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1دورية أكاديمية
المؤلفون: Fasana, Elisa, Fregno, Ilaria, Galli, Carmela, Soldà, Tatiana, Molinari, MaurizioAff1, Aff2, IDs4431902400165y_cor5
المصدر: EMBO Reports. 25(6):2773-2785
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2دورية أكاديميةHSPB8 frameshift mutant aggregates weaken chaperone-assisted selective autophagy in neuromyopathies.
المؤلفون: Tedesco, Barbara, Vendredy, Leen, Adriaenssens, Elias, Cozzi, Marta, Asselbergh, Bob, Crippa, Valeria, Cristofani, Riccardo, Rusmini, Paola, Ferrari, Veronica, Casarotto, Elena, Chierichetti, Marta, Mina, Francesco, Pramaggiore, Paola, Galbiati, Mariarita, Piccolella, Margherita, Baets, Jonathan, Baeke, Femke, De Rycke, Riet, Mouly, Vincent, Laurenzi, Tommaso, Eberini, Ivano, Vihola, Anna, Udd, Bjarne, Weiss, Lan, Timmerman, Vincent, Poletti, Angelo, Kimonis, Virginia
المصدر: Autophagy. 19(8)
مصطلحات موضوعية: BAG3, CASA, HSPA, HSPB8, misfolding, myopathy, neuromuscular disorders, neuropathy, protein quality control, Humans, Sequestosome-1 Protein, Autophagy, Heat-Shock Proteins, Neuromuscular Diseases, Charcot-Marie-Tooth Disease, Ubiquitin-Protein Ligases, Adaptor Proteins, Signal Transducing, Apoptosis Regulatory Proteins, Molecular Chaperones
وصف الملف: application/pdf
URL الوصول: https://escholarship.org/uc/item/6zr1w6hq
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3دورية أكاديمية
المؤلفون: Monda, Julie K, Ge, Xuezhen, Hunkeler, Moritz, Donovan, Katherine A, W., Michelle, Jin, Cyrus Y, Leonard, Marilyn, Fischer, Eric S, Bennett, Eric J
المصدر: Cell Reports. 42(5)
مصطلحات موضوعية: Biochemistry and Cell Biology, Biological Sciences, 1.1 Normal biological development and functioning, Underpinning research, Generic health relevance, Ubiquitin-Protein Ligases, Ubiquitin, Cell Line, DNA Repair, Cell Nucleus, Signal Transduction, CP: Cell biology, CP: Molecular biology, HAPSTR1/TAPR1/C16orf72, HUWE1, protein quality control, stress signaling, ubiquitin, Medical Physiology, Biological sciences
وصف الملف: application/pdf
URL الوصول: https://escholarship.org/uc/item/8v65k4cz
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4دورية أكاديمية
المؤلفون: Martin Grønbæk-Thygesen, Rasmus Hartmann-Petersen
المصدر: Cell & Bioscience, Vol 14, Iss 1, Pp 1-33 (2024)
مصطلحات موضوعية: Protein folding, Protein stability, Protein degradation, Protein quality control, Protein misfolding, Proteasome, Biotechnology, TP248.13-248.65, Biology (General), QH301-705.5, Biochemistry, QD415-436
وصف الملف: electronic resource
Relation: https://doaj.org/toc/2045-3701
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5دورية أكاديمية
المؤلفون: Stefano Magnati, Enrico Bracco
المصدر: Biophysica, Vol 4, Iss 2, Pp 158-167 (2024)
مصطلحات موضوعية: ubiquitin–proteasome system (UPS), protein quality control (PQC), intrinsically disordered regions (IDRs), Biology (General), QH301-705.5
وصف الملف: electronic resource
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6رسالة جامعية
المؤلفون: García Santamarina, Sarela
المساهمون: University/Department: Universitat Pompeu Fabra. Departament de Ciències Experimentals i de la Salut
مرشدي الرسالة: Hidalgo Hernando, Elena
المصدر: TDX (Tesis Doctorals en Xarxa)
مصطلحات موضوعية: Cysteine oxidation, Protein carbonylation, Methionine sulphoxide reductases, Protein quality control, H2O2 scavengers, Oxidación de cisteínas, Carbonilación de proteínas, Metionina sulfóxido reductases, Detoxificadores de H2O2, Control de calidad de proteínas
وصف الملف: application/pdf
URL الوصول: http://hdl.handle.net/10803/666989
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7دورية أكاديمية
المؤلفون: Attila Kolonics, Zoltán Bori, Ferenc Torma, Dora Abraham, János Fehér, Zsolt Radak
المصدر: BMC Neuroscience, Vol 24, Iss 1, Pp 1-12 (2023)
مصطلحات موضوعية: Bifidobacterium longum, Lactobacillus acidophilus, Alzheimer’s disease, Cognitive function, Gut microbiota, Mitochondrial protein quality control, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571, Neurophysiology and neuropsychology, QP351-495
وصف الملف: electronic resource
Relation: https://doaj.org/toc/1471-2202
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8دورية أكاديمية
المؤلفون: Kolonics, AttilaAff1, IDs1286802300836x_cor1, Bori, Zoltán, Torma, FerencAff1, Aff3, Aff4, Abraham, Dora, Fehér, János, Radak, Zsolt
المصدر: BMC Neuroscience. 24(1)
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9دورية أكاديمية
المؤلفون: Chawla, SrishtiAff1, Aff2, IDs1296402301242w_cor1, Ahmadpour, Doryaneh, Schneider, Kara L., Kumar, Navinder, Fischbach, Arthur, Molin, Mikael, Nystrom, ThomasAff1, IDs1296402301242w_cor7
المصدر: Cell Communication and Signaling. 21(1)
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10دورية أكاديمية
المصدر: Acta Myologica. 41(2)
مصطلحات موضوعية: Biomedical and Clinical Sciences, Cardiovascular Medicine and Haematology, Clinical Sciences, Neurosciences, Infectious Diseases, Charcot-Marie-Tooth Disease, Rare Diseases, 2.1 Biological and endogenous factors, Aetiology, Adaptor Proteins, Signal Transducing, Apoptosis Regulatory Proteins, Cardiomyopathy, Dilated, Humans, Leucine, Proline, Protein Aggregates, Bcl2-associated athanogene 3, Chaperone Assisted Selective Autophagy, Charcot-Marie-Tooth disease, Dilated Cardiomyopathy, IPV motif, oligomerization, protein aggregation, protein quality control, Cardiorespiratory Medicine and Haematology, Neurology & Neurosurgery, Cardiovascular medicine and haematology, Clinical sciences
وصف الملف: application/pdf
URL الوصول: https://escholarship.org/uc/item/183526d5