المؤلفون: Veys K; Department of Pediatrics, University Hospitals Leuven, campus Gasthuisberg, Leuven, Belgium; Department of Development & Regeneration, Laboratory of Pediatric Nephrology, KU Leuven, campus Gasthuisberg, Leuven, Belgium., Elmonem MA; Department of Clinical and Chemical Pathology, Faculty of Medicine, Cairo University, Cairo 11628, Egypt., van den Heuvel L; Department of Development & Regeneration, Laboratory of Pediatric Nephrology, KU Leuven, campus Gasthuisberg, Leuven, Belgium., Gahl WA; National Genome Research Institute (NHGRI), National Institutes of Health, Medical Genetics Branch, 9000 Rockville Pike, Bethesda, MD 20892, United States., Levtchenko E; Department of Pediatric Nephrology, Emma Children's Hospital, Amsterdam University Medical Centers, 1105, AZ, Amsterdam, the Netherlands. Electronic address: e.n.levtchenko@amsterdamumc.nl.

المصدر: Molecular genetics and metabolism [Mol Genet Metab] 2024 May; Vol. 142 (1), pp. 108454. Date of Electronic Publication: 2024 Mar 21.

نوع المنشور: Journal Article; Validation Study; Research Support, Non-U.S. Gov't

بيانات الدورية: Publisher: Academic Press Country of Publication: United States NLM ID: 9805456 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1096-7206 (Electronic) Linking ISSN: 10967192 NLM ISO Abbreviation: Mol Genet Metab Subsets: MEDLINE

مواضيع طبية MeSH: Cysteamine*/therapeutic use , Cystinosis*/drug therapy , Cystinosis*/blood , Hexosaminidases*/blood , Cystine*/blood, Humans ; Male ; Female ; Retrospective Studies ; Adolescent ; Child ; Adult ; Biomarkers/blood ; Young Adult ; Drug Monitoring/methods ; Cystine Depleting Agents/therapeutic use ; Child, Preschool ; Kidney Transplantation

المؤلفون: Kariya M; Department of Nutrition Support Team, Kobe Minimally Invasive Cancer, Kobe, Japan.; Department of Pharmacy, Kobe Minimally Invasive Cancer Center, Kobe, Japan., Yamamoto K; Department of Pharmacy, Kobe University Hospital, Kobe, Japan., Kawamura A; Department of Nutrition Support Team, Kobe Minimally Invasive Cancer, Kobe, Japan.; Department of Gastroenterology, Kobe Minimally Invasive Cancer Center, Kobe, Japan., Tanizaki S; Department of Nutrition Support Team, Kobe Minimally Invasive Cancer, Kobe, Japan.; Department of Nursing, Kobe Minimally Invasive Cancer Center, Kobe, Japan., Ueda K; Department of Nutrition Support Team, Kobe Minimally Invasive Cancer, Kobe, Japan.; Department of Nutrition, Kobe Minimally Invasive Cancer Center, Kobe, Japan., Sai K; Department of Nutrition Support Team, Kobe Minimally Invasive Cancer, Kobe, Japan.; Department of Nutrition, Kobe Minimally Invasive Cancer Center, Kobe, Japan., Hata A; Department of Thoracic Oncology, Kobe Minimally Invasive Cancer Center, 8-5-1, Nakamati Minatojima, Chuo-Ku, Kobe, Hyogo, 650-0046, Japan. akitohata@hotmail.com.

المصدر: Supportive care in cancer : official journal of the Multinational Association of Supportive Care in Cancer [Support Care Cancer] 2024 Jun 03; Vol. 32 (6), pp. 400. Date of Electronic Publication: 2024 Jun 03.

نوع المنشور: Journal Article; Observational Study

بيانات الدورية: Publisher: Springer International Country of Publication: Germany NLM ID: 9302957 Publication Model: Electronic Cited Medium: Internet ISSN: 1433-7339 (Electronic) Linking ISSN: 09414355 NLM ISO Abbreviation: Support Care Cancer Subsets: MEDLINE

مواضيع طبية MeSH: Carcinoma, Non-Small-Cell Lung*/therapy , Carcinoma, Non-Small-Cell Lung*/radiotherapy , Carcinoma, Non-Small-Cell Lung*/drug therapy , Esophagitis*/etiology , Chemoradiotherapy*/adverse effects , Chemoradiotherapy*/methods , Lung Neoplasms*/radiotherapy , Lung Neoplasms*/therapy , Cystine*/administration & dosage , Cystine*/analogs & derivatives , Quality of Life* , Glutamates*/administration & dosage , Glutamates*/adverse effects , Glutamates*/therapeutic use, Humans ; Prospective Studies ; Male ; Female ; Middle Aged ; Aged

