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1دورية أكاديمية
المؤلفون: Célia Dos Santos, Juvenal Paiva, María Lucila Romero, Mara Agazzoni, Ana Catalina Kempfer, Sabrina Rotondo, María Marta Casinelli, María Fabiana Alberto, Analía Sánchez‐Luceros
المصدر: eJHaem, Vol 2, Iss 2, Pp 149-156 (2021)
مصطلحات موضوعية: ADAMTS13, atypical haemolytic uraemic syndrome, thrombotic microangiopathies, thrombotic thrombocytopenic purpura, Diseases of the blood and blood-forming organs, RC633-647.5
وصف الملف: electronic resource
Relation: https://doaj.org/toc/2688-6146
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المؤلفون: Juvenal Paiva, María Marta Casinelli, Célia Dos Santos, Ana Catalina Kempfer, Sabrina Rotondo, Maria Fabiana Alberto, Analía Sánchez-Luceros, María Lucila Romero, Mara Agazzoni
المصدر: CONICET Digital (CONICET)
Consejo Nacional de Investigaciones Científicas y Técnicas
instacron:CONICETمصطلحات موضوعية: Pediatrics, medicine.medical_specialty, business.industry, Thrombotic Microangiopathies, Thrombotic thrombocytopenic purpura, medicine.disease, ADAMTS13, purl.org/becyt/ford/3.2 [https], medicine, purl.org/becyt/ford/3 [https], Single institution, thrombotic thrombocytopenic purpura, business
وصف الملف: application/pdf
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ae4e85861591f09f28de03ad7a870260
https://onlinelibrary.wiley.com/doi/10.1002/jha2.154 -
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المؤلفون: Ana Catalina Kempfer, Adriana I. Woods, Maria A. Lazzari, Alicia N. Blanco, Juvenal Paiva, Analía Sánchez-Luceros, Débora Marina Primrose
المصدر: Research and Practice in Thrombosis and Haemostasis
CONICET Digital (CONICET)
Consejo Nacional de Investigaciones Científicas y Técnicas
instacron:CONICETمصطلحات موضوعية: 0301 basic medicine, Proband, medicine.medical_specialty, congenital, hereditary, and neonatal diseases and abnormalities, desmopressin, CIENCIAS MÉDICAS Y DE LA SALUD, Medicina Clínica, 030204 cardiovascular system & hematology, von Willebrand factor, 03 medical and health sciences, 0302 clinical medicine, Von Willebrand factor, Internal medicine, hemic and lymphatic diseases, purl.org/becyt/ford/3.2 [https], medicine, Von Willebrand disease, Missense mutation, Platelet, Hematología, Allele, Desmopressin, von Willbrand factor, Original Articles: Haemostasis, type 2M, biology, business.industry, Brief Report, Hematology, medicine.disease, mutations, Phenotype, 030104 developmental biology, Endocrinology, biology.protein, purl.org/becyt/ford/3 [https], hemorrhage, business, von Willebrand disease, circulatory and respiratory physiology, medicine.drug
وصف الملف: application/pdf
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المؤلفون: Adriana I. Woods, Maria A. Lazzari, Maria Fabiana Alberto, Roberto Chuit, Analía Sánchez-Luceros, Ana Catalina Kempfer, Emilse Bermejo, Juvenal Paiva, Alicia N. Blanco
المصدر: Seminars in Thrombosis and Hemostasis. 43:092-100
مصطلحات موضوعية: Male, medicine.medical_specialty, CIENCIAS MÉDICAS Y DE LA SALUD, Genotype, RIPSA, von Willebrand Disease, Type 2, 030204 cardiovascular system & hematology, Single Center, medicine.disease_cause, Gastroenterology, 03 medical and health sciences, 0302 clinical medicine, Von Willebrand factor, Internal medicine, von Willebrand Factor, medicine, Von Willebrand disease, Humans, Missense mutation, Platelet, VON WILLEBRAND DISEASE TYPE 2, Mutation, biology, business.industry, Patología, Hematology, medicine.disease, Penetrance, GENOTYPE, Medicina Básica, von Willebrand Diseases, Glycoprotein Ib, 030220 oncology & carcinogenesis, Immunology, VWD 2B, biology.protein, Female, Cardiology and Cardiovascular Medicine, business
وصف الملف: application/pdf
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f30a99613201a7db427c49c003f0d55d
https://doi.org/10.1055/s-0036-1597293 -
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المؤلفون: Adriana I. Woods, Juvenal Paiva, Maria A. Lazzari, Ana Catalina Kempfer, Alicia N. Blanco, Analía Sánchez-Luceros
المصدر: CONICET Digital (CONICET)
