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المصدر: The Journal of Biological Chemistry
The journal of biological chemistry 298(1), 101438 (2022). doi:10.1016/j.jbc.2021.101438مصطلحات موضوعية: Protein Conformation, membrane tethering, MLV, multilamellar vesicle, DRP, dynamin-related protein, FRET, Förster resonance energy transfer, HSN, hereditary sensory neuropathy, EEG, electroencephalogram, GTP Phosphohydrolases, ER, endoplasmic reticulum, GTP-Binding Proteins, Humans, ddc:610, CP, cerebral palsy, GED, GTPase effector domain, GTPase, HSP, hereditary spastic paraplegia, Spastic Paraplegia, Hereditary, BSE, bundle signaling element, Membrane Proteins, ATL1, atlastin-1, WT, wild-type, Mutagenesis, Insertional, TKO, triple-knockout, Mutation, ACTH, adrenocorticotropic hormone, neuropathy, MRI, magnetic resonance imaging, Research Article
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::19ae4587531d6d7ae408deb09c6a347e
http://europepmc.org/articles/PMC8688574 -
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المؤلفون: Emma R, Wilson, Umaiyal, Kugathasan, Andrey Y, Abramov, Alex J, Clark, David L H, Bennett, Mary M, Reilly, Linda, Greensmith, Bernadett, Kalmar
المصدر: Neurobiology of Disease
مصطلحات موضوعية: NCX, sodium-Ca2+ exchanger, Peripheral neuropathy, MN, motor neuron, mPTP, mitochondrial permeability transition pore, TMRM, tetramethylrhodamine methyl ester, CHOP, C/EBP homologous protein, DSp, deoxysphinganine, NMDA, N-methyl-D-asparatate, HSN, hereditary sensory neuropathy, Article, Sphingolipid, ER, endoplasmic reticulum, Mice, UPR, unfolded protein response, SOC, store-operated calcium, Animals, ∆ψm, mitochondrial membrane potential, Hereditary Sensory and Autonomic Neuropathies, Cells, Cultured, Motor Neurons, Sphingolipids, ES-285, PMCA, plasma membrane Ca2+ ATPase, Deoxysphingolipid, Neuron, SPT, serine palmitoyltransferase, Mitochondria, Mice, Inbred C57BL, DRG, dorsal root ganglia, DMSp, deoxymethylsphinganine, SERCA, sarco/endoplasmic reticulum Ca2+-ATPase, Sp, sphinganine, MAM, mitochondria-associated ER membrane, Calcium, FCCP, carbonyl cyanide-p-trifluoromethoxyphenylhydrazone, PLP, pyridoxal 5′-phosphate, GADD153, growth arrest and DNA damage-inducible protein, CsA, cyclosporine A, Endoplasmic reticulum