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المؤلفون: Guo, Jiasong, Wang, Leiming, Zhang, Yang, Wu, Jiawen, Arpag, Sezgi, Hu, Bo, Imhof, Beat, Tian, Xinxia, Carter, Bruce D, Suter, Ueli, Li, Jun
المصدر: Annals of neurology
Annals of Neurology, Vol. 75, No 2 (2014) pp. 255-65مصطلحات موضوعية: Junctional Adhesion Molecules, Mutation/genetics, Neural Conduction, Action Potentials, Hereditary Sensory and Motor Neuropathy/genetics/metabolism, Mice, Transgenic, ddc:616.07, Gene Expression Regulation/genetics, Article, Tight Junctions, Mice, Peripheral Nerves/metabolism/pathology, Myelin Proteins/deficiency, Animals, Humans, Neural Conduction/drug effects/genetics, Peripheral Nerves, Myelin Sheath, Myelin Sheath/metabolism, Arthrogryposis, Arthrogryposis/genetics/metabolism, Tight Junction Proteins, Action Potentials/drug effects/genetics, Tight Junctions/genetics/metabolism/pathology, Age Factors, Axons, Potassium/pharmacology, Disease Models, Animal, HEK293 Cells, Gene Expression Regulation, Junctional Adhesion Molecules/metabolism, Mutation, Potassium, Tight Junction Proteins/metabolism, Hereditary Sensory and Motor Neuropathy, Axons/drug effects/metabolism/pathology, Myelin Proteins