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1دورية أكاديمية
المؤلفون: Murali K. Yanda, Vartika Tomar, Liudmila Cebotaru
المصدر: Cellular and Molecular Gastroenterology and Hepatology, Vol 12, Iss 5, Pp 1517-1529 (2021)
مصطلحات موضوعية: Processing, Trafficking, ARPKD, FPC, ERAD, Diseases of the digestive system. Gastroenterology, RC799-869
وصف الملف: electronic resource
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2
المؤلفون: Murali K. Yanda, Adi Zeidan, Liudmila Cebotaru
المصدر: American Journal of Physiology-Gastrointestinal and Liver Physiology. 324:G404-G414
مصطلحات موضوعية: Hepatology, Physiology, Physiology (medical), Gastroenterology
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::2a7751848f40153528f3d5a9cfe93bb6
https://doi.org/10.1152/ajpgi.00255.2022 -
3
المؤلفون: Vartika Tomar, Liudmila Cebotaru, Murali K. Yanda
المصدر: Cellular and Molecular Gastroenterology and Hepatology
Cellular and Molecular Gastroenterology and Hepatology, Vol 12, Iss 5, Pp 1517-1529 (2021)مصطلحات موضوعية: ARPKD, Cystic Fibrosis Transmembrane Conductance Regulator, RC799-869, Cystic fibrosis, Mice, Heat-Shock Proteins, Original Research, Sequence Deletion, Mice, Knockout, Trafficking, biology, Gastroenterology, Endoplasmic Reticulum-Associated Degradation, Diseases of the digestive system. Gastroenterology, cAMP, adenosine 3′,5′-cyclic monophosphate, Autosomal Recessive Polycystic Kidney Disease, Cystic fibrosis transmembrane conductance regulator, Protein Transport, Phenotype, FPC, HSP, heat shock protein, WGA, wheat germ agglutinin, PBS, phosphate-buffered saline, ERAD, endoplasmic reticulum–associated degradation, Receptors, Cell Surface, Endoplasmic-reticulum-associated protein degradation, Processing, Cholangiocyte, Cell Line, ER, endoplasmic reticulum, Hsp27, Heat shock protein, 3D, 3-dimensional, medicine, Animals, Humans, CFTR, cystic fibrosis transmembrane conductance regulator, Genetic Predisposition to Disease, Gene Silencing, ARPKD, autosomal recessive polycystic kidney disease, Polycystic Kidney, Autosomal Recessive, CF, cystic fibrosis, FPC, fibrocystin/polyductin, Hepatology, business.industry, Genetic Therapy, ERAD, medicine.disease, WT, wild-type, Hsp70, Disease Models, Animal, Gene Expression Regulation, Mutation, Cancer research, biology.protein, ADPKD, autosomal dominant polycystic kidney disease, business, AHA1, ATPase homolog 1
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4
المصدر: Cell Calcium
مصطلحات موضوعية: Voltage-dependent anion channel, TRPP Cation Channels, biology, Physiology, Chemistry, Cell growth, Cysts, Endoplasmic reticulum, Cell Biology, Mitochondrion, Pyruvate dehydrogenase phosphatase, medicine.disease, Polycystic Kidney, Autosomal Dominant, Article, Cell biology, Mitochondria, Mice, Apoptosis, biology.protein, Polycystic kidney disease, medicine, Animals, Calcium, Uniporter, Molecular Biology
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::060905f80c36677231e998717fa5494a
https://europepmc.org/articles/PMC8840832/ -
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المؤلفون: William B. Guggino, Liudmila Cebotaru, Murali K. Yanda
المصدر: American Journal of Physiology-Gastrointestinal and Liver Physiology. 318:G120-G129
مصطلحات موضوعية: 0301 basic medicine, Hepatology, biology, Physiology, business.industry, Gastroenterology, Clostridium difficile toxin B, Clostridium difficile, Cystic fibrosis transmembrane conductance regulator, Microbiology, Heat shock factor, 03 medical and health sciences, 030104 developmental biology, 0302 clinical medicine, Hsp27, Physiology (medical), Heat shock protein, Chaperone (protein), biology.protein, Medicine, business, Pathogen, 030217 neurology & neurosurgery
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::a82b4837b8f42d3aa73de63fee480255
https://doi.org/10.1152/ajpgi.00166.2019 -
6
المؤلفون: Liudmila Cebotaru, Cristina V. Cebotaru, Murali K. Yanda, Boyoung Cha
المصدر: J Biol Chem
