المؤلفون: Emily Anne Smith Bergbower, Inna Sabirzhanova, Clément Boinot, William B. Guggino, Liudmila Cebotaru

المصدر: Cellular Physiology and Biochemistry, Vol 52, Iss 6, Pp 1267-1279 (2019)

مصطلحات موضوعية: Physiology, QP1-981, Biochemistry, QD415-436

وصف الملف: electronic resource

Relation: https://www.cellphysiolbiochem.com/Articles/000089/; https://doaj.org/toc/1015-8987

URL الوصول: https://doaj.org/article/6ad549979b1249a096b4e70ac778cad6

المؤلفون: Inna Sabirzhanova, Clément Boinot, William B. Guggino, Liudmila Cebotaru

المصدر: Cellular Physiology and Biochemistry, Vol 51, Iss 3, Pp 1489-1499 (2018)

مصطلحات موضوعية: Snare, Processing, Degradation, Mutant, CFTR, Physiology, QP1-981, Biochemistry, QD415-436

وصف الملف: electronic resource

Relation: https://www.karger.com/Article/FullText/495596; https://doaj.org/toc/1015-8987; https://doaj.org/toc/1421-9778

URL الوصول: https://doaj.org/article/72a194b27d754f52b3001997eeaefa36

المؤلفون: Miquéias Lopes-Pacheco, Clément Boinot, Inna Sabirzhanova, Daniele Rapino, Liudmila Cebotaru

المصدر: Cellular Physiology and Biochemistry, Vol 41, Iss 6, Pp 2194-2210 (2017)

مصطلحات موضوعية: CFTR mutants, Cystic fibrosis, Electrophysiology, Heat shock protein, Intracellular trafficking, Membrane-spanning, Precision medicine, Protein folding, Proteostasis network, Physiology, QP1-981, Biochemistry, QD415-436

وصف الملف: electronic resource

Relation: http://www.karger.com/Article/FullText/475578; https://doaj.org/toc/1015-8987; https://doaj.org/toc/1421-9778

URL الوصول: https://doaj.org/article/d1bd1adde0284c35a122fc0d9f0b6a7e

المؤلفون: Clément Boinot, Inna Sabirzhanova, William B. Guggino, Liudmila Cebotaru

المصدر: Cellular physiology and biochemistry : international journal of experimental cellular physiology, biochemistry, and pharmacology
Cellular Physiology and Biochemistry, Vol 51, Iss 3, Pp 1489-1499 (2018)

مصطلحات موضوعية: 0301 basic medicine, Cystic Fibrosis, Physiology, Endosome, Immunoprecipitation, SUMO protein, Cystic Fibrosis Transmembrane Conductance Regulator, Processing, Endoplasmic Reticulum, lcsh:Physiology, Article, Cell Line, lcsh:Biochemistry, 03 medical and health sciences, Degradation, Syntaxin, Humans, lcsh:QD415-436, Gene Silencing, CFTR, ΔF508, lcsh:QP1-981, Snare, Chemistry, Qa-SNARE Proteins, Endoplasmic reticulum, Mutant, Transmembrane protein, Cell biology, Protein Transport, 030104 developmental biology, Proteolysis, Protein folding

URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9ec0aadb18a49f00c9e3c2f0883e1112
http://europepmc.org/articles/PMC6482459

المؤلفون: Inna Sabirzhanova, William B. Guggino, Qiangni Liu, Liudmila Cebotaru, Emily Bergbower, Clément Boinot, Murali K. Yanda

المصدر: Journal of Cystic Fibrosis. 17:582-594

مصطلحات موضوعية: 0301 basic medicine, Pulmonary and Respiratory Medicine, Autophagosome, Mutation, business.industry, Autophagy, Mutant, Regulator, medicine.disease_cause, Transmembrane protein, Cell biology, 03 medical and health sciences, 030104 developmental biology, 0302 clinical medicine, Aggresome, 030220 oncology & carcinogenesis, Pediatrics, Perinatology and Child Health, Chloride channel, Medicine, business

URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::59efb62285220a94c48be73432b40d55
https://doi.org/10.1016/j.jcf.2018.05.016

المؤلفون: Liudmila Cebotaru, Inna Sabirzhanova, Miquéias Lopes-Pacheco, Daniele Rapino, Clément Boinot

المصدر: Cellular Physiology and Biochemistry, Vol 41, Iss 6, Pp 2194-2210 (2017)
Cellular physiology and biochemistry : international journal of experimental cellular physiology, biochemistry, and pharmacology

مصطلحات موضوعية: 0301 basic medicine, Leupeptins, Physiology, Cystic Fibrosis Transmembrane Conductance Regulator, Plasma protein binding, Endoplasmic Reticulum, Hydroxamic Acids, Cystic fibrosis, lcsh:Physiology, Chlorocebus aethiops, Anilides, lcsh:QD415-436, COS cells, Heat shock protein, lcsh:QP1-981, Protein Stability, Precision medicine, Temperature, respiratory system, Proteostasis network, Cystic fibrosis transmembrane conductance regulator, Cell biology, Electrophysiology, Transmembrane domain, COS Cells, Protein Binding, CFTR mutants, Proteasome Endopeptidase Complex, congenital, hereditary, and neonatal diseases and abnormalities, Immunoprecipitation, Cysteine Proteinase Inhibitors, Biology, Transfection, Article, lcsh:Biochemistry, Membrane-spanning, 03 medical and health sciences, medicine, Animals, Humans, Protein folding, HEK 293 cells, medicine.disease, Molecular biology, respiratory tract diseases, HEK293 Cells, 030104 developmental biology, Proteostasis, Proteolysis, Mutagenesis, Site-Directed, biology.protein, Intracellular trafficking

URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9805f3caab76ae25cfc1fea5df0af1c5
https://doi.org/10.1159/000475578

المؤلفون: William B. Guggino, Clément Boinot, Marcelo M. Morales, Liudmila Cebotaru, Inna Sabirzhanova, Miquéias Lopes-Pacheco

المصدر: Journal of Biological Chemistry. 290:25636-25645

مصطلحات موضوعية: HSP27 Heat-Shock Proteins, Cystic Fibrosis Transmembrane Conductance Regulator, ATP-binding cassette transporter, macromolecular substances, Cycloheximide, Protein degradation, Biochemistry, chemistry.chemical_compound, Heat shock protein, Chlorocebus aethiops, Animals, Humans, ΔF508, Molecular Biology, biology, Endoplasmic reticulum, Temperature, Molecular Bases of Disease, Cell Biology, Transfection, HSP40 Heat-Shock Proteins, Molecular biology, Cystic fibrosis transmembrane conductance regulator, HEK293 Cells, chemistry, COS Cells, Mutation, biology.protein, Protein Binding

URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::c2125c6ca4e46a67c3ce9c7a3ca7fa7b
https://doi.org/10.1074/jbc.m115.671925

المؤلفون: Inna Sabirzhanova, Clément Boinot, William B. Guggino, Emily Bergbower, Liudmila Cebotaru

المصدر: Cellular Physiology and Biochemistry, Vol 45, Iss 2, Pp 639-655 (2018)

مصطلحات موضوعية: 0301 basic medicine, Scaffold protein, Cystic Fibrosis, Physiology, Cell, Cystic Fibrosis Transmembrane Conductance Regulator, Endoplasmic Reticulum, lcsh:Physiology, F508-del CFTR, Maturation, Chlorocebus aethiops, lcsh:QD415-436, RNA, Small Interfering, Trafficking, lcsh:QP1-981, biology, Chemistry, respiratory system, Ligand (biochemistry), Hsp90, Cell biology, Protein Transport, medicine.anatomical_structure, COS Cells, RNA Interference, Macrolides, Protein Binding, congenital, hereditary, and neonatal diseases and abnormalities, Sodium-Hydrogen Exchangers, PDZ domain, Article, Cell Line, lcsh:Biochemistry, 03 medical and health sciences, Lysosome, medicine, Animals, Humans, HSP70 Heat-Shock Proteins, HSP90 Heat-Shock Proteins, Adaptor Proteins, Signal Transducing, Endoplasmic reticulum, PDZ-domain, Cell Membrane, Golgi Matrix Proteins, Membrane Proteins, Membrane Transport Proteins, HSP40 Heat-Shock Proteins, Phosphoproteins, digestive system diseases, respiratory tract diseases, 030104 developmental biology, Proteasome, RNA, Ribosomal, biology.protein, Carrier Proteins

URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::49101b2bb9b0dcb5f447681557c5e6d5
https://europepmc.org/articles/PMC5861351/

المؤلفون: Clément Boinot, Ann Harris, Isabelle Callebaut, Toby S. Scott-Ward, Michael J. Mutolo, David N. Sheppard, Timea Palmai-Pallag, Zhiwei Cai, Pissared Khuituan, Beihui Liu

المصدر: The Journal of Physiology. 593:2427-2446

مصطلحات موضوعية: congenital, hereditary, and neonatal diseases and abnormalities, medicine.medical_specialty, Mutation, biology, Physiology, Chinese hamster ovary cell, HEK 293 cells, Gating, respiratory system, medicine.disease, medicine.disease_cause, Cystic fibrosis, digestive system diseases, Cystic fibrosis transmembrane conductance regulator, respiratory tract diseases, Cell biology, Endocrinology, Internal medicine, medicine, Chloride channel, biology.protein, Phosphorylation

URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::d5686b29370f1c0e7a275fe48a22362b
https://doi.org/10.1113/jp270227

المؤلفون: Clément Boinot, H. Wang, Cristina V. Cebotaru, Inna Sabirzhanova, William B. Guggino, Liudmila Cebotaru

المصدر: Journal of Cystic Fibrosis. 17:S27-S28

مصطلحات موضوعية: Pulmonary and Respiratory Medicine, business.industry, Bicarbonate, Mutant, Conductance, medicine.disease, Cystic fibrosis, Chloride, chemistry.chemical_compound, chemistry, Pediatrics, Perinatology and Child Health, medicine, Biophysics, business, medicine.drug

URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::56147dacbc72be31e38a2068c65290b0
https://doi.org/10.1016/s1569-1993(18)30203-0