المؤلفون: Lee EJ; Department of Pediatrics, Severance Hospital, Yonsei University College of Medicine, Seoul, Korea., Woo MH; Department of Pediatrics, Seoul National University Children's Hospital, Seoul National University College of Medicine, Seoul, Korea., Moon JS; Department of Pediatrics, Seoul National University Children's Hospital, Seoul National University College of Medicine, Seoul, Korea., Ko JS; Department of Pediatrics, Seoul National University Children's Hospital, Seoul National University College of Medicine, Seoul, Korea. kojs@snu.ac.kr.

المصدر: Orphanet journal of rare diseases [Orphanet J Rare Dis] 2024 Jul 09; Vol. 19 (1), pp. 261. Date of Electronic Publication: 2024 Jul 09.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: BioMed Central Country of Publication: England NLM ID: 101266602 Publication Model: Electronic Cited Medium: Internet ISSN: 1750-1172 (Electronic) Linking ISSN: 17501172 NLM ISO Abbreviation: Orphanet J Rare Dis Subsets: MEDLINE

مواضيع طبية MeSH: Hepatolenticular Degeneration*/drug therapy , Hepatolenticular Degeneration*/metabolism , Penicillamine*/therapeutic use , Penicillamine*/adverse effects , Trientine*/therapeutic use , Trientine*/adverse effects , Zinc*/therapeutic use, Humans ; Child ; Male ; Female ; Adolescent ; Child, Preschool ; Chelating Agents/therapeutic use ; Treatment Outcome

المؤلفون: Kirk FT; Department of Hepatology and Gastroenterology, Aarhus University Hospital, Aarhus, Denmark., Munk DE; Department of Hepatology and Gastroenterology, Aarhus University Hospital, Aarhus, Denmark., Swenson ES; Alexion, AstraZeneca Rare Disease, Boston, Massachusetts, USA., Quicquaro AM; Alexion, AstraZeneca Rare Disease, Boston, Massachusetts, USA., Vendelbo MH; Department of Nuclear Medicine & PET-center, Aarhus University Hospital, Aarhus, Denmark.; Department of Biomedicine, Aarhus University, Aarhus, Denmark., Schilsky ML; Department of Medicine, Section of Digestive Diseases, Yale School of Medicine, New Haven, Connecticut, USA.; Department of Surgery, Section of Transplant and Immunology, Yale School of Medicine, New Haven, Connecticut, USA., Ott P; Department of Hepatology and Gastroenterology, Aarhus University Hospital, Aarhus, Denmark., Sandahl TD; Department of Hepatology and Gastroenterology, Aarhus University Hospital, Aarhus, Denmark.

المصدر: Hepatology (Baltimore, Md.) [Hepatology] 2024 May 01; Vol. 79 (5), pp. 1065-1074. Date of Electronic Publication: 2023 Dec 13.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: Wolters Kluwer Health, Inc Country of Publication: United States NLM ID: 8302946 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1527-3350 (Electronic) Linking ISSN: 02709139 NLM ISO Abbreviation: Hepatology Subsets: MEDLINE

مواضيع طبية MeSH: Penicillamine*/pharmacology , Penicillamine*/therapeutic use , Hepatolenticular Degeneration*/drug therapy, Humans ; Trientine/pharmacology ; Trientine/therapeutic use ; Copper ; Positron Emission Tomography Computed Tomography ; Copper Radioisotopes/therapeutic use ; Positron-Emission Tomography

المؤلفون: Wang X; School of Bioengineering, Zunyi Medical University, Jinwan Road No. 368, Zhuhai, 519090, Guangdong, China., Wu H; School of Bioengineering, Zunyi Medical University, Jinwan Road No. 368, Zhuhai, 519090, Guangdong, China., Wong KH; State Key Laboratory of Quality Research in Chinese Medicine, Institute of Chinese Medical Sciences, University of Macau, Macau, 999078, China., Wang Y; School of Bioengineering, Zunyi Medical University, Jinwan Road No. 368, Zhuhai, 519090, Guangdong, China., Chen B; School of Bioengineering, Zunyi Medical University, Jinwan Road No. 368, Zhuhai, 519090, Guangdong, China., Feng K; School of Bioengineering, Zunyi Medical University, Jinwan Road No. 368, Zhuhai, 519090, Guangdong, China. fengk@zmu.edu.cn.

