor, 03 medical and health sciences, chemistry.chemical_compound, 0302 clinical medicine, Internal medicine, medicine, Humans, In patient, Benzodioxoles, Chloride Channel Agonists, Lung function, ComputingMilieux_MISCELLANEOUS, business.industry, Lumacaftor, Authorization, medicine.disease, 3. Good health, Respiratory Function Tests, Drug Combinations, 030104 developmental biology, Cftr mutation, 030228 respiratory system, chemistry, Pediatrics, Perinatology and Child Health, Disease Progression, Female, France, business, medicine.drug
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المؤلفون: Laurianne Coutier, Camille Ohlmann, Catherine Mainguy, M. Perceval, Aurélie Labaste, Philippe Reix, V. Jubin
المصدر: Journal of Cystic Fibrosis. 16:709-712
مصطلحات موضوعية: Male, Pulmonary and Respiratory Medicine, Adolescent, Cystic Fibrosis, Aminopyridines, Quinolones, Aminophenols, Cystic fibrosis, Ivacaftor, 03 medical and health sciences, chemistry.chemical_compound, 0302 clinical medicine, Forced Expiratory Volume, medicine, Humans, Benzodioxoles, 030212 general & internal medicine, Respiratory system, Chloride Channel Agonists, Inhalation, business.industry, Lumacaftor, respiratory system, Airway obstruction, medicine.disease, Respiratory Function Tests, respiratory tract diseases, Drug Combinations, Treatment Outcome, 030228 respiratory system, chemistry, Anesthesia, Pediatrics, Perinatology and Child Health, Salbutamol, Female, Bronchoconstriction, France, Drug Monitoring, Symptom Assessment, medicine.symptom, business, circulatory and respiratory physiology, medicine.drug
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المؤلفون: Philippe Reix, Stéphanie Wanin, Antoine Deschildre, Gabriel Reboux, Véronique Houdouin, Jacques de Blic, Nadia Nathan, Clara Malka-Ruimy
المصدر: Pediatric pulmonologyREFERENCES. 55(1)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Male, medicine.medical_specialty, Adolescent, Lymphocyte, CD4-CD8 Ratio, Lung biopsy, Gastroenterology, Serology, 03 medical and health sciences, 0302 clinical medicine, 030225 pediatrics, Internal medicine, medicine, Humans, Exertion, Child, Lung, medicine.diagnostic_test, business.industry, Interstitial lung disease, medicine.disease, respiratory tract diseases, Respiratory Function Tests, Bronchoalveolar lavage, medicine.anatomical_structure, Dyspnea, 030228 respiratory system, Child, Preschool, Pediatrics, Perinatology and Child Health, Cohort, Female, business, Tomography, X-Ray Computed, Bronchoalveolar Lavage Fluid, Hypersensitivity pneumonitis, Alveolitis, Extrinsic Allergic
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المؤلفون: Diana Bilton, Tacjana Pressler, Isabelle Fajac, John Paul Clancy, Dorota Sands, Predrag Minic, Marco Cipolli, Ivanka Galeva, Amparo Solé, Alexandra L. Quittner, Keith Liu, John P. McGinnis, Gina Eagle, Renu Gupta, Michael W. Konstan, Sabine Renner, Christiane Knoop, Anne Malfroot, Lieven Dupont, Kristine Desager, Frans De Baets, Miroslava Bosheva, Vania Nedkova, Ivan Galabov, Andreas Freitag, Nancy Morrison, Pearce Wilcox, Tanja Pressler, Yves Martinet, Raphael Chiron, Stephan Dominique, Philippe Reix, Anne Prevotat, Isabelle Sermet, Isabelle Durieu, Rainald Fischer, Rudolf Huber, Doris Staab, Uwe Mellies, Wolfgang Sextro, Tobias Welte, Heinrike Wilkens, Urte Sommerwerk, Burkhard Bewig, Ilias Inglezos, Stavros-Eleftherios Doudounakis, Olga Bede, Ferenc Gönczi, Rita Újhelyi, Edward McKone, Paul McNally, Vincenzina Lucidi, Mario La Rosa, Laura Minicucci, Rita Padoan, Giovanna Pisi, Rolando Gagliardini, Carla Colombo, Inez Bronsveld, Ewa Sapiejka, Henryk Mazurek, Grażyna Górnicka, Iwona Stelmach, Halina Batura-Gabryel, Marta Rachel, Jaroslava Orosova, Branko Takac, Anna Feketova, Carmen Martinez, Gloria Garcia Hernandez, Jose Ramon Villa-Asensi, Silvia Gartner, Amparo Sole, Anders Lindblad, Martin Ledson, Joanna Whitehouse, Alan Smyth, Ian Ketchell, Timothy Lee, Gordon MacGregor