المؤلفون: Bondue T; Laboratory of Pediatric Nephrology, Department of Development and Regeneration, KU Leuven, Leuven, Belgium., Khodaparast L; Switch Laboratory, VIB Center for Brain and Disease Research, Leuven, Belgium.; Switch Laboratory, Department of Cellular and Molecular Medicine, KU Leuven, Leuven, Belgium., Khodaparast L; Switch Laboratory, VIB Center for Brain and Disease Research, Leuven, Belgium.; Switch Laboratory, Department of Cellular and Molecular Medicine, KU Leuven, Leuven, Belgium., Cairoli S; Laboratory of Metabolic Biochemistry, Department of Pediatric Medicine, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy., Goffredo BM; Laboratory of Metabolic Biochemistry, Department of Pediatric Medicine, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy., Gijsbers R; Laboratory for Molecular Virology and Gene Therapy, Department of Pharmaceutical and Pharmacological Sciences, KU Leuven, Leuven, Belgium.; Leuven Viral Vector Core, KU Leuven, Leuven, Belgium., van den Heuvel L; Laboratory of Pediatric Nephrology, Department of Development and Regeneration, KU Leuven, Leuven, Belgium.; Department of Pediatric Nephrology, Radboud University Medical Center, Nijmegen, The Netherlands., Levtchenko E; Laboratory of Pediatric Nephrology, Department of Development and Regeneration, KU Leuven, Leuven, Belgium.; Department of Pediatric Nephrology, Emma Children's Hospital, Amsterdam UMC, Amsterdam, The Netherlands.

المصدر: American journal of physiology. Renal physiology [Am J Physiol Renal Physiol] 2024 Jun 01; Vol. 326 (6), pp. F981-F987. Date of Electronic Publication: 2024 Mar 28.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: American Physiological Society Country of Publication: United States NLM ID: 100901990 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1522-1466 (Electronic) Linking ISSN: 15221466 NLM ISO Abbreviation: Am J Physiol Renal Physiol Subsets: MEDLINE

مواضيع طبية MeSH: Zebrafish*/metabolism , Kidney Tubules, Proximal*/metabolism , Kidney Tubules, Proximal*/pathology , Cystinosis*/metabolism , Cystinosis*/genetics , Cystinosis*/pathology , Cystine*/metabolism , Disease Models, Animal*, Animals ; Humans ; Zebrafish Proteins/metabolism ; Zebrafish Proteins/genetics ; Epithelial Cells/metabolism ; Amino Acid Transport Systems, Neutral/genetics ; Amino Acid Transport Systems, Neutral/metabolism ; CRISPR-Cas Systems

المؤلفون: Nakamoto R; Division of Nuclear Medicine and Molecular Imaging, Department of Radiology, Stanford University, 300 Pasteur Drive, H2200, Stanford, CA, 94305-5281, USA., Ferri V; Division of Nuclear Medicine and Molecular Imaging, Department of Radiology, Stanford University, 300 Pasteur Drive, H2200, Stanford, CA, 94305-5281, USA., Duan H; Division of Nuclear Medicine and Molecular Imaging, Department of Radiology, Stanford University, 300 Pasteur Drive, H2200, Stanford, CA, 94305-5281, USA., Hatami N; Division of Nuclear Medicine and Molecular Imaging, Department of Radiology, Stanford University, 300 Pasteur Drive, H2200, Stanford, CA, 94305-5281, USA., Goel M; Division of Nuclear Medicine and Molecular Imaging, Department of Radiology, Stanford University, 300 Pasteur Drive, H2200, Stanford, CA, 94305-5281, USA., Rosenberg J; Division of Nuclear Medicine and Molecular Imaging, Department of Radiology, Stanford University, 300 Pasteur Drive, H2200, Stanford, CA, 94305-5281, USA., Kimura R; Molecular Imaging Program at Stanford, Department of Radiology, Stanford University, 300 Pasteur Drive, Stanford, CA, 94305-5281, USA., Wardak M; Molecular Imaging Program at Stanford, Department of Radiology, Stanford University, 300 Pasteur Drive, Stanford, CA, 94305-5281, USA., Haywood T; Molecular Imaging Program at Stanford, Department of Radiology, Stanford University, 300 Pasteur Drive, Stanford, CA, 94305-5281, USA., Kellow R; Molecular Imaging Program at Stanford, Department of Radiology, Stanford University, 300 Pasteur Drive, Stanford, CA, 94305-5281, USA., Shen B; Molecular Imaging Program at Stanford, Department of Radiology, Stanford University, 300 Pasteur Drive, Stanford, CA, 94305-5281, USA., Park W; Division of Gastroenterology and Hepatology, Stanford University, 300 Pasteur Drive, Stanford, CA, 94305-5281, USA., Iagaru A; Division of Nuclear Medicine and Molecular Imaging, Department of Radiology, Stanford University, 300 Pasteur Drive, H2200, Stanford, CA, 94305-5281, USA. aiagaru@stanford.edu., Gambhir SS; Division of Nuclear Medicine and Molecular Imaging, Department of Radiology, Stanford University, 300 Pasteur Drive, H2200, Stanford, CA, 94305-5281, USA.; Molecular Imaging Program at Stanford, Department of Radiology, Stanford University, 300 Pasteur Drive, Stanford, CA, 94305-5281, USA.

