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1دورية أكاديمية
المؤلفون: Hua X; Key Laboratory of Environmental Medicine Engineering of Ministry of Education, Medical School, Southeast University, Nanjing 210009, China., Liang G; School of Public Health, Southeast University, Nanjing 210009, China., Chao J; Key Laboratory of Environmental Medicine Engineering of Ministry of Education, Medical School, Southeast University, Nanjing 210009, China., Wang D; Key Laboratory of Environmental Medicine Engineering of Ministry of Education, Medical School, Southeast University, Nanjing 210009, China; Shenzhen Ruipuxun Academy for Stem Cell & Regenerative Medicine, Shenzhen, China. Electronic address: dayongw@seu.edu.cn.
المصدر: Journal of hazardous materials [J Hazard Mater] 2024 Jul 05; Vol. 472, pp. 134598. Date of Electronic Publication: 2024 May 13.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Elsevier Country of Publication: Netherlands NLM ID: 9422688 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1873-3336 (Electronic) Linking ISSN: 03043894 NLM ISO Abbreviation: J Hazard Mater Subsets: MEDLINE
مواضيع طبية MeSH: Caenorhabditis elegans*/drug effects , Longevity*/drug effects , Caenorhabditis elegans Proteins*/genetics , Caenorhabditis elegans Proteins*/metabolism , Mitochondria*/drug effects , Mitochondria*/metabolism , Electron Transport Complex I*/metabolism , Electron Transport Complex I*/genetics, Animals ; Electron Transport Complex II/metabolism ; Electron Transport Complex II/genetics ; Insulin/metabolism ; Adenosine Triphosphate/metabolism ; Reactive Oxygen Species/metabolism ; NADH Dehydrogenase ; Cytochromes b
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2دورية أكاديمية
المؤلفون: Parmar G; Department of Biochemistry, Microbiology and Immunology, Faculty of Medicine, University of Ottawa, Ottawa, Ontario, Canada; Ottawa Institute of Systems Biology, University of Ottawa, Ontario, Canada., Fong-McMaster C; Department of Biochemistry, Microbiology and Immunology, Faculty of Medicine, University of Ottawa, Ottawa, Ontario, Canada; Ottawa Institute of Systems Biology, University of Ottawa, Ontario, Canada., Pileggi CA; Department of Biochemistry, Microbiology and Immunology, Faculty of Medicine, University of Ottawa, Ottawa, Ontario, Canada; Ottawa Institute of Systems Biology, University of Ottawa, Ontario, Canada., Patten DA; Department of Biochemistry, Microbiology and Immunology, Faculty of Medicine, University of Ottawa, Ottawa, Ontario, Canada; Ottawa Institute of Systems Biology, University of Ottawa, Ontario, Canada., Cuillerier A; Children's Hospital of Eastern Ontario Research Institute, Ottawa, Ontario, Canada., Myers S; Department of Biochemistry, Microbiology and Immunology, Faculty of Medicine, University of Ottawa, Ottawa, Ontario, Canada; Ottawa Institute of Systems Biology, University of Ottawa, Ontario, Canada., Wang Y; Department of Biology, McGill University, Montreal, Quebec, Canada., Hekimi S; Department of Biology, McGill University, Montreal, Quebec, Canada., Cuperlovic-Culf M; Department of Biochemistry, Microbiology and Immunology, Faculty of Medicine, University of Ottawa, Ottawa, Ontario, Canada; Ottawa Institute of Systems Biology, University of Ottawa, Ontario, Canada; National Research Council of Canada, Digital Technologies Research Centre, Ottawa, Ontario, Canada., Harper ME; Department of Biochemistry, Microbiology and Immunology, Faculty of Medicine, University of Ottawa, Ottawa, Ontario, Canada; Ottawa Institute of Systems Biology, University of Ottawa, Ontario, Canada. Electronic address: mharper@uottawa.ca.
