دورية أكاديمية

Association of amyloidosis cutis dyschromica and familial Mediterranean fever

التفاصيل البيبلوغرافية
العنوان: Association of amyloidosis cutis dyschromica and familial Mediterranean fever
المؤلفون: Asli Akin Belli, Asude Kara, Yelda Dere, Nevin Yilmaz
المصدر: Anais Brasileiros de Dermatologia, Vol 92, Iss 5 suppl 1, Pp 21-23 (2017)
بيانات النشر: Sociedade Brasileira de Dermatologia, 2017.
سنة النشر: 2017
المجموعة: LCC:Dermatology
مصطلحات موضوعية: Amyloidosis, Autoimmune diseases, Familial mediterranean fever, Pigmentation disorders, Dermatology, RL1-803
الوصف: Abstract: Amyloidosis cutis dyschromica is a rare type of primary cutaneous amyloidosis characterized by reticulate hyper-pigmentation with discrete hypopigmented macules. Up to date, about 50 cases of amyloidosis cutis dyschromica have been reported and the majority are familial cases of Asian ethnicity. Various diseases, particularly autoimmune diseases such as systemic sclerosis and systemic lupus erythematosus, have been associated with amyloidosis cutis dyschromica. Herein, we report a case of amyloidosis cutis dyschromica accompanying familial Mediterranean fever with a delayed diagnosis of 40 years. To the best of our knowledge, this is the first report of the association of amyloidosis cutis dyschromica and familial mediterranean fever.
نوع الوثيقة: article
وصف الملف: electronic resource
اللغة: English
Portuguese
تدمد: 0365-0596
1806-4841
Relation: http://www.scielo.br/pdf/abd/v92n5s1/0365-0596-abd-92-05-s1-0021.pdf; http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017001100021&tlng=en; https://doaj.org/toc/0365-0596
DOI: 10.1590/abd1806-4841.20176114
URL الوصول: https://doaj.org/article/47e2bad26f9047abb68e340905c24d4e
رقم الأكسشن: edsdoj.47e2bad26f9047abb68e340905c24d4e
قاعدة البيانات: Directory of Open Access Journals
الوصف
تدمد:03650596
18064841
DOI:10.1590/abd1806-4841.20176114