المصدر: J Cyst Fibros
مصطلحات موضوعية: 0301 basic medicine, Male, Cystic Fibrosis, Gastroenterology, Cystic fibrosis, 0302 clinical medicine, Surveys and Questionnaires, Tobramycin, education.field_of_study, Inhalation, Symptom Flare Up, 3. Good health, Anti-Bacterial Agents, Respiratory Function Tests, Hospitalization, medicine.anatomical_structure, Treatment Outcome, Amikacin, Pseudomonas aeruginosa, Female, medicine.symptom, Symptom Assessment, medicine.drug, Pulmonary and Respiratory Medicine, Adult, medicine.medical_specialty, Population, Article, 03 medical and health sciences, Internal medicine, Administration, Inhalation, medicine, Humans, Pseudomonas Infections, education, Adverse effect, Lung, Dose-Response Relationship, Drug, business.industry, Sputum, medicine.disease, respiratory tract diseases, 030104 developmental biology, 030228 respiratory system, Pediatrics, Perinatology and Child Health, Liposomes, business
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المؤلفون: Sylvain Roche, Muriel Rabilloud, C. Llerena, Jean Iwaz, Philippe Reix, Raphaele Nove-Josserand, Isabelle Durieu, Emilie Blond, S. Poupon-Bourdy, Martine Laville, Quitterie Reynaud, Sébastien Quétant, Sandrine Touzet
المساهمون: Hospices Civils de Lyon (HCL), Health Service and Performance Research (HESPER), Université Claude Bernard Lyon 1 (UCBL), Université de Lyon-Université de Lyon, Service de Biostatistiques [Lyon], Biostatistiques santé, Département biostatistiques et modélisation pour la santé et l'environnement [LBBE], Laboratoire de Biométrie et Biologie Evolutive - UMR 5558 (LBBE), Université de Lyon-Université de Lyon-Institut National de Recherche en Informatique et en Automatique (Inria)-VetAgro Sup - Institut national d'enseignement supérieur et de recherche en alimentation, santé animale, sciences agronomiques et de l'environnement (VAS)-Centre National de la Recherche Scientifique (CNRS)-Université Claude Bernard Lyon 1 (UCBL), Université de Lyon-Université de Lyon-Institut National de Recherche en Informatique et en Automatique (Inria)-VetAgro Sup - Institut national d'enseignement supérieur et de recherche en alimentation, santé animale, sciences agronomiques et de l'environnement (VAS)-Centre National de la Recherche Scientifique (CNRS)-Laboratoire de Biométrie et Biologie Evolutive - UMR 5558 (LBBE), Université de Lyon-Université de Lyon-Institut National de Recherche en Informatique et en Automatique (Inria)-VetAgro Sup - Institut national d'enseignement supérieur et de recherche en alimentation, santé animale, sciences agronomiques et de l'environnement (VAS)-Centre National de la Recherche Scientifique (CNRS), Pôle Information Médicale Evaluation Recherche (IMER), Cardiovasculaire, métabolisme, diabétologie et nutrition (CarMeN), Institut National de la Recherche Agronomique (INRA)-Université Claude Bernard Lyon 1 (UCBL), Université de Lyon-Université de Lyon-Institut National des Sciences Appliquées de Lyon (INSA Lyon), Université de Lyon-Institut National des Sciences Appliquées (INSA)-Institut National des Sciences Appliquées (INSA)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Hospices Civils de Lyon (HCL), Centre Hospitalier Universitaire [Grenoble] (CHU), Université Grenoble Alpes - UFR Médecine (UGA UFRM), Université Grenoble Alpes (UGA), Hospices Civils de Lyon (HCL)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Institut National des Sciences Appliquées de Lyon (INSA Lyon), Université de Lyon-Institut National des Sciences Appliquées (INSA)-Université de Lyon-Institut National des Sciences Appliquées (INSA)-Université Claude Bernard Lyon 1 (UCBL), Université de Lyon-Institut National de la Recherche Agronomique (INRA), Université Grenoble Alpes [2016-2019] (UGA [2016-2019]), Université de Lyon-Institut National des Sciences Appliquées (INSA)-Institut National des Sciences Appliquées (INSA)-Hospices Civils de Lyon (HCL)-Institut National de la Santé et de la Recherche Médicale (INSERM)