المصدر: European journal of nuclear medicine and molecular imaging [Eur J Nucl Med Mol Imaging] 2022 Dec; Vol. 50 (1), pp. 184-193. Date of Electronic Publication: 2021 Nov 03.

نوع المنشور: Clinical Study; Journal Article

بيانات الدورية: Publisher: Springer-Verlag Berlin Country of Publication: Germany NLM ID: 101140988 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1619-7089 (Electronic) Linking ISSN: 16197070 NLM ISO Abbreviation: Eur J Nucl Med Mol Imaging Subsets: MEDLINE

مواضيع طبية MeSH: Cystine-Knot Miniproteins*/metabolism , Pancreatic Neoplasms*/diagnostic imaging , Pancreatic Neoplasms*/metabolism, Female ; Humans ; Male ; Cystine/metabolism ; Peptides/metabolism ; Positron Emission Tomography Computed Tomography ; Radiopharmaceuticals ; Tissue Distribution ; Pancreatic Neoplasms

المؤلفون: Chen J; Clinical Research Center, Zhujiang Hospital, Southern Medical University, Guangzhou, China., Gao L; Department of Obstetrics and Gynecology, Zhujiang Hospital, Southern Medical University, Guangzhou, China. Electronic address: gaoliuze2016@outlook.com.

المصدر: Biochemical and biophysical research communications [Biochem Biophys Res Commun] 2024 Sep 03; Vol. 723, pp. 150178. Date of Electronic Publication: 2024 May 29.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: Elsevier Country of Publication: United States NLM ID: 0372516 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1090-2104 (Electronic) Linking ISSN: 0006291X NLM ISO Abbreviation: Biochem Biophys Res Commun Subsets: MEDLINE

مواضيع طبية MeSH: Cystine*/metabolism , Electron Transport Complex I*/metabolism , Electron Transport Complex I*/genetics , Electron Transport Complex I*/deficiency , Amino Acid Transport System y+*/metabolism , Amino Acid Transport System y+*/genetics, Humans ; HEK293 Cells ; Oxidative Stress ; Cell Death ; Glutathione/metabolism ; Reactive Oxygen Species/metabolism ; Apoptosis

المؤلفون: Bhatt NP; Department of Immunology, Central Clinical School, Monash University, Melbourne, VIC, Australia.; Bladder and Kidney Health Discovery Program, Central Clinical School, Monash University, Melbourne, VIC, Australia., Deshpande AV; Bladder and Kidney Health Discovery Program, Central Clinical School, Monash University, Melbourne, VIC, Australia.; Centre for Kidney Research, Children's Hospital at Westmead, New South Wales, Australia.; Department of Surgery, Urology Unit, Children's Hospital at Westmead, Sydney, NSW, Australia., Starkey MR; Department of Immunology, Central Clinical School, Monash University, Melbourne, VIC, Australia. malcolm.starkey@monash.edu.; Bladder and Kidney Health Discovery Program, Central Clinical School, Monash University, Melbourne, VIC, Australia. malcolm.starkey@monash.edu.

المصدر: Journal of nephrology [J Nephrol] 2024 Mar; Vol. 37 (2), pp. 293-308. Date of Electronic Publication: 2023 Nov 13.

