دورية أكاديمية
Association of amyloidosis cutis dyschromica and familial Mediterranean fever
العنوان: | Association of amyloidosis cutis dyschromica and familial Mediterranean fever |
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المؤلفون: | Asli Akin Belli, Asude Kara, Yelda Dere, Nevin Yilmaz |
المصدر: | Anais Brasileiros de Dermatologia, Vol 92, Iss 5 suppl 1, Pp 21-23 (2017) |
بيانات النشر: | Sociedade Brasileira de Dermatologia, 2017. |
سنة النشر: | 2017 |
المجموعة: | LCC:Dermatology |
مصطلحات موضوعية: | Amyloidosis, Autoimmune diseases, Familial mediterranean fