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1دورية أكاديمية
المؤلفون: Tetsuro Matsuhashi, Takeya Sato, Shin-ichiro Kanno, Takehiro Suzuki, Akihiro Matsuo, Yuki Oba, Motoi Kikusato, Emi Ogasawara, Tai Kudo, Kosuke Suzuki, Osamu Ohara, Hiroko Shimbo, Fumika Nanto, Hiroaki Yamaguchi, Daisuke Saigusa, Yasuno Mukaiyama, Akiko Watabe, Koichi Kikuchi, Hisato Shima, Eikan Mishima, Yasutoshi Akiyama, Yoshitsugu Oikawa, HO Hsin-Jung, Yukako Akiyama, Chitose Suzuki, Mitsugu Uematsu, Masaki Ogata, Naonori Kumagai, Masaaki Toyomizu, Atsushi Hozawa, Nariyasu Mano, Yuji Owada, Setsuya Aiba, Teruyuki Yanagisawa, Yoshihisa Tomioka, Shigeo Kure, Sadayoshi Ito, Kazuto Nakada, Ken-ichiro Hayashi, Hitoshi Osaka, Takaaki Abe
المصدر: EBioMedicine, Vol 20, Iss C, Pp 27-38 (2017)
مصطلحات موضوعية: MA-5, Mitochondrial disease, ATPase dimer formation, Supercomplex, GDF-15, Medicine, Medicine (General), R5-920
وصف الملف: electronic resource
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المؤلفون: Yasutoshi Akiyama, Emi Ogasawara, Teruyuki Yanagisawa, Naonori Kumagai, Nariyasu Mano, Hitoshi Osaka, Mitsugu Uematsu, Daisuke Saigusa, Yuji Owada, Takehiro Suzuki, Atsushi Hozawa, Fumika Nanto, Motoi Kikusato, Tai Kudo, Ken-ichiro Hayashi, Takaaki Abe, Tetsuro Matsuhashi, Yuki Oba, Yoshihisa Tomioka, Yasuno Mukaiyama, Sadayoshi Ito, Takeya Sato, Kosuke Suzuki, Setsuya Aiba, Yukako Akiyama, Shin Ichiro Kanno, Akihiro Matsuo, Eikan Mishima, Hiroko Shimbo, Chitose Suzuki, Kazuto Nakada, Akiko Watabe, Masaki Ogata, Hiroaki Yamaguchi, Masaaki Toyomizu, Hisato Shima, Shigeo Kure, Yoshitsugu Oikawa, H. O. Hsin-Jung, Koichi Kikuchi, Osamu Ohara
المصدر: EBioMedicine
EBioMedicine, Vol 20, Iss C, Pp 27-38 (2017)مصطلحات موضوعية: 0301 basic medicine, Mitochondrial Diseases, OXPHOS, oxidative phosphorylation, lcsh:Medicine, Mitochondrion, Mitochondrial Dynamics, CPEO, chronic progressive external ophthalmoplegia, BSO, l-buthionine-(S,R)-sulfoximine, Mice, MELAS, myopathy encephalopathy lactic acidosis and stroke-like episodes, chemistry.chemical_compound, Adenosine Triphosphate, OCR, oxygen consumption rate, Membrane Potential, Mitochondrial, lcsh:R5-920, Organelle Biogenesis, ATP synthase, biology, MA-5, 4-(2,4-difluorophenyl)-2-(1H-indole-3-yl)-4-oxobutanoic acid, General Medicine, Mitochondrial Proton-Translocating ATPases, Prognosis, ECAR, extra-cellular acidification rate, Phenylbutyrates, Mitochondria, Cell biology, MA-5, Biochemistry, ATPase dimer formation, lcsh:Medicine (General), Protein Binding, Research Paper, LHON, Leber hereditary optic neuropathy, Supercomplex, Growth Differentiation Factor 15, Cell Survival, Mitochondrial disease, Oxidative phosphorylation, Protective Agents, DNA, Mitochondrial, General Biochemistry, Genetics and Molecular Biology, Cell Line, 03 medical and health sciences, medicine, Animals, Humans, Indoleacetic Acids, lcsh:R, Fibroblasts, medicine.disease, GDF-15, Fibroblast Growth Factors, Disease Models, Animal, 030104 developmental biology, Mitochondrial biogenesis, chemistry, Multiprotein Complexes, Mutation, ETC, electron transfer complex, biology.protein, FCCP, carbonyl cyanide-p-trifluoromethoxyphenylhydrazone, Carbonyl cyanide-p-trifluoromethoxyphenylhydrazone, Protein Multimerization, Chronic progressive external ophthalmoplegia, MINOS, mitofilin/mitochondrial inner membrane organizing system, Biomarkers, KSS, Kearns-Sayre syndrome
وصف الملف: application/pdf