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1
المؤلفون: S.J. England, Thomas F. Scanlin, L. Uppaluri
المصدر: Journal of Cystic Fibrosis. 11:312-315
مصطلحات موضوعية: Lung Diseases, Pulmonary and Respiratory Medicine, medicine.medical_specialty, Pathology, Novel mutation, Delayed Diagnosis, Cystic Fibrosis, Cystic Fibrosis Transmembrane Conductance Regulator, India, Compound heterozygosity, Cystic fibrosis, Pulmonary function testing, FEV1/FVC ratio, Internal medicine, medicine, South Asian, Humans, Point Mutation, Genetic Predisposition to Disease, Pakistan, Pediatrics, Perinatology, and Child Health, Child, Retrospective Studies, Newborn screening, Bronchiectasis, biology, business.industry, CF, respiratory system, medicine.disease, Cystic fibrosis transmembrane conductance regulator, Lung disease, Pediatrics, Perinatology and Child Health, biology.protein, Sputum, Female, V456A, medicine.symptom, Tomography, X-Ray Computed, business
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2
المؤلفون: Barbara McLurkin, Antoinette Gardner, Luis Alba, Cynthia Moodie, Paula J. Anderson, Thomas Lahiri, Terry Spencer, Mary H. Wagner, Denise B. Angst, Cindy L. Capen, Samiya Razvi, John McNamara, Mary Sachs, Henry A. Wojtczak, Catherine Kier, Monica Leupold, Donna Lindner, William M. Gershan, Manisha Desai, Ran D. Anbar, Jackie Swartz, Juyan Zhou, Kimberly Jones, Larry Gann, Yvette LeFlore, Joanna Reboul, Dana G. Kissner, Kathleen Buckley, Jerri Gray, Janet Garbarz, Thomas F. Scanlin, Daniel B. Rosenbluth, Raj Padman, Nancy N. Dambro, Ofelia Vargas-Shiraishi, Andrew J. Lipton, Mary Ellen Freeman, Elizabeth Garber, Amy Szymanski, Robert Kaslovsky, Thomas M. Murphy, Lisa Saiman, Karen McCoy, Joel H. Schmidt, Beth D'Antonio, Bettina C. Hilman, Scott A. Schroeder, Barbara T. Jansma, Rodolfo Amaro, Howard B. Panitch, David A. Hicks, Teresa Carney, Michael J. Rock, Laurie Varlotta, Jane Quante, Lynne M. Quittell, Deborah Conklin, Michael D. Cabana, Scott H. Davis, Amanda Dove, Monya Rucker
المصدر: Pediatric Pulmonology. 43:900-907
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Self-efficacy, Infection Control, medicine.medical_specialty, Quality management, Cystic Fibrosis, business.industry, media_common.quotation_subject, Socialization, Psychological intervention, MEDLINE, Surgery, Hygiene, Family medicine, Pediatrics, Perinatology and Child Health, Health care, Humans, Medicine, Infection control, Guideline Adherence, Child, business, media_common
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3
المؤلفون: Thomas F. Scanlin, Virginia A. Stallings, Deborah A. Kawachak, Kathleen J. Propert, Nicolas Stettler, Babette S. Zemela, Lisa L. Boyle
المصدر: Annals of the New York Academy of Sciences. 904:406-409
مصطلحات موضوعية: Male, Radioisotope Dilution Technique, medicine.medical_specialty, Pediatrics, Cystic Fibrosis, Population, Body water, Growth, Cystic fibrosis, General Biochemistry, Genetics and Molecular Biology, Cohort Studies, History and Philosophy of Science, Reference Values, Internal medicine, medicine, Humans, Prospective Studies, Child, education, Prospective cohort study, education.field_of_study, Chemistry, General Neuroscience, Body Weight, Electric Conductivity, Nutritional status, Total body, Deuterium, medicine.disease, Skinfold Thickness, Skinfold thickness, Endocrinology, Child, Preschool, Body Composition, Female
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4
المؤلفون: Maria R. Mascarenhas, Joan I. Schall, Thomas F. Scanlin, Virginia A. Stallings, Babette S. Zemel, Jean Tomezsko, Nicolas Stettler
المصدر: Clinical Nutrition. 24:737-745
مصطلحات موضوعية: Adult, medicine.medical_specialty, Adolescent, Cystic Fibrosis, Nutritional Status, Critical Care and Intensive Care Medicine, Cystic fibrosis, Intestinal absorption, Pulmonary function testing, Internal medicine, medicine, Humans, Resting energy expenditure, Sexual Maturation, Child, Menarche, Nutrition and Dietetics, business.industry, Body Weight, Case-control study, Calorimetry, Indirect, Anthropometry, medicine.disease, Body Height, Respiratory Function Tests, Endocrinology, Intestinal Absorption, Case-Control Studies, Basal metabolic rate, Body Composition, Exocrine Pancreatic Insufficiency, Female, Basal Metabolism, Energy Metabolism, business
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5
المصدر: Current Organic Chemistry. 8:385-394
مصطلحات موضوعية: Pathology, medicine.medical_specialty, Chemistry, Glycobiology, Organic Chemistry, medicine, medicine.disease, Cystic fibrosis
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::8ee0197865a3997d96592715993e8716
https://doi.org/10.2174/1385272043485891 -
6
المؤلفون: Maria R. Mascarenhas, Eduardo Ruchelli, Binita M. Kamath, Jonathan E. Markowitz, Sumit Bhargava, Thomas F. Scanlin
المصدر: The Journal of Pediatrics. 143:115-119
مصطلحات موضوعية: Pediatrics, medicine.medical_specialty, Pathology, Pancreatic disease, Cystic Fibrosis, Duodenum, Biopsy, media_common.quotation_subject, Gene Expression, Cystic fibrosis, Diagnosis, Differential, Intestinal malabsorption, Chlorides, Malabsorption Syndromes, Dientamoebiasis, medicine, Humans, Point Mutation, Vitamin E, Amebicides, Girl, Sweat, media_common, Growth retardation, business.industry, Infant, medicine.disease, Failure to Thrive, Celiac Disease, Pediatrics, Perinatology and Child Health, Failure to thrive, Prothrombin Time, Female, medicine.symptom, business
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7
المؤلفون: Qian-Chun Yu, Mary Catherine Glick, Daniel T. Klink, Thomas F. Scanlin
المصدر: Molecular Therapy. 7:73-80
مصطلحات موضوعية: DNA, Complementary, Cystic Fibrosis, Endosome, media_common.quotation_subject, Lactose, Endocytosis, complex mixtures, Clathrin, Cell membrane, Complementary DNA, Drug Discovery, Genetics, medicine, Humans, Polylysine, Internalization, Molecular Biology, Cells, Cultured, media_common, Pharmacology, biology, Coated Pits, Cell-Membrane, Epithelial Cells, Receptor-mediated endocytosis, Transfection, Molecular biology, Trachea, Microscopy, Electron, medicine.anatomical_structure, biology.protein, bacteria, Molecular Medicine
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8Activity of fucosyltransferases and altered glycosylation in cystic fibrosis airway epithelial cells
المؤلفون: Lidia I. Stoykova, Aihui Liu, Mary Catherine Glick, Vaishali A. Kothari, Thomas F. Scanlin
المصدر: Biochimie. 83:743-747
مصطلحات موضوعية: Glycosylation, Fucosyltransferase, Cystic Fibrosis, Glycoconjugate, Cystic Fibrosis Transmembrane Conductance Regulator, Bronchi, Disaccharides, Biochemistry, Fucosyltransferases, chemistry.chemical_compound, Humans, Fucosidase, Cells, Cultured, Fucosylation, chemistry.chemical_classification, Membrane Glycoproteins, biology, Epithelial Cells, General Medicine, Transfection, Cell biology, chemistry, biology.protein, Nasal Cavity, Glycoprotein
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9
المصدر: Glycoconjugate Journal. 18:649-659
مصطلحات موضوعية: chemistry.chemical_classification, Glycosylation, Glycoconjugate, Cell Biology, Biology, medicine.disease, Biochemistry, Cystic fibrosis, Fucose, Microbiology, Cell biology, Sialic acid, chemistry.chemical_compound, chemistry, medicine, Glycoprotein, Molecular Biology, Selectin, Fucosylation
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10
المؤلفون: Mary Catherine Glick, Daniel T. Klink, Thomas F. Scanlin
المصدر: Glycoconjugate Journal. 18:731-740
مصطلحات موضوعية: Lung, Genetic enhancement, Immunogenicity, Cell Biology, Transfection, Biology, medicine.disease, Biochemistry, Cystic fibrosis, chemistry.chemical_compound, medicine.anatomical_structure, chemistry, Polylysine, Immunology, medicine, Receptor, Molecular Biology, Gene