Consejo Nacional de Investigaciones Científicas y Técnicas
instacron:CONICETمصطلحات موضوعية: congenital, hereditary, and neonatal diseases and abnormalities, medicine.medical_specialty, CIENCIAS MÉDICAS Y DE LA SALUD, Population, VON WILLEBRAND DISEASE, Medicina Clínica, PHENOTYPE, Gastroenterology, Von Willebrand factor, hemic and lymphatic diseases, Internal medicine, Genotype, purl.org/becyt/ford/3.2 [https], medicine, Von Willebrand disease, Hematología, Family history, Desmopressin, education, education.field_of_study, biology, DESMOPRESSIN, Hematology, medicine.disease, GENOTYPE, biology.protein, purl.org/becyt/ford/3 [https], Abnormality, Antibody, medicine.drug
وصف الملف: application/pdf
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d77e09195c500c00f3a4c725e96d82d1
http://aob.amegroups.com/article/view/4207/4934 -
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المؤلفون: Maria A. Lazzari, Ana Catalina Kempfer, Juvenal Hernán Paiva Palomino, Yanina Powazniak, Julio C Calderazzo Pereyra
المصدر: European Journal of Haematology. 86:140-147
مصطلحات موضوعية: RNA metabolism, Hematology, General Medicine, Biology, Molecular biology, ADAMTS13
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المؤلفون: Ileana R. López, Maria A. Lazzari, Adriana I. Woods, Yanina Powazniak, Ana Catalina Kempfer, Julio Cesar Calderazzo, Analía Sánchez-Luceros
المصدر: Thrombosis and Haemostasis. 108:401-403
مصطلحات موضوعية: 0301 basic medicine, CIENCIAS MÉDICAS Y DE LA SALUD, Thrombotic thrombocytopenic purpura, Medicina Clínica, 030204 cardiovascular system & hematology, 03 medical and health sciences, 0302 clinical medicine, immune system diseases, hemic and lymphatic diseases, medicine, Missense mutation, THROMBOTIC THROMBOCYTOPENIC PURPURA, Pregnancy, business.industry, CUB-2 DOMAIN, Vascular biology, Hematology, medicine.disease, ADAMTS13, Thrombosis, PREGNANCY, 030104 developmental biology, Immunology, SITE-DIRECTED MUTAGENESIS, Medicina Critica y de Emergencia, business
وصف الملف: application/pdf
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::eafc80d65e03ceb9608dbbc17d281510
https://doi.org/10.1160/th11-11-0783 -
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المؤلفون: Gonzalo A. Carballo, Adriana I. Woods, Cristina Elena Farias, Maria A. Lazzari, María R. Silaf, Ana Catalina Kempfer
المصدر: American Journal of Clinical Pathology. 111:418-423
مصطلحات موضوعية: congenital, hereditary, and neonatal diseases and abnormalities, Pathology, medicine.medical_specialty, Enzyme-Linked Immunosorbent Assay, Immunoelectrophoresis, Hemophilia A, Sensitivity and Specificity, Flow cytometry, Von Willebrand factor, Antigen, Reference Values, hemic and lymphatic diseases, von Willebrand Factor, medicine, Von Willebrand disease, Coagulopathy, Animals, Humans, Deamino Arginine Vasopressin, Detection limit, medicine.diagnostic_test, biology, Liaison, Chemistry, General Medicine, Flow Cytometry, medicine.disease, Molecular biology, Microspheres, Molecular Weight, von Willebrand Diseases, cardiovascular system, biology.protein, Polystyrenes, Collagen, Rabbits, Protein Binding, circulatory and respiratory physiology
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::381a3be7cf18e0bad9c7c6f23ae70300
https://doi.org/10.1093/ajcp/111.3.418 -
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المؤلفون: Cristina Elena Farias, Adriana I. Woods, Ana Catalina Kempfer, Gonzalo A. Carballo, Maria A. Lazzari, Patricia Casais, Silvia H. Grosso
المصدر: Thrombosis and Haemostasis. 96:228-230
مصطلحات موضوعية: Genetics, Von Willebrand Factor Gene, COS cells, biology, business.industry, Substitution (logic), Hematology, Phenotype, Exon, Von Willebrand factor, Polymorphism (computer science), biology.protein, Medicine, business, Gene
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::8bab99cd28206a89ce2fd8cd46d956be
https://doi.org/10.1160/th06-03-0144 -
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المؤلفون: Ana Catalina Kempfer, Maria A. Lazzari
المصدر: Thrombosis Research. 80:277-280
مصطلحات موضوعية: Hematology