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المصدر: Bioresource Technology. 97:1696-1702
مصطلحات موضوعية: Environmental Engineering, Size-exclusion chromatography, Bioengineering, Acetates, chemistry.chemical_compound, Agave, X-Ray Diffraction, Acetamides, Organic chemistry, Cellulose, Derivatization, Nuclear Magnetic Resonance, Biomolecular, Waste Management and Disposal, Dissolution, SISAL, computer.programming_language, Gossypium, Molar mass, Viscosity, Renewable Energy, Sustainability and the Environment, Acetylation, General Medicine, Alkali metal, Molecular Weight, Solutions, chemistry, Chromatography, Gel, Solvents, Proton NMR, Lithium Chloride, computer
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المساهمون: Laboratoire Génie des procédés papetiers (LGP2 ), Centre National de la Recherche Scientifique (CNRS)-Institut National Polytechnique de Grenoble (INPG)-Institut polytechnique de Grenoble - Grenoble Institute of Technology (Grenoble INP ), Leclerc, Sylvie, Institut polytechnique de Grenoble - Grenoble Institute of Technology (Grenoble INP )-Institut National Polytechnique de Grenoble (INPG)-Centre National de la Recherche Scientifique (CNRS)
المصدر: Carbohydrate Polymers
Carbohydrate Polymers, Elsevier, 2006, 63, pp.19-29مصطلحات موضوعية: [CHIM.MATE] Chemical Sciences/Material chemistry, Polymers and Plastics, Organic Chemistry, [CHIM.MATE]Chemical Sciences/Material chemistry, 02 engineering and technology, 010402 general chemistry, 021001 nanoscience & nanotechnology, 01 natural sciences, Cellulose acetate, Dimethylacetamide, 0104 chemical sciences, chemistry.chemical_compound, Acetic anhydride, chemistry, Materials Chemistry, Inverse gas chromatography, Lithium chloride, Organic chemistry, Reactivity (chemistry), Cellulose, 0210 nano-technology, Derivatization, ComputingMilieux_MISCELLANEOUS, Nuclear chemistry
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المصدر: e-Polymers. 8
مصطلحات موضوعية: Materials science, Polymers and Plastics, General Chemical Engineering, Dimethylacetamide, Microcrystalline cellulose, chemistry.chemical_compound, chemistry, Lithium chloride, Organic chemistry, Hemicellulose, Physical and Theoretical Chemistry, Cellulose, Solubility, Bagasse, computer, SISAL, computer.programming_language
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::1b1cb0c814ae90ce74774c9cd2492a7c
https://doi.org/10.1515/epoly.2008.8.1.226 -
4تقرير
المؤلفون: Paz JA; Child Neurology Unit Children's Institute, University of Sao Paulo School of Medicine Sao Paulo Brazil., Embiruçu EK; Medical Genetic Service Professor Edgard Santos University Hospital Salvador Brazil.; Life Sciences Department University of the State of Bahia Salvador Brazil., Bueno C; Child Neurology Unit Children's Institute, University of Sao Paulo School of Medicine Sao Paulo Brazil.; Child Neurology Service, Department of Neurology University of Sao Paulo School of Medicine Sao Paulo Brazil., Ferreira RCCL; Child Neurology Service, Department of Neurology University of Sao Paulo School of Medicine Sao Paulo Brazil., Oliveira FS; Medical Genetic Service Professor Edgard Santos University Hospital Salvador Brazil., Pereira ASS; Medical Genetic Service Professor Edgard Santos University Hospital Salvador Brazil.; Life Sciences Department University of the State of Bahia Salvador Brazil., Schwartz IVD; Child Neurology Service, Department of Neurology University of Sao Paulo School of Medicine Sao Paulo Brazil.; Medical Genetics Service Hospital de Clinicas de Porto Alegre Porto Alegre Brazil., Paiva ARB; Neurogenetics Unit, Department of Neurology University of Sao Paulo School of Medicine Sao Paulo Brazil., Lucato LT; Department of Radiology University of Sao Paulo School of Medicine Sao Paulo Brazil., Kok F; Child Neurology Unit Children's Institute, University of Sao Paulo School of Medicine Sao Paulo Brazil.; Child Neurology Service, Department of Neurology University of Sao Paulo School of Medicine Sao Paulo Brazil.; Mendelics Genomic Analysis Sao Paulo Brazil.
المصدر: JIMD reports [JIMD Rep] 2021 Sep 30; Vol. 62 (1), pp. 49-55. Date of Electronic Publication: 2021 Sep 30 (Print Publication: 2021).