المصدر: Microbial cell factories [Microb Cell Fact] 2023 Jul 28; Vol. 22 (1), pp. 139. Date of Electronic Publication: 2023 Jul 28.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: BioMed Central Country of Publication: England NLM ID: 101139812 Publication Model: Electronic Cited Medium: Internet ISSN: 1475-2859 (Electronic) Linking ISSN: 14752859 NLM ISO Abbreviation: Microb Cell Fact Subsets: MEDLINE

مواضيع طبية MeSH: Trientine* , Triterpenes*/metabolism, Biotransformation

SCR Organism: Ganoderma sessile

المؤلفون: Farrant J; BHF Manchester Centre for Heart and Lung Magnetic Resonance Research, Manchester University NHS Foundation Trust, Manchester, UK.; Division of Cardiovascular Sciences, School of Medical Sciences, Faculty of Biology, Medicine and Health, Manchester Academic Health Science Centre, University of Manchester, Manchester, UK., Dodd S; Liverpool Clinical Trials Centre, University of Liverpool, Liverpool, UK.; Department of Health Data Sciences, Faculty of Health and Life Sciences, University of Liverpool, Liverpool, UK., Vaughan C; Liverpool Clinical Trials Centre, University of Liverpool, Liverpool, UK., Reid A; BHF Manchester Centre for Heart and Lung Magnetic Resonance Research, Manchester University NHS Foundation Trust, Manchester, UK., Schmitt M; BHF Manchester Centre for Heart and Lung Magnetic Resonance Research, Manchester University NHS Foundation Trust, Manchester, UK., Garratt C; BHF Manchester Centre for Heart and Lung Magnetic Resonance Research, Manchester University NHS Foundation Trust, Manchester, UK., Akhtar M; Division of Cardiovascular Medicine, University of Oxford, Oxford, UK.; NIHR Oxford Biomedical Research Centre, Oxford University Hospitals NHS Foundation Trust, Oxford, UK., Mahmod M; Division of Cardiovascular Medicine, University of Oxford, Oxford, UK.; NIHR Oxford Biomedical Research Centre, Oxford University Hospitals NHS Foundation Trust, Oxford, UK., Neubauer S; Division of Cardiovascular Medicine, University of Oxford, Oxford, UK.; NIHR Oxford Biomedical Research Centre, Oxford University Hospitals NHS Foundation Trust, Oxford, UK., Cooper RM; Institute of Cardiovascular Medicine and Science, Liverpool Heart and Chest Hospital, Liverpool, UK.; School of Sport and Exercise Sciences, Liverpool John Moores University, Liverpool, UK., Prasad SK; Cardiology, Royal Brompton and Harefield Hospitals, London, UK., Singh A; Department of Cardiovascular Sciences, University of Leicester and the NIHR Leicester Biomedical Research Centre, Glenfield Hospital, Leicester, UK., Valkovič L; Division of Cardiovascular Medicine, University of Oxford, Oxford, UK.; Department of Imaging Methods, Institute of Measurement Science, Slovak Academy of Sciences, Bratislava, Slovakia., Raman B; Division of Cardiovascular Medicine, University of Oxford, Oxford, UK.; NIHR Oxford Biomedical Research Centre, Oxford University Hospitals NHS Foundation Trust, Oxford, UK., Ashkir Z; Division of Cardiovascular Medicine, University of Oxford, Oxford, UK.; NIHR Oxford Biomedical Research Centre, Oxford University Hospitals NHS Foundation Trust, Oxford, UK., Clayton D; Liverpool Clinical Trials Centre, University of Liverpool, Liverpool, UK.; Department of Health Data Sciences, Faculty of Health and Life Sciences, University of Liverpool, Liverpool, UK., Baroja O; BHF Manchester Centre for Heart and Lung Magnetic Resonance Research, Manchester University NHS Foundation Trust, Manchester, UK., Duran B; BHF Manchester Centre for Heart and Lung Magnetic Resonance Research, Manchester University NHS Foundation Trust, Manchester, UK., Spowart C; Liverpool Clinical Trials Centre, University of Liverpool, Liverpool, UK., Bedson E; Liverpool Clinical Trials Centre, University of Liverpool, Liverpool, UK., Naish JH; BHF Manchester Centre for Heart and Lung Magnetic Resonance Research, Manchester University NHS Foundation Trust, Manchester, UK.; Division of Cardiovascular Sciences, School of Medical Sciences, Faculty of Biology, Medicine and Health, Manchester Academic Health Science Centre, University of Manchester, Manchester, UK., Harrington C; SAS Trace Element Laboratory, Surrey Research Park, Guildford, UK.; Royal Surrey NHS Foundation Trust, Guildford, UK., Miller CA; BHF Manchester Centre for Heart and Lung Magnetic Resonance Research, Manchester University NHS Foundation Trust, Manchester, UK christopher.miller@manchester.ac.uk.; Division of Cardiovascular Sciences, School of Medical Sciences, Faculty of Biology, Medicine and Health, Manchester Academic Health Science Centre, University of Manchester, Manchester, UK.; Wellcome Centre for Cell-Matrix Research, Division of Cell-Matrix Biology & Regenerative Medicine, School of Biology, Faculty of Biology, Medicine & Health, Manchester Academic Health Science Centre, University of Manchester, Oxford Road, Manchester, M13 9PT, UK.

مؤلفون مشاركون: TEMPEST investigators

المصدر: Heart (British Cardiac Society) [Heart] 2023 Jul 12; Vol. 109 (15), pp. 1175-1182. Date of Electronic Publication: 2023 Jul 12.

نوع المنشور: Randomized Controlled Trial; Multicenter Study; Clinical Trial, Phase II; Journal Article; Research Support, Non-U.S. Gov't

بيانات الدورية: Publisher: BMJ Pub. Group Country of Publication: England NLM ID: 9602087 Publication Model: Electronic Cited Medium: Internet ISSN: 1468-201X (Electronic) Linking ISSN: 13556037 NLM ISO Abbreviation: Heart Subsets: MEDLINE

مواضيع طبية MeSH: Trientine*/therapeutic use , Cardiomyopathy, Hypertrophic*/diagnosis , Cardiomyopathy, Hypertrophic*/drug therapy , Cardiomyopathy, Hypertrophic*/complications, Humans ; Copper/therapeutic use ; Heart ; Hypertrophy, Left Ventricular/drug therapy ; Hypertrophy, Left Ventricular/etiology ; Hypertrophy, Left Ventricular/prevention & control ; Fibrosis

مؤلفون مشاركون: Workplace Environmental Exposure Level (WEEL) Committee, Occupational Alliance for Risk Science (OARS), Toxicology Excellence for Risk Assessment (TERA); Cincinnati, OH, USA.

المصدر: Toxicology and industrial health [Toxicol Ind Health] 2023 Apr; Vol. 39 (4), pp. 183-187. Date of Electronic Publication: 2023 Mar 20.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: SAGE Publications Country of Publication: England NLM ID: 8602702 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1477-0393 (Electronic) Linking ISSN: 07482337 NLM ISO Abbreviation: Toxicol Ind Health Subsets: MEDLINE

مواضيع طبية MeSH: Trientine*/therapeutic use , Trientine*/toxicity , Hepatolenticular Degeneration*, Humans ; Animals ; Mice ; Copper ; No-Observed-Adverse-Effect Level

المؤلفون: Mohr I; Department of Internal Medicine IV, Department of Gastroenterology, University Hospital Heidelberg, Heidelberg, Germany., Bourhis H; Medizinische Klinik und Poliklinik II, Hospital of the Ludwig-Maximilians University Munich, Munich, Germany., Woimant F; Department of Neurology, Hôpital Lariboisière, Paris, France., Obadia MA; Department of Neurology, Rothschild Foundation Hospital, National reference center for Wilson disease, Paris, France., Morgil M; Department of Internal Medicine, Salem Hospital Heidelberg, Heidelberg, Germany., Morvan E; Department of Neurology, Rothschild Foundation Hospital, National reference center for Wilson disease, Paris, France., Merle U; Department of Internal Medicine IV, Department of Gastroenterology, University Hospital Heidelberg, Heidelberg, Germany., Denk G; Medizinische Klinik und Poliklinik II, Hospital of the Ludwig-Maximilians University Munich, Munich, Germany., Poujois A; Department of Neurology, Rothschild Foundation Hospital, National reference center for Wilson disease, Paris, France., Weiss KH; Department of Internal Medicine, Salem Hospital Heidelberg, Heidelberg, Germany.