نوع المنشور: Systematic Review; Journal Article; Review

بيانات الدورية: Publisher: Springer Country of Publication: Italy NLM ID: 9012268 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1724-6059 (Electronic) Linking ISSN: 11218428 NLM ISO Abbreviation: J Nephrol Subsets: MEDLINE

مواضيع طبية MeSH: Cystinuria*/drug therapy , Cystinuria*/urine , Cystine*, Humans ; Sulfhydryl Compounds/therapeutic use ; Sulfhydryl Compounds/urine ; Treatment Outcome ; Diuresis/drug effects

المؤلفون: Harada M; Research Institute for Bioscience Products & Fine Chemicals, Ajinomoto Co., Inc., 1-1 Suzuki-cho, Kawasaki-ku, Kawasaki-shi, Kanagawa 210-8681, Japan., Kato Y; Research Institute for Bioscience Products & Fine Chemicals, Ajinomoto Co., Inc., 1-1 Suzuki-cho, Kawasaki-ku, Kawasaki-shi, Kanagawa 210-8681, Japan., Tsuji C; Research Institute for Bioscience Products & Fine Chemicals, Ajinomoto Co., Inc., 1-1 Suzuki-cho, Kawasaki-ku, Kawasaki-shi, Kanagawa 210-8681, Japan., Higuchi T; Research Institute for Bioscience Products & Fine Chemicals, Ajinomoto Co., Inc., 1-1 Suzuki-cho, Kawasaki-ku, Kawasaki-shi, Kanagawa 210-8681, Japan., Minami A; Research Institute for Bioscience Products & Fine Chemicals, Ajinomoto Co., Inc., 1-1 Suzuki-cho, Kawasaki-ku, Kawasaki-shi, Kanagawa 210-8681, Japan., Furomitsu S; Research Institute for Bioscience Products & Fine Chemicals, Ajinomoto Co., Inc., 1-1 Suzuki-cho, Kawasaki-ku, Kawasaki-shi, Kanagawa 210-8681, Japan., Arakawa A; Research Institute for Bioscience Products & Fine Chemicals, Ajinomoto Co., Inc., 1-1 Suzuki-cho, Kawasaki-ku, Kawasaki-shi, Kanagawa 210-8681, Japan.

المصدر: Analytical chemistry [Anal Chem] 2024 Apr 23; Vol. 96 (16), pp. 6459-6466. Date of Electronic Publication: 2024 Apr 09.

نوع المنشور: Journal Article; Research Support, Non-U.S. Gov't

بيانات الدورية: Publisher: American Chemical Society Country of Publication: United States NLM ID: 0370536 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1520-6882 (Electronic) Linking ISSN: 00032700 NLM ISO Abbreviation: Anal Chem Subsets: MEDLINE

مواضيع طبية MeSH: Culture Media*/chemistry , Cysteine*/chemistry , Cysteine*/analysis , Cystine*/chemistry , Cystine*/analogs & derivatives , Cystine*/analysis , Sulfhydryl Compounds*/chemistry , Sulfhydryl Compounds*/analysis , Tandem Mass Spectrometry*/methods, Chromatography, Liquid/methods ; Click Chemistry ; Liquid Chromatography-Mass Spectrometry ; Malonates/chemistry ; Oxidation-Reduction

المؤلفون: Liu X; Department of Experimental Radiation Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, USA., Zhuang L; Department of Experimental Radiation Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, USA., Gan B; Department of Experimental Radiation Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, USA; The University of Texas MD Anderson UTHealth Graduate School of Biomedical Sciences, Houston, TX, USA. Electronic address: bgan@mdanderson.org.

المصدر: Trends in cell biology [Trends Cell Biol] 2024 Apr; Vol. 34 (4), pp. 327-337. Date of Electronic Publication: 2023 Aug 12.

نوع المنشور: Journal Article; Review

بيانات الدورية: Publisher: Elsevier Science Publishers Country of Publication: England NLM ID: 9200566 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1879-3088 (Electronic) Linking ISSN: 09628924 NLM ISO Abbreviation: Trends Cell Biol Subsets: MEDLINE

مواضيع طبية MeSH: Disulfides* , Cystine*/metabolism, Humans ; Cell Line, Tumor ; Oxidative Stress ; Cell Death

المؤلفون: You F; Division of Anti-Oxidant Research, Life Science Research Center, Gifu University, Yanagito 1-1, Gifu 501-1194, Japan.; Anti-Oxidant Research Laboratory, Louis Pasteur Center for Medical Research, Tanakamonzen-cho 103-5, Sa-kyo-ku, Kyoto 606-8225, Japan., Nicco C; Université Paris Cité, 45 Rue des Saints-Pères, 75006 Paris, France., Harakawa Y; Division of Anti-Oxidant Research, Life Science Research Center, Gifu University, Yanagito 1-1, Gifu 501-1194, Japan., Yoshikawa T; Louis Pasteur Center for Medical Research, Tanakamonzen-cho 103-5, Sakyo-ku, Kyoto 606-8225, Japan.; School of Medicine, Kyoto Prefectural University of Medicine, Kajii-cho, Kawaramachi-Hirokoji, Kamigyo-ku, Kyoto 602-8566, Japan., Inufusa H; Division of Anti-Oxidant Research, Life Science Research Center, Gifu University, Yanagito 1-1, Gifu 501-1194, Japan.; Anti-Oxidant Research Laboratory, Louis Pasteur Center for Medical Research, Tanakamonzen-cho 103-5, Sa-kyo-ku, Kyoto 606-8225, Japan.

المصدر: International journal of molecular sciences [Int J Mol Sci] 2024 Mar 06; Vol. 25 (5). Date of Electronic Publication: 2024 Mar 06.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: MDPI Country of Publication: Switzerland NLM ID: 101092791 Publication Model: Electronic Cited Medium: Internet ISSN: 1422-0067 (Electronic) Linking ISSN: 14220067 NLM ISO Abbreviation: Int J Mol Sci Subsets: MEDLINE

مواضيع طبية MeSH: Antioxidants*/pharmacology , Scleroderma, Systemic*/metabolism , Ascorbic Acid* , Cystine* , Glutamine*, Humans ; Mice ; Animals ; Dietary Supplements ; Fibrosis ; Skin/metabolism ; Disease Models, Animal

المؤلفون: Ivanov AV; Department of Molecular and Cell Pathophysiology, Federal State Budgetary Scientific Institution 'Institute of General Pathology and Pathophysiology', Moscow, Russia., Popov MA; Moscow Regional Research and Clinical Institute n.a. M.F. Vladimirskiy, Moscow, Russia., Aleksandrin V; Department of Molecular and Cell Pathophysiology, Federal State Budgetary Scientific Institution 'Institute of General Pathology and Pathophysiology', Moscow, Russia., Pudova PA; Department of Molecular and Cell Pathophysiology, Federal State Budgetary Scientific Institution 'Institute of General Pathology and Pathophysiology', Moscow, Russia., Galdobina MP; Department of Molecular and Cell Pathophysiology, Federal State Budgetary Scientific Institution 'Institute of General Pathology and Pathophysiology', Moscow, Russia., Metelkin AA; Department of Molecular and Cell Pathophysiology, Federal State Budgetary Scientific Institution 'Institute of General Pathology and Pathophysiology', Moscow, Russia., Kruglova MP; Federal State Autonomous Educational Institution of Higher Education I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University), Moscow, Russia., Maslennikov RA; Moscow Regional Research and Clinical Institute n.a. M.F. Vladimirskiy, Moscow, Russia., Silina EV; Federal State Autonomous Educational Institution of Higher Education I.M. Sechenov First Moscow State Medical University of the Ministry of Health of the Russian Federation (Sechenov University), Moscow, Russia., Stupin VA; Pirogov Russian National Research Medical University (RNRMU), Moscow, Russia., Kubatiev AA; Department of Molecular and Cell Pathophysiology, Federal State Budgetary Scientific Institution 'Institute of General Pathology and Pathophysiology', Moscow, Russia.

المصدر: Electrophoresis [Electrophoresis] 2024 Mar; Vol. 45 (5-6), pp. 411-419. Date of Electronic Publication: 2023 Dec 12.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: Wiley-VCH Country of Publication: Germany NLM ID: 8204476 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1522-2683 (Electronic) Linking ISSN: 01730835 NLM ISO Abbreviation: Electrophoresis Subsets: MEDLINE

مواضيع طبية MeSH: Cystine* , Sulfhydryl Compounds*, Humans ; Reproducibility of Results ; Electrophoresis, Capillary/methods ; Amines ; Plasma ; Hydrogen-Ion Concentration