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21دورية أكاديمية
المؤلفون: Guffon N; Reference Centre of Inherited Metabolic Diseases, CERLYMM, HCL, Lyon, France., Konstantopoulou V; Department of Pediatrics and Adolescent Medicine, Medical University of Vienna, Vienna, Austria., Hennermann JB; Center for Pediatric and Adolescent Medicine, Villa Metabolica, University Medical Center Mainz, Mainz, Germany., Muschol N; Department of Pediatrics, International Center for Lysosomal Disorders (ICLD), University Medical Center Hamburg-Eppendorf, Hamburg, Germany., Bruno I; Institute for Maternal and Child Health-IRCCS Burlo Garofolo, Trieste, Italy., Tummolo A; Department of Metabolic Diseases and Clinical Genetics, Bari, Italy., Ceravolo F; Chiesi Farmaceutici, Parma, Italy., Zardi G; CROS NT S.r.l, Verona, Italy., Ballabeni A; Chiesi Farmaceutici, Parma, Italy., Lund A; Centre for Inherited Metabolic Diseases, Department of Paediatrics and Adolescent Medicine and Department of Clinical Genetics, Copenhagen University Hospital, Rigshospitalet, Copenhagen, Denmark.; Department of Clinical Medicine, Faculty of Health and Medical Sciences, University of Copenhagen, Copenhagen, Denmark.
المصدر: Journal of inherited metabolic disease [J Inherit Metab Dis] 2023 Jul; Vol. 46 (4), pp. 705-719. Date of Electronic Publication: 2023 Mar 13.
نوع المنشور: Multicenter Study; Clinical Trial, Phase II; Journal Article
بيانات الدورية: Publisher: Wiley Country of Publication: United States NLM ID: 7910918 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1573-2665 (Electronic) Linking ISSN: 01418955 NLM ISO Abbreviation: J Inherit Metab Dis Subsets: MEDLINE
مواضيع طبية MeSH: alpha-Mannosidosis*, Male ; Adult ; Adolescent ; Humans ; Child ; Child, Preschool ; Quality of Life ; alpha-Mannosidase/adverse effects ; Lysosomes ; Antibodies
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22دورية أكاديمية
المؤلفون: Morales-Quintana L; Multidisciplinary Agroindustry Research Laboratory, Instituto de Ciencias Biomédicas, Facultad de Ciencias de la Salud, Universidad Autónoma de Chile, Talca, Chile. luis.morales@uautonoma.cl., Méndez-Yáñez A; Multidisciplinary Agroindustry Research Laboratory, Instituto de Ciencias Biomédicas, Facultad de Ciencias de la Salud, Universidad Autónoma de Chile, Talca, Chile. angela.mendez@uautonoma.cl.
المصدر: Plant molecular biology [Plant Mol Biol] 2023 Jun; Vol. 112 (3), pp. 107-117. Date of Electronic Publication: 2023 May 13.
نوع المنشور: Journal Article; Review
بيانات الدورية: Publisher: Kluwer Academic Country of Publication: Netherlands NLM ID: 9106343 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1573-5028 (Electronic) Linking ISSN: 01674412 NLM ISO Abbreviation: Plant Mol Biol Subsets: MEDLINE
مواضيع طبية MeSH: Glycoside Hydrolases*/metabolism , Fruit*/metabolism, alpha-Mannosidase/metabolism ; Polysaccharides/metabolism ; Plant Proteins/metabolism ; Cell Wall/metabolism
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23دورية أكاديمية
المؤلفون: Kołaczkowski BM; Department of Science and Environment, Roskilde University, Universitetsvej 1, Building 28, 4000 Roskilde, Denmark., Moroz OV; York Structural Biology Laboratory, Department of Chemistry, University of York, York YO10 5DD, United Kingdom., Blagova E; York Structural Biology Laboratory, Department of Chemistry, University of York, York YO10 5DD, United Kingdom., Davies GJ; York Structural Biology Laboratory, Department of Chemistry, University of York, York YO10 5DD, United Kingdom., Møller MS; Department of Biotechnology and Biomedicine, Technical University of Denmark, Building 224, 2800 Kongens Lyngby, Denmark., Meyer AS; Department of Biotechnology and Biomedicine, Technical University of Denmark, Building 224, 2800 Kongens Lyngby, Denmark., Westh P; Department of Biotechnology and Biomedicine, Technical University of Denmark, Building 224, 2800 Kongens Lyngby, Denmark., Jensen K; Novozymes A/S, Biologiens Vej 2, 2800 Kongens Lyngby, Denmark., Wilson KS; York Structural Biology Laboratory, Department of Chemistry, University of York, York YO10 5DD, United Kingdom., Krogh KBRM; Novozymes A/S, Biologiens Vej 2, 2800 Kongens Lyngby, Denmark.
المصدر: Acta crystallographica. Section D, Structural biology [Acta Crystallogr D Struct Biol] 2023 May 01; Vol. 79 (Pt 5), pp. 387-400. Date of Electronic Publication: 2023 Apr 18.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: John Wiley & Sons Country of Publication: United States NLM ID: 101676043 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2059-7983 (Electronic) Linking ISSN: 20597983 NLM ISO Abbreviation: Acta Crystallogr D Struct Biol Subsets: MEDLINE
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24دورية أكاديمية
المؤلفون: Yan X; Jiangsu Provincial Engineering Laboratory for Biomass Conversion and Process Integration, Huaiyin Institute of Technology, Huaian, 223003, Jiangsu, China., Nie X; Jiangsu Provincial Engineering Laboratory for Biomass Conversion and Process Integration, Huaiyin Institute of Technology, Huaian, 223003, Jiangsu, China., Li Q; Jiangsu Provincial Engineering Laboratory for Biomass Conversion and Process Integration, Huaiyin Institute of Technology, Huaian, 223003, Jiangsu, China., Gao F; Jiangsu Provincial Engineering Laboratory for Biomass Conversion and Process Integration, Huaiyin Institute of Technology, Huaian, 223003, Jiangsu, China., Liu P; Jiangsu Provincial Engineering Laboratory for Biomass Conversion and Process Integration, Huaiyin Institute of Technology, Huaian, 223003, Jiangsu, China., Tan Z; Jiangsu Provincial Engineering Laboratory for Biomass Conversion and Process Integration, Huaiyin Institute of Technology, Huaian, 223003, Jiangsu, China., Shi H; Jiangsu Provincial Engineering Laboratory for Biomass Conversion and Process Integration, Huaiyin Institute of Technology, Huaian, 223003, Jiangsu, China. ilyshihao@163.com.
المصدر: Applied biochemistry and biotechnology [Appl Biochem Biotechnol] 2023 Mar; Vol. 195 (3), pp. 1823-1836. Date of Electronic Publication: 2022 Nov 18.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Humana Press Country of Publication: United States NLM ID: 8208561 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1559-0291 (Electronic) Linking ISSN: 02732289 NLM ISO Abbreviation: Appl Biochem Biotechnol Subsets: MEDLINE
مواضيع طبية MeSH: Bacteria*/metabolism , Mannosidases*/metabolism, alpha-Mannosidase/genetics ; alpha-Mannosidase/chemistry ; Kinetics
SCR Organism: Pseudothermotoga thermarum
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25دورية أكاديمية
المؤلفون: Munteanu CVA; Department of Bioinformatics and Structural Biochemistry, Institute of Biochemistry, Bucharest, Romania., Chirițoiu GN; Department of Molecular Cell Biology, Institute of Biochemistry, Bucharest, Romania., Chirițoiu M; Department of Molecular Cell Biology, Institute of Biochemistry, Bucharest, Romania., Ghenea S; Department of Molecular Cell Biology, Institute of Biochemistry, Bucharest, Romania., Petrescu AJ; Department of Bioinformatics and Structural Biochemistry, Institute of Biochemistry, Bucharest, Romania., Petrescu ŞM; Department of Molecular Cell Biology, Institute of Biochemistry, Bucharest, Romania. Electronic address: stefana.petrescu@biochim.ro.
المصدر: Molecular & cellular proteomics : MCP [Mol Cell Proteomics] 2021; Vol. 20, pp. 100125. Date of Electronic Publication: 2021 Jul 29.
نوع المنشور: Journal Article; Research Support, Non-U.S. Gov't
بيانات الدورية: Publisher: Elsevier Inc. on behalf of American Society for Biochemistry and Molecular Biology Country of Publication: United States NLM ID: 101125647 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1535-9484 (Electronic) Linking ISSN: 15359476 NLM ISO Abbreviation: Mol Cell Proteomics Subsets: MEDLINE
مواضيع طبية MeSH: Endoplasmic Reticulum/*metabolism , Glycoproteins/*metabolism , Melanoma/*metabolism , alpha-Mannosidase/*metabolism, Cell Line, Tumor ; Glycomics ; Glycoproteins/genetics ; Humans ; Melanoma/genetics ; Proteomics ; alpha-Mannosidase/genetics
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26دورية أكاديمية
المؤلفون: Males A; York Structural Biology Laboratory, Department of Chemistry, The University of York, YO10 5DD York, UK. gideon.davies@york.ac.uk., Speciale G, Williams SJ, Davies GJ
المصدر: Organic & biomolecular chemistry [Org Biomol Chem] 2019 Aug 28; Vol. 17 (34), pp. 7863-7869.
نوع المنشور: Journal Article; Research Support, Non-U.S. Gov't
بيانات الدورية: Publisher: Royal Society of Chemistry Country of Publication: England NLM ID: 101154995 Publication Model: Print Cited Medium: Internet ISSN: 1477-0539 (Electronic) Linking ISSN: 14770520 NLM ISO Abbreviation: Org Biomol Chem Subsets: MEDLINE
مواضيع طبية MeSH: Clostridium perfringens/*enzymology , Enzyme Inhibitors/*metabolism , Imidazoles/*metabolism , Mannose/*metabolism , alpha-Mannosidase/*metabolism, Biocatalysis ; Catalytic Domain ; Enzyme Inhibitors/chemistry ; Imidazoles/chemistry ; Mannose/analogs & derivatives ; Molecular Conformation ; Mutation ; Protein Binding ; alpha-Mannosidase/chemistry ; alpha-Mannosidase/genetics
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27دورية أكاديمية
المؤلفون: Wang GY; College of chemistry and environmental science, Hebei University, Baoding 071002, PR China; Key laboratory of medicinal chemistry and molecular diagnosis (Ministry of education), Key laboratory of chemical biology of Hebei province, Baoding 071002, PR China; College of Chemical Engineering & Material, Hebei Key Laboratory of Heterocyclic Compounds, Handan University, Handan 056005, PR China., Wei WT; College of chemistry and environmental science, Hebei University, Baoding 071002, PR China; Key laboratory of medicinal chemistry and molecular diagnosis (Ministry of education), Key laboratory of chemical biology of Hebei province, Baoding 071002, PR China., Rong RX; Key laboratory of medicinal chemistry and molecular diagnosis (Ministry of education), Key laboratory of chemical biology of Hebei province, Baoding 071002, PR China; Department of Immunology, Medical Comprehensive Experimental Center, School of Basic Medical Science, Hebei University, Baoding 071002, PR China., Su SS; College of chemistry and environmental science, Hebei University, Baoding 071002, PR China; Key laboratory of medicinal chemistry and molecular diagnosis (Ministry of education), Key laboratory of chemical biology of Hebei province, Baoding 071002, PR China., Yan DX; Key laboratory of medicinal chemistry and molecular diagnosis (Ministry of education), Key laboratory of chemical biology of Hebei province, Baoding 071002, PR China; Department of Immunology, Medical Comprehensive Experimental Center, School of Basic Medical Science, Hebei University, Baoding 071002, PR China., Yin FQ; College of chemistry and environmental science, Hebei University, Baoding 071002, PR China; Key laboratory of medicinal chemistry and molecular diagnosis (Ministry of education), Key laboratory of chemical biology of Hebei province, Baoding 071002, PR China; College of Chemical Engineering & Material, Hebei Key Laboratory of Heterocyclic Compounds, Handan University, Handan 056005, PR China., Li XL; College of chemistry and environmental science, Hebei University, Baoding 071002, PR China; Key laboratory of medicinal chemistry and molecular diagnosis (Ministry of education), Key laboratory of chemical biology of Hebei province, Baoding 071002, PR China. Electronic address: lixl@hbu.cn., Wang KR; College of chemistry and environmental science, Hebei University, Baoding 071002, PR China; Key laboratory of medicinal chemistry and molecular diagnosis (Ministry of education), Key laboratory of chemical biology of Hebei province, Baoding 071002, PR China. Electronic address: kerangwang@hbu.edu.cn.
المصدر: Bioorganic chemistry [Bioorg Chem] 2023 Mar; Vol. 132, pp. 106373. Date of Electronic Publication: 2023 Jan 13.
نوع المنشور: Journal Article; Research Support, Non-U.S. Gov't
بيانات الدورية: Publisher: Elsevier Country of Publication: United States NLM ID: 1303703 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1090-2120 (Electronic) Linking ISSN: 00452068 NLM ISO Abbreviation: Bioorg Chem Subsets: MEDLINE
مواضيع طبية MeSH: Enzyme Inhibitors*/chemistry , Glycoside Hydrolases*/metabolism, Mice ; Animals ; Naphthalimides/pharmacology ; Fluorescence ; alpha-Mannosidase
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28دورية أكاديمية
المؤلفون: Wang Y; Department of Veterinary Medicine, College of Veterinary Medicine, Northwest A&F University, Yangling, China., Zhang JY; Department of Veterinary Medicine, College of Veterinary Medicine, Northwest A&F University, Yangling, China., Teng JY; Department of Veterinary Medicine, College of Veterinary Medicine, Northwest A&F University, Yangling, China., Xiong HF; Department of Veterinary Medicine, College of Veterinary Medicine, Northwest A&F University, Yangling, China., Li QF; Department of Veterinary Medicine, College of Veterinary Medicine, Northwest A&F University, Yangling, China.
المصدر: The Journal of veterinary medical science [J Vet Med Sci] 2023 Feb 21; Vol. 85 (2), pp. 244-251. Date of Electronic Publication: 2023 Jan 02.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Japanese Society Of Veterinary Science Country of Publication: Japan NLM ID: 9105360 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1347-7439 (Electronic) Linking ISSN: 09167250 NLM ISO Abbreviation: J Vet Med Sci Subsets: MEDLINE
مواضيع طبية MeSH: Lysosomes*/metabolism , Swainsonine*, Animals ; alpha-Mannosidase/genetics ; Molecular Docking Simulation ; Goats/metabolism ; Mannosidases/metabolism
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29دورية أكاديمية
المؤلفون: Wang W; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China., Wu Y; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China., Shi R; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China., Sun M; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China., Li Q; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China., Zhang G; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China., Wu J; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China., Wang Y; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China., Wang W; State Key Laboratory of Crop Biology, Shandong Key Laboratory of Crop Biology, College of Life Sciences, Shandong Agricultural University, Tai'an, 271018, Shandong, China. wangw@sdau.edu.cn.
المصدر: Plant cell reports [Plant Cell Rep] 2020 May; Vol. 39 (5), pp. 653-667. Date of Electronic Publication: 2020 Mar 02.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Springer Country of Publication: Germany NLM ID: 9880970 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1432-203X (Electronic) Linking ISSN: 07217714 NLM ISO Abbreviation: Plant Cell Rep Subsets: MEDLINE
مواضيع طبية MeSH: Brachypodium/*growth & development , Plant Leaves/*growth & development , Salt Tolerance/*genetics , Triticum/*enzymology , alpha-Mannosidase/*metabolism, Abscisic Acid/pharmacology ; Antioxidants/metabolism ; Brachypodium/drug effects ; Brachypodium/genetics ; Brachypodium/physiology ; Cell Nucleus/genetics ; Cell Nucleus/metabolism ; Droughts ; Endoplasmic Reticulum/genetics ; Endoplasmic Reticulum/metabolism ; Gene Expression Regulation, Plant/drug effects ; Hydrogen Peroxide/pharmacology ; Photosynthesis/drug effects ; Plant Leaves/drug effects ; Plant Leaves/metabolism ; Plant Leaves/physiology ; Plants, Genetically Modified ; Potassium/analysis ; Potassium/metabolism ; Reactive Oxygen Species/metabolism ; Sodium/analysis ; Sodium/metabolism ; Sodium/pharmacology ; Triticum/genetics ; Up-Regulation ; alpha-Mannosidase/genetics
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30دورية أكاديمية
المؤلفون: Umekawa M; Graduate School of Bioresources, Mie University, Tsu, Japan., Shiraishi D; Faculty of Bioresources, Mie University, Tsu, Japan., Fuwa M; Faculty of Bioresources, Mie University, Tsu, Japan., Sawaguchi K; Faculty of Bioresources, Mie University, Tsu, Japan., Mashima Y; Graduate School of Biostudies, Kyoto University, Japan., Katayama T; Graduate School of Biostudies, Kyoto University, Japan., Karita S; Graduate School of Bioresources, Mie University, Tsu, Japan.
المصدر: FEBS letters [FEBS Lett] 2020 Apr; Vol. 594 (8), pp. 1329-1338. Date of Electronic Publication: 2019 Dec 29.
نوع المنشور: Journal Article; Research Support, Non-U.S. Gov't
بيانات الدورية: Publisher: John Wiley & Sons Ltd Country of Publication: England NLM ID: 0155157 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1873-3468 (Electronic) Linking ISSN: 00145793 NLM ISO Abbreviation: FEBS Lett Subsets: MEDLINE
مواضيع طبية MeSH: Cyclin B/*metabolism , Glucose/*metabolism , Saccharomyces cerevisiae/*physiology , Saccharomyces cerevisiae Proteins/*metabolism , alpha-Mannosidase/*metabolism, Adaptation, Biological ; Autophagy/physiology ; Cyclin B/genetics ; DNA-Binding Proteins/metabolism ; Saccharomyces cerevisiae Proteins/genetics ; Transcription Factors/metabolism ; alpha-Mannosidase/genetics