المصدر: Journal of gastroenterology and hepatology [J Gastroenterol Hepatol] 2023 Feb; Vol. 38 (2), pp. 219-224. Date of Electronic Publication: 2022 Nov 12.

نوع المنشور: Multicenter Study; Journal Article

بيانات الدورية: Publisher: Blackwell Scientific Publications Country of Publication: Australia NLM ID: 8607909 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1440-1746 (Electronic) Linking ISSN: 08159319 NLM ISO Abbreviation: J Gastroenterol Hepatol Subsets: MEDLINE

مواضيع طبية MeSH: Trientine*/adverse effects , Hepatolenticular Degeneration*/drug therapy, Humans ; Young Adult ; Adult ; Copper ; Retrospective Studies ; Chelating Agents/adverse effects ; Transaminases

المؤلفون: Zhu Z; State Key Laboratory Basis of Xinjiang Indigenous Medicinal Plants Resource Utilization, and the Key Laboratory of Plant Resources and Chemistry of Arid Zone, Xinjiang Technical Institute of Physics and Chemistry, Chinese Academy of Sciences, Urumqi, 830011, China; University of the Chinese Academy of Sciences, Beijing, 100039, China., Ablajan T; State Key Laboratory Basis of Xinjiang Indigenous Medicinal Plants Resource Utilization, and the Key Laboratory of Plant Resources and Chemistry of Arid Zone, Xinjiang Technical Institute of Physics and Chemistry, Chinese Academy of Sciences, Urumqi, 830011, China., Zang D; State Key Laboratory Basis of Xinjiang Indigenous Medicinal Plants Resource Utilization, and the Key Laboratory of Plant Resources and Chemistry of Arid Zone, Xinjiang Technical Institute of Physics and Chemistry, Chinese Academy of Sciences, Urumqi, 830011, China., Aisa HA; State Key Laboratory Basis of Xinjiang Indigenous Medicinal Plants Resource Utilization, and the Key Laboratory of Plant Resources and Chemistry of Arid Zone, Xinjiang Technical Institute of Physics and Chemistry, Chinese Academy of Sciences, Urumqi, 830011, China; University of the Chinese Academy of Sciences, Beijing, 100039, China. Electronic address: haji@ms.xjb.ac.cn.

المصدر: Phytochemistry [Phytochemistry] 2024 Apr; Vol. 220, pp. 114019. Date of Electronic Publication: 2024 Feb 10.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: Elsevier Country of Publication: England NLM ID: 0151434 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1873-3700 (Electronic) Linking ISSN: 00319422 NLM ISO Abbreviation: Phytochemistry Subsets: MEDLINE

مواضيع طبية MeSH: Artemisia*/chemistry , Sesquiterpenes*/pharmacology , Sesquiterpenes*/chemistry , Asteraceae*/chemistry, beta Catenin ; Glycogen Synthase Kinase 3 beta ; Interleukin-6 ; Proto-Oncogene Proteins c-akt ; Trientine ; Sesquiterpenes, Guaiane/pharmacology ; Sesquiterpenes, Guaiane/chemistry ; Anti-Inflammatory Agents ; RNA, Messenger ; Lactones/pharmacology ; Lactones/chemistry ; Molecular Structure