المصدر: Journal of Cystic Fibrosis
Journal of Cystic Fibrosis, Elsevier, 2018, 17 (3), pp.400-406. ⟨10.1016/j.jcf.2017.09.010⟩
Journal of Cystic Fibrosis, 2018, 17 (3), pp.400-406. ⟨10.1016/j.jcf.2017.09.010⟩مصطلحات موضوعية: Adult, Blood Glucose, Male, Pulmonary and Respiratory Medicine, medicine.medical_specialty, Pediatrics, Cystic Fibrosis, medicine.medical_treatment, [SDV]Life Sciences [q-bio], Cystic fibrosis-related diabetes, 030209 endocrinology & metabolism, Cystic fibrosis, Body Mass Index, Pulmonary function testing, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, Diabetes mellitus, Glucose Intolerance, Diabetes Mellitus, medicine, Humans, Respiratory system, Child, Correlation of Data, ComputingMilieux_MISCELLANEOUS, business.industry, Insulin, Glucose Tolerance Test, medicine.disease, Respiratory Function Tests, 3. Good health, Endocrinology, 030228 respiratory system, Pediatrics, Perinatology and Child Health, Disease Progression, Female, France, Abnormality, business, Body mass index
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المؤلفون: Stefan Zielen, Judy Bradley, Cesare Braggion, Katherine O'Neill, H.G.M. Arets, K. De Boeck, Keith G. Brownlee, Diana Bilton, Katie J Bayfield, S. Lever, M. Le Bourgeois, J. A. Innes, Daniela Savi, Isabelle Sermet, Philippe Reix, Jane C. Davies, Lisa Kent, Anders Lindblad
المصدر: Kent, L, Reix, P, Innes, J A, Zielen, S, Le Bourgeois, M, Braggion, C, Lever, S, Arets, H G M, Brownlee, K, Bradley, J M, Bayfield, K, O'Neill, K, Savi, D, Bilton, D, Lindblad, A, Davies, J C, Sermet, I & De Boeck, K 2014, ' Lung clearance index: Evidence for use in clinical trials in cystic fibrosis ', Journal of Cystic Fibrosis, vol. 13, no. 2, pp. 123-138 . https://doi.org/10.1016/j.jcf.2013.09.005
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, medicine.medical_specialty, Cystic Fibrosis, Lung Clearance Index, Severity of Illness Index, Cystic fibrosis, clinimetric properties, lung clearance index, multiple breath washout, outcome measures, surrogate endpoints, Outcome Assessment, Health Care, Clinical endpoint, Humans, Medicine, In patient, Pediatrics, Perinatology, and Child Health, Intensive care medicine, Randomized Controlled Trials as Topic, business.industry, Surrogate endpoint, Outcome measures, Reproducibility of Results, medicine.disease, Respiratory Function Tests, Clinical trial, Breath Tests, Lung disease, Pediatrics, Perinatology and Child Health, Physical therapy, Feasibility Studies, business, Biomarkers
وصف الملف: application/pdf
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المؤلفون: Raphaele Nove-Josserand, Zoe Cavalli, Philippe Reix, Isabelle Durieu, Quitterie Reynaud, Michèle Pérouse de Montclos, Stéphane Durupt, M. Perceval, Gerard Lina, Romain Bricca
المصدر: Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society. 16(5)
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Adult, Male, medicine.medical_specialty, Multivariate analysis, Adolescent, Cystic Fibrosis, Itraconazole, Mycobacterium Infections, Nontuberculous, Mycobacterium abscessus, Cystic fibrosis, 03 medical and health sciences, 0302 clinical medicine, Internal medicine, medicine, Humans, 030212 general & internal medicine, Longitudinal Studies, Respiratory Tract Infections, Univariate analysis, biology, business.industry, Incidence (epidemiology), Incidence, Case-control study, Nontuberculous Mycobacteria, bacterial infections and mycoses, medicine.disease, biology.organism_classification, Respiratory Function Tests, 030228 respiratory system, Case-Control Studies, Pediatrics, Perinatology and Child Health, Immunology, Female, France, Allergic bronchopulmonary aspergillosis, business, medicine.drug