المصدر: The Journal of biological chemistry [J Biol Chem] 2024 Feb; Vol. 300 (2), pp. 105626. Date of Electronic Publication: 2024 Jan 09.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Elsevier Inc. on behalf of American Society for Biochemistry and Molecular Biology Country of Publication: United States NLM ID: 2985121R Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1083-351X (Electronic) Linking ISSN: 00219258 NLM ISO Abbreviation: J Biol Chem Subsets: MEDLINE
مواضيع طبية MeSH: Electron Transport Complex I*/genetics , Electron Transport Complex I*/metabolism , Mitochondria*/genetics , Mitochondria*/metabolism, Electron Transport ; Electron Transport Complex III/genetics ; Electron Transport Complex III/metabolism ; Energy Metabolism ; Mitochondrial Membranes/metabolism ; Humans ; HEK293 Cells
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3دورية أكاديميةThe Structure of the Cardiac Mitochondria Respirasome Is Adapted for the β-Oxidation of Fatty Acids.
المؤلفون: Panov AV; Department of Biomedical Sciences, School of Medicine, Mercer University, Macon, GA 31201, USA.
المصدر: International journal of molecular sciences [Int J Mol Sci] 2024 Feb 18; Vol. 25 (4). Date of Electronic Publication: 2024 Feb 18.
نوع المنشور: Journal Article; Review
بيانات الدورية: Publisher: MDPI Country of Publication: Switzerland NLM ID: 101092791 Publication Model: Electronic Cited Medium: Internet ISSN: 1422-0067 (Electronic) Linking ISSN: 14220067 NLM ISO Abbreviation: Int J Mol Sci Subsets: MEDLINE
مواضيع طبية MeSH: Fatty Acids*/metabolism , Electron Transport Complex III*/metabolism, Oxidation-Reduction ; Mitochondria, Heart/metabolism ; Mitochondrial Membranes/metabolism ; Electron Transport Complex IV/metabolism ; Succinic Acid/metabolism ; Succinates/metabolism ; Electron Transport Complex I/metabolism ; Adenosine Triphosphate/metabolism
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4دورية أكاديمية
المؤلفون: Peruzzotti-Jametti L; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK. lp429@cam.ac.uk.; Department of Metabolism, Digestion and Reproduction, Imperial College London, London, UK. lp429@cam.ac.uk., Willis CM; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Krzak G; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Hamel R; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Pirvan L; Wellcome-MRC Cambridge Stem Cell Institute, University of Cambridge, Cambridge, UK., Ionescu RB; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Reisz JA; Department of Biochemistry and Molecular Genetics, University of Colorado School of Medicine, Aurora, CO, USA., Prag HA; MRC Mitochondrial Biology Unit, University of Cambridge, Cambridge Biomedical Campus, Cambridge, UK., Garcia-Segura ME; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Wu V; Department of Metabolism, Digestion and Reproduction, Imperial College London, London, UK., Xiang Y; Department of Metabolism, Digestion and Reproduction, Imperial College London, London, UK., Barlas B; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK.; UK Dementia Research Institute, University of Cambridge, Cambridge, UK., Casey AM; MRC Mitochondrial Biology Unit, University of Cambridge, Cambridge Biomedical Campus, Cambridge, UK., van den Bosch AMR; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Nicaise AM; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Roth L; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Bates GR; MRC Mitochondrial Biology Unit, University of Cambridge, Cambridge Biomedical Campus, Cambridge, UK., Huang H; Department of Metabolism, Digestion and Reproduction, Imperial College London, London, UK., Prasad P; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK., Vincent AE; Wellcome Centre for Mitochondrial Research, Translational and Clinical Research Institute, Faculty of Medical Sciences, Newcastle University, Newcastle upon Tyne, UK., Frezza C; University Hospital Cologne, Cologne, Germany., Viscomi C; University of Padua, Padova, Italy., Balmus G; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK.; UK Dementia Research Institute, University of Cambridge, Cambridge, UK.; Department of Molecular Neuroscience, Transylvanian Institute of Neuroscience, Cluj-Napoca, Romania., Takats Z; Department of Metabolism, Digestion and Reproduction, Imperial College London, London, UK., Marioni JC; European Molecular Biology Laboratory, European Bioinformatics Institute, EMBL-EBI, Wellcome Genome Campus, Hinxton, UK., D'Alessandro A; Department of Biochemistry and Molecular Genetics, University of Colorado School of Medicine, Aurora, CO, USA., Murphy MP; MRC Mitochondrial Biology Unit, University of Cambridge, Cambridge Biomedical Campus, Cambridge, UK., Mohorianu I; Wellcome-MRC Cambridge Stem Cell Institute, University of Cambridge, Cambridge, UK., Pluchino S; Department of Clinical Neurosciences and NIHR Biomedical Research Centre, University of Cambridge, Cambridge, UK. spp24@cam.ac.uk.