مصطلحات موضوعية: 0301 basic medicine, Epithelial sodium channel, medicine.medical_specialty, Autosomal dominant polycystic kidney disease, Aminopyridines, Cystic Fibrosis Transmembrane Conductance Regulator, Golgi Apparatus, Endoplasmic Reticulum, Biochemistry, 03 medical and health sciences, Internal medicine, medicine, Polycystic kidney disease, Humans, Benzodioxoles, Molecular Biology, Epithelial polarity, Kidney, 030102 biochemistry & molecular biology, PKD1, biology, Cysts, Sodium-Hydrogen Exchanger 3, urogenital system, Chemistry, Cell Biology, respiratory system, Apical membrane, Polycystic Kidney, Autosomal Dominant, medicine.disease, Cystic fibrosis transmembrane conductance regulator, Protein Transport, 030104 developmental biology, Endocrinology, medicine.anatomical_structure, Absorption, Physicochemical, biology.protein
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::67bdb14024b88d725145578ac273ca7f
https://doi.org/10.1074/jbc.ra119.010320 -
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المؤلفون: Liudmila Cebotaru, Murali K. Yanda
المصدر: FASEB J
مصطلحات موضوعية: Male, Epithelial sodium channel, medicine.medical_specialty, Autosomal dominant polycystic kidney disease, Aminopyridines, Cystic Fibrosis Transmembrane Conductance Regulator, Kidney, Biochemistry, Cystic fibrosis, Article, Mice, Internal medicine, Genetics, medicine, Polycystic kidney disease, Animals, Cyst, Benzodioxoles, Molecular Biology, Epithelial polarity, biology, Cysts, business.industry, Apical membrane, Polycystic Kidney, Autosomal Dominant, medicine.disease, Cystic fibrosis transmembrane conductance regulator, Mice, Inbred C57BL, Endocrinology, biology.protein, Female, business, Biotechnology
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8
المؤلفون: Inna Sabirzhanova, William B. Guggino, Qiangni Liu, Liudmila Cebotaru, Emily Bergbower, Clément Boinot, Murali K. Yanda
المصدر: Journal of Cystic Fibrosis. 17:582-594
مصطلحات موضوعية: 0301 basic medicine, Pulmonary and Respiratory Medicine, Autophagosome, Mutation, business.industry, Autophagy, Mutant, Regulator, medicine.disease_cause, Transmembrane protein, Cell biology, 03 medical and health sciences, 030104 developmental biology, 0302 clinical medicine, Aggresome, 030220 oncology & carcinogenesis, Pediatrics, Perinatology and Child Health, Chloride channel, Medicine, business
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9Transduction of Surface and Basal Cells in Rhesus Macaque Lung Following Repeat Dosing with AAV1CFTR
المصدر: Hum Gene Ther
مصطلحات موضوعية: Cystic Fibrosis, Genetic Vectors, Cystic Fibrosis Transmembrane Conductance Regulator, Spleen, Genome, Viral, Cystic fibrosis, Virus, Green fluorescent protein, 03 medical and health sciences, 0302 clinical medicine, Transduction, Genetic, Genetics, medicine, Animals, Humans, Molecular Biology, Lung, 030304 developmental biology, 0303 health sciences, biology, Dose-Response Relationship, Drug, ELISPOT, Gene Transfer Techniques, Genetic Therapy, respiratory system, Dependovirus, medicine.disease, biology.organism_classification, Molecular biology, Macaca mulatta, Cystic fibrosis transmembrane conductance regulator, respiratory tract diseases, Titer, Rhesus macaque, medicine.anatomical_structure, 030220 oncology & carcinogenesis, biology.protein, Molecular Medicine, Research Article
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9c61a0632b0f279e9b21529f33eacd50
https://pubmed.ncbi.nlm.nih.gov/32862701 -
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المؤلفون: Vartika Tomar, Cristina V. Cebotaru, Murali K. Yanda, William B. Guggino, Liudmila Cebotaru
المصدر: Journal of Cystic Fibrosis. 20:S288
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Prednisone treatment, Lung, biology, business.industry, Pharmacology, biology.organism_classification, medicine.disease, Cystic fibrosis, Rhesus macaque, Transduction (genetics), medicine.anatomical_structure, Pediatrics, Perinatology and Child Health, Medicine, Dosing, business