المؤلفون: Zakaria DS; Faculty of Chemical Engineering & Technology, Universiti Malaysia Perlis, Kompleks Pusat Pengajian Jejawi, Arau, 02600, Perlis, Malaysia., Rozi SKM; Faculty of Chemical Engineering & Technology, Universiti Malaysia Perlis, Kompleks Pusat Pengajian Jejawi, Arau, 02600, Perlis, Malaysia. khalijahrozi@unimap.edu.my.; Centre of Excellence for Biomass Utilization, Universiti Malaysia Perlis (UniMAP), Perlis, Malaysia. khalijahrozi@unimap.edu.my., Halim HNA; Faculty of Chemical Engineering & Technology, Universiti Malaysia Perlis, Kompleks Pusat Pengajian Jejawi, Arau, 02600, Perlis, Malaysia.; Centre of Excellence for Biomass Utilization, Universiti Malaysia Perlis (UniMAP), Perlis, Malaysia., Mohamad S; Department of Chemistry, Faculty of Science, University of Malaya, 50603, Kuala Lumpur, Malaysia., Zheng GK; Faculty of Chemical Engineering & Technology, Universiti Malaysia Perlis, Kompleks Pusat Pengajian Jejawi, Arau, 02600, Perlis, Malaysia.

المصدر: Environmental science and pollution research international [Environ Sci Pollut Res Int] 2024 Mar; Vol. 31 (11), pp. 16309-16327. Date of Electronic Publication: 2024 Feb 05.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: Springer Country of Publication: Germany NLM ID: 9441769 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1614-7499 (Electronic) Linking ISSN: 09441344 NLM ISO Abbreviation: Environ Sci Pollut Res Int Subsets: MEDLINE

مواضيع طبية MeSH: Carbon Dioxide*/chemistry , Cocos*, Porosity ; Charcoal ; Spectroscopy, Fourier Transform Infrared ; Trientine ; Adsorption ; Kinetics

المؤلفون: Peng X; School of Chemistry and Chemical Engineering, Wuhan Textile University, China., Yan J; School of Chemistry and Chemical Engineering, Wuhan Textile University, China., He C; School of Chemistry and Chemical Engineering, Wuhan Textile University, China., Liu R; School of Chemistry and Chemical Engineering, Wuhan Textile University, China., Liu Y; Hubei Key Laboratory of Biomass Fibers and Eco-Dyeing and Finishing, Wuhan Textile University, 430200, China; School of Chemistry and Chemical Engineering, Wuhan Textile University, China. Electronic address: liuyangshuo8858@163.com.

المصدر: International journal of biological macromolecules [Int J Biol Macromol] 2024 Mar; Vol. 261 (Pt 2), pp. 129741. Date of Electronic Publication: 2024 Jan 26.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: Elsevier Country of Publication: Netherlands NLM ID: 7909578 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1879-0003 (Electronic) Linking ISSN: 01418130 NLM ISO Abbreviation: Int J Biol Macromol Subsets: MEDLINE

مواضيع طبية MeSH: Chitosan* , Metals, Heavy* , Water Pollutants, Chemical*/analysis , Graphite*, Cadmium ; Trientine ; Lead ; Adsorption ; Ions ; Kinetics

المؤلفون: Yen PH; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Tai BH; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam.; Graduate University of Science and Technology, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Hoang NH; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Dung DT; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Nhiem NX; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam.; Graduate University of Science and Technology, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Yen DTH; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Huong PTT; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Dung NV; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Hang DTT; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Ha NT; Drug, Comestic and Food Quality Control Center of Ha Tinh Province, 46 Ha Hoang street, Thach Trung, Ha Tinh, 480000, Vietnam., Trang DT; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam., Thu VK; Faculty of Basic Sciences, Hanoi University of Mining and Geology, Hanoi, 10000, Vietnam., Kiem PV; Institute of Marine Biochemistry, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam.; Graduate University of Science and Technology, VAST, 18 Hoang Quoc Viet, Cau Giay, Hanoi, 10072, Vietnam.

المصدر: Chemistry & biodiversity [Chem Biodivers] 2024 Feb; Vol. 21 (2), pp. e202301963. Date of Electronic Publication: 2024 Jan 04.

نوع المنشور: Journal Article

بيانات الدورية: Publisher: Verlag Helvetica Chimica Acta Country of Publication: Switzerland NLM ID: 101197449 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1612-1880 (Electronic) Linking ISSN: 16121872 NLM ISO Abbreviation: Chem Biodivers Subsets: MEDLINE

مواضيع طبية MeSH: Lipopolysaccharides*/pharmacology , Saponins*/pharmacology , Saponins*/chemistry , Dracaena*, Mice ; Animals ; Nitric Oxide ; RAW 264.7 Cells ; Trientine ; Molecular Structure

SCR Organism: Dracaena cambodiana