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المؤلفون: Isabelle Sermet, Judy Bradley, Stefan Matecki, Lisa Kent, Stephanie D. Davis, Stefan Zielen, Kris De Boeck, Hubertus G.M. Arets, Philippe Reix, Cesare Braggion, Muriel Le Bourgeois
المساهمون: Physiologie & médecine expérimentale du Cœur et des Muscles [U 1046] (PhyMedExp), Université de Montpellier (UM)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), Centre Hospitalier Régional Universitaire [Montpellier] (CHRU Montpellier), Health and Rehabilitation Sciences Research Institute, University of Ulster, University of Ulster, Newtownabbey, University of Leuven Medical School, University Hospitals KULeuven, CHU Necker - Enfants Malades [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), J.W. Goethe Universität, Institut für Geowissenschaften, Altenhöferallee 1, D-60438 Frankfurt am Main, Germany, Anna Meyer Children's Hospital Florence, University of Florence, University Medical Center [Utrecht], Belfast Health and Social Care Trust, Cystic Fibrosis Pediatric Centre, Indianapolis, Centre de recherche Croissance et signalisation (UMR_S 845), Centre National de la Recherche Scientifique (CNRS)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université Paris Descartes - Paris 5 (UPD5), Université Claude Bernard Lyon 1 (UCBL), Université de Lyon, Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Montpellier (UM)-Centre National de la Recherche Scientifique (CNRS), Università degli Studi di Firenze = University of Florence (UniFI), Université Paris Descartes - Paris 5 (UPD5)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Centre National de la Recherche Scientifique (CNRS), MORNET, Dominique
المصدر: Journal of Cystic Fibrosis, 15(1), 10. Elsevier
Journal of Cystic Fibrosis
Journal of Cystic Fibrosis, Elsevier, 2016, 15 (1), pp.10-20. ⟨10.1016/j.jcf.2015.03.015⟩
Journal of Cystic Fibrosis, 2016, 15 (1), pp.10-20. ⟨10.1016/j.jcf.2015.03.015⟩مصطلحات موضوعية: Pulmonary and Respiratory Medicine, medicine.medical_specialty, Standardization, [SDV]Life Sciences [q-bio], Context (language use), Review, Pediatrics, Cystic fibrosis, Surrogate outcome, 03 medical and health sciences, 0302 clinical medicine, Primary outcome, Clinical trials, Outcome Assessment, Health Care, medicine, Journal Article, Humans, 030212 general & internal medicine, Raised volume rapid thoracic compression, Pediatrics, Perinatology, and Child Health, Societies, Medical, Clinical Trials as Topic, Surrogate endpoint, business.industry, Patient Acuity, Infant, medicine.disease, Perinatology, Respiratory Function Tests, 3. Good health, [SDV] Life Sciences [q-bio], Europe, and Child Health, Natural history, Clinical trial, 030228 respiratory system, Reference values, Pediatrics, Perinatology and Child Health, Physical therapy, business, Infant pulmonary function, Clinimetric properties
وصف الملف: image/pdf; application/pdf
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المصدر: Respiratory Physiology & Neurobiology. 136:13-23
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Physiology, animal diseases, Diaphragm, Blood Pressure, Stimulation, Cardiovascular Physiological Phenomena, Songbirds, Electrocardiography, chemistry.chemical_compound, Heart Rate, Reflex, parasitic diseases, Heart rate, Animals, Medicine, Wakefulness, Analysis of Variance, Nerve Fibers, Unmyelinated, Electromyography, business.industry, Goats, Respiration, General Neuroscience, Laryngeal Nerves, Water, Antipruritics, Carbon Dioxide, respiratory system, Respiratory Function Tests, Diaphragm (structural system), Blockade, Laryngeal inlet, Menthol, Blood pressure, Animals, Newborn, chemistry, Capsaicin, Anesthesia, business