نوع المنشور: Case Reports
بيانات الدورية: Publisher: Wiley Country of Publication: United States NLM ID: 101568557 Publication Model: eCollection Cited Medium: Print ISSN: 2192-8304 (Print) Linking ISSN: 21928304 NLM ISO Abbreviation: JIMD Rep Subsets: PubMed not MEDLINE
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5دورية أكاديمية
المؤلفون: Horovitz DDG; Centro de Genética Médica, Instituto Nacional de Saúde da Mulher, da Criança e do Adolescente Fernandes Figueira/FIOCRUZ, Rio de Janeiro, RJ, Brazil. Electronic address: dafne.horovitz@iff.fiocruz.br., Leão EKEA; Serviço de Genética Médica, Universidade Federal da Bahia, Salvador, BA, Brazil; Universidade do Estado da Bahia, Salvador, Bahia, Brazil., Ribeiro EM; Hospital Albert Sabin, Fortaleza, CE, Brazil., Martins AM; Centro de Referência em Erros Inatos do Metabolismo, Universidade Federal de São Paulo, SP, Brazil., Barth AL; Centro de Genética Médica, Instituto Nacional de Saúde da Mulher, da Criança e do Adolescente Fernandes Figueira/FIOCRUZ, Rio de Janeiro, RJ, Brazil., Neri JICF; Centro de Reabilitação Infantil de Natal, Natal, RN, Brazil., Kerstenetzky M; Centro de Referência em Doenças Raras (RARUS), Hospital Maria Lucinda, Recife, PE, Brazil., Siqueira ACM; Centro de Tratamento de Erros Inatos do Metabolismo, Instituto de Medicina Integral Professor Fernando Figueira, Brazil., Ribeiro BFR; Fundação Hospital do Acre - FUNDHACRE, Rio Branco, AC, Brazil., Kim CA; Instituto da Criança, Faculdade de Medicina da Universidade de São Paulo, São Paulo, SP, Brazil., Santos FC; Hospital Universitário do Maranhão, São Luís, MA, Brazil., Franco JFS; Enzyme Replacement Therapy Service at Hospital e Maternidade Celso Pierro, PUC-Campinas, Campinas, SP, Brazil; Centro de Biotecnologia/Instituto de Pesquisa de energia Nuclear/Universidade de São Paulo, CBio/IPEN/USP, São Paulo, SP, Brazil., Lichtvan LCL; Universidade Federal do Paraná, Curitiba, PR, Brazil., Giuliani LR; Faculdade de Medicina, Universidade Federal do Mato Grosso do Sul, Campo Grande, MS, Brazil., Rodrigues MDCS; Hospital Universitário Cassiano Antonio de Moraes, Universidade Federal do Espírito Santo, Empresa Brasileira de Serviços Hospitalares (HUCAM/UFES/EBSERH), Vitória, ES, Brazil., Bonatti RCF; Universidade Federal do Triângulo Mineiro, Uberaba, MG, Brazil., Teixeira TB; Associação de Pais e Amigos dos Excepcionais de Anápolis - APAE, Anápolis, GO, Brazil., Gonçalves A; Associação de Pais e Amigos dos Excepcionais de Anápolis - APAE, Anápolis, GO, Brazil., Lourenço CM; Faculdade de Medicina, Centro Universitário Estácio de Ribeirão Preto, Ribeirão Preto, SP, Brazil., Pereira ASS; Universidade do Estado da Bahia, Salvador, Bahia, Brazil., Acosta AX; Serviço de Genética Médica, Universidade Federal da Bahia, Salvador, BA, Brazil.
المصدر: Molecular genetics and metabolism [Mol Genet Metab] 2021 May; Vol. 133 (1), pp. 94-99. Date of Electronic Publication: 2021 Feb 27.
نوع المنشور: Journal Article; Research Support, Non-U.S. Gov't
بيانات الدورية: Publisher: Academic Press Country of Publication: United States NLM ID: 9805456 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1096-7206 (Electronic) Linking ISSN: 10967192 NLM ISO Abbreviation: Mol Genet Metab Subsets: MEDLINE
مواضيع طبية MeSH: Enzyme Replacement Therapy*, Cognition/*drug effects , Mucopolysaccharidosis VI/*therapy , N-Acetylgalactosamine-4-Sulfatase/*genetics, Adolescent ; Brazil/epidemiology ; Child ; Child, Preschool ; Female ; Glycosaminoglycans/urine ; Humans ; Male ; Mucopolysaccharidosis VI/enzymology ; Mucopolysaccharidosis VI/pathology ; Mucopolysaccharidosis VI/urine ; N-Acetylgalactosamine-4-Sulfatase/therapeutic use ; Phenotype ; Quality of Life ; Recombinant Proteins/genetics ; Recombinant Proteins/therapeutic use ; Severity of Illness Index
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