المصدر: Nature [Nature] 2024 Apr; Vol. 628 (8006), pp. 195-203. Date of Electronic Publication: 2024 Mar 13.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Nature Publishing Group Country of Publication: England NLM ID: 0410462 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1476-4687 (Electronic) Linking ISSN: 00280836 NLM ISO Abbreviation: Nature Subsets: MEDLINE
مواضيع طبية MeSH: Electron Transport Complex I*/antagonists & inhibitors , Electron Transport Complex I*/metabolism , Inflammation*/drug therapy , Inflammation*/metabolism , Inflammation*/pathology , Microglia*/drug effects , Microglia*/metabolism , Microglia*/pathology , Neuroinflammatory Diseases*/drug therapy , Neuroinflammatory Diseases*/metabolism , Neuroinflammatory Diseases*/pathology, Animals ; Female ; Humans ; Male ; Mice ; Central Nervous System/drug effects ; Central Nervous System/metabolism ; Central Nervous System/pathology ; Disease Models, Animal ; Electron Transport/drug effects ; Mitochondria/drug effects ; Mitochondria/metabolism ; Mitochondria/pathology ; Multiomics ; Myeloid Cells/metabolism ; Myeloid Cells/pathology ; Reactive Oxygen Species/metabolism
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5دورية أكاديمية
المؤلفون: Oh Y; Department of Integrated Biological Science, Pusan National University, Busan, Korea., Oh JI; Department of Integrated Biological Science, Pusan National University, Busan, Korea; Microbiological Resource Research Institute, Pusan National University, Busan, Korea. Electronic address: joh@pusan.ac.kr.
المصدر: The Journal of biological chemistry [J Biol Chem] 2024 Mar; Vol. 300 (3), pp. 105764. Date of Electronic Publication: 2024 Feb 16.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Elsevier Inc. on behalf of American Society for Biochemistry and Molecular Biology Country of Publication: United States NLM ID: 2985121R Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1083-351X (Electronic) Linking ISSN: 00219258 NLM ISO Abbreviation: J Biol Chem Subsets: MEDLINE
مواضيع طبية MeSH: Bacterial Proteins*/genetics , Bacterial Proteins*/metabolism , Electron Transport Complex IV*/genetics , Electron Transport Complex IV*/metabolism , Mycobacterium smegmatis*/enzymology , Mycobacterium smegmatis*/genetics , Sigma Factor*/genetics , Sigma Factor*/metabolism, Electron Transport ; Gene Expression Regulation, Bacterial ; Histidine Kinase/genetics ; Histidine Kinase/metabolism ; Phosphoric Monoester Hydrolases/metabolism
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6تقرير
المؤلفون: Misceo D; Department of Medical Genetics, Oslo University Hospital and University of Oslo, 0450 Oslo, Norway., Strømme P; Division of Pediatrics and Adolescent Medicine, Oslo University Hospital and Faculty of Medicine, University of Oslo, 0450 Oslo, Norway., Bitarafan F; Department of Medical Genetics, Oslo University Hospital and University of Oslo, 0450 Oslo, Norway., Chawla MS; Department of Neuroradiology, Oslo University Hospital, 0450 Oslo, Norway., Sheng Y; Department of Medical Genetics, Oslo University Hospital and University of Oslo, 0450 Oslo, Norway., Bach de Courtade SM; Department of Biochemistry, Oslo University Hospital and University of Oslo, 0450 Oslo, Norway., Eide L; Department of Biochemistry, Oslo University Hospital and University of Oslo, 0450 Oslo, Norway., Frengen E; Department of Medical Genetics, Oslo University Hospital and University of Oslo, 0450 Oslo, Norway.
المصدر: Genes [Genes (Basel)] 2024 Apr 17; Vol. 15 (4). Date of Electronic Publication: 2024 Apr 17.
نوع المنشور: Case Reports; Research Support, Non-U.S. Gov't
بيانات الدورية: Publisher: MDPI Country of Publication: Switzerland NLM ID: 101551097 Publication Model: Electronic Cited Medium: Internet ISSN: 2073-4425 (Electronic) Linking ISSN: 20734425 NLM ISO Abbreviation: Genes (Basel) Subsets: MEDLINE
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7دورية أكاديمية
المؤلفون: Tabata Fukushima C; Departments of Anesthesiology, University of Rochester Medical Center, USA; Departments of Biochemistry, University of Rochester Medical Center, USA; Pharmacology and Physiology, University of Rochester Medical Center, USA., Dancil IS; Departments of Anesthesiology, University of Rochester Medical Center, USA., Clary H; Departments of Biochemistry, University of Rochester Medical Center, USA., Shah N; Pharmacology and Physiology, University of Rochester Medical Center, USA., Nadtochiy SM; Departments of Anesthesiology, University of Rochester Medical Center, USA., Brookes PS; Departments of Anesthesiology, University of Rochester Medical Center, USA; Pharmacology and Physiology, University of Rochester Medical Center, USA. Electronic address: paul_brookes@urmc.rochester.edu.
المصدر: Redox biology [Redox Biol] 2024 Apr; Vol. 70, pp. 103047. Date of Electronic Publication: 2024 Jan 27.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Elsevier, B.V Country of Publication: Netherlands NLM ID: 101605639 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2213-2317 (Electronic) Linking ISSN: 22132317 NLM ISO Abbreviation: Redox Biol Subsets: MEDLINE
مواضيع طبية MeSH: Electron Transport Complex I*/metabolism , Reperfusion Injury*/metabolism, Mice ; Animals ; Reactive Oxygen Species/metabolism ; Electrons ; Electron Transport ; Mitochondria, Heart/metabolism ; Reperfusion ; Succinates
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8دورية أكاديمية
المؤلفون: Wang Y; State Key Laboratory of Chemical Biology and Drug Discovery, Department of Applied Biology and Chemical Technology, The Hong Kong Polytechnic University, Hung Hom, Kowloon, Hong Kong SAR, China., Paidi VK; European Synchrotron Radiation Facility, 71 Avenue des Martyrs, Grenoble, 38043, Cedex 9, France., Wang W; Department of Applied Physics, The Hong Kong Polytechnic University, Hung Hom, Kowloon, Hong Kong SAR, China., Wang Y; State Key Laboratory of Chemical Biology and Drug Discovery, Department of Applied Biology and Chemical Technology, The Hong Kong Polytechnic University, Hung Hom, Kowloon, Hong Kong SAR, China., Jia G; State Key Laboratory of Automotive Simulation and Control, Department of Materials Science, Key Laboratory of Automobile Materials of MOE, Jilin University, Changchun, 130012, China., Yan T; Key Laboratory of Photonic and Electronic Bandgap Materials of MOE, College of Chemistry and Chemical Engineering, Harbin Normal University, Harbin, 150025, PR China., Cui X; State Key Laboratory of Automotive Simulation and Control, Department of Materials Science, Key Laboratory of Automobile Materials of MOE, Jilin University, Changchun, 130012, China., Cai S; Department of Applied Physics, The Hong Kong Polytechnic University, Hung Hom, Kowloon, Hong Kong SAR, China. songhua.cai@polyu.edu.hk., Zhao J; Key Laboratory of Photonic and Electronic Bandgap Materials of MOE, College of Chemistry and Chemical Engineering, Harbin Normal University, Harbin, 150025, PR China. xjz_hmily@163.com., Lee KS; Pohang Accelerator Laboratory (PAL), Pohang University of Science and Technology (POSTECH), Pohang, 37673, Republic of Korea. lks3006@postech.ac.kr., Lee LYS; State Key Laboratory of Chemical Biology and Drug Discovery, Department of Applied Biology and Chemical Technology, The Hong Kong Polytechnic University, Hung Hom, Kowloon, Hong Kong SAR, China. lawrence.ys.lee@polyu.edu.hk.; Research Institute for Smart Energy, The Hong Kong Polytechnic University, Hung Hom, Kowloon, Hong Kong SAR, China. lawrence.ys.lee@polyu.edu.hk., Wong KY; State Key Laboratory of Chemical Biology and Drug Discovery, Department of Applied Biology and Chemical Technology, The Hong Kong Polytechnic University, Hung Hom, Kowloon, Hong Kong SAR, China. kwok-yin.wong@polyu.edu.hk.
المصدر: Nature communications [Nat Commun] 2024 Mar 12; Vol. 15 (1), pp. 2239. Date of Electronic Publication: 2024 Mar 12.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: Nature Pub. Group Country of Publication: England NLM ID: 101528555 Publication Model: Electronic Cited Medium: Internet ISSN: 2041-1723 (Electronic) Linking ISSN: 20411723 NLM ISO Abbreviation: Nat Commun Subsets: MEDLINE
مواضيع طبية MeSH: Biomimetics* , Electron Transport Complex IV*, Biocatalysis ; Electron Transport ; Engineering ; Catalysis
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9دورية أكاديمية
المؤلفون: Hagras MA; Department of Basic Sciences, University of Health Sciences and Pharmacy, St. Louis, Missouri 63110, United States.
المصدر: The journal of physical chemistry. B [J Phys Chem B] 2024 Feb 01; Vol. 128 (4), pp. 990-1000. Date of Electronic Publication: 2024 Jan 19.
نوع المنشور: Journal Article
بيانات الدورية: Publisher: American Chemical Society Country of Publication: United States NLM ID: 101157530 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1520-5207 (Electronic) Linking ISSN: 15205207 NLM ISO Abbreviation: J Phys Chem B Subsets: MEDLINE
مواضيع طبية MeSH: Electron Transport Complex III*/metabolism , Electrons*, Ligands ; Electron Transport ; Oxidation-Reduction ; Binding Sites ; Molecular Dynamics Simulation ; Heme/chemistry
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10دورية أكاديمية
المؤلفون: Nithianandam V; Department of Pathology, Brigham and Women's Hospital, Harvard Medical School, 77 Avenue Louis Pasteur, Boston, MA 02115, United States.; Aligning Science Across Parkinson's (ASAP) Collaborative Research Network, 5425 Wisconsin Avenue, Chevy Chase, MD 20815, United States., Sarkar S; Department of Pathology, Brigham and Women's Hospital, Harvard Medical School, 77 Avenue Louis Pasteur, Boston, MA 02115, United States.; Aligning Science Across Parkinson's (ASAP) Collaborative Research Network, 5425 Wisconsin Avenue, Chevy Chase, MD 20815, United States., Feany MB; Department of Pathology, Brigham and Women's Hospital, Harvard Medical School, 77 Avenue Louis Pasteur, Boston, MA 02115, United States.; Aligning Science Across Parkinson's (ASAP) Collaborative Research Network, 5425 Wisconsin Avenue, Chevy Chase, MD 20815, United States.
المصدر: Human molecular genetics [Hum Mol Genet] 2024 May 04; Vol. 33 (10), pp. 860-871.
نوع المنشور: Journal Article; Research Support, Non-U.S. Gov't; Research Support, N.I.H., Extramural
بيانات الدورية: Publisher: IRL Press at Oxford University Press Country of Publication: England NLM ID: 9208958 Publication Model: Print Cited Medium: Internet ISSN: 1460-2083 (Electronic) Linking ISSN: 09646906 NLM ISO Abbreviation: Hum Mol Genet Subsets: MEDLINE
مواضيع طبية MeSH: Electron Transport Complex I*/*deficiency, Proteostasis* , Electron Transport Complex I*/genetics , Electron Transport Complex I*/metabolism , Mitochondria*/metabolism , Mitochondria*/genetics , Mitochondria*/pathology , Drosophila Proteins*/genetics , Drosophila Proteins*/metabolism , Drosophila Proteins*/deficiency , Mitochondrial Diseases*/genetics , Mitochondrial Diseases*/metabolism , Mitochondrial Diseases*/pathology , Disease Models, Animal*, Animals ; Humans ; Proteasome Endopeptidase Complex/metabolism ; Proteasome Endopeptidase Complex/genetics ; Autophagy/genetics ; Oxidative Stress/genetics ; Drosophila melanogaster/genetics ; Mutation ; Lysosomes/metabolism ; Lysosomes/genetics ; Drosophila/genetics ; Drosophila/metabolism ; Signal Transduction
SCR Disease Name: Mitochondrial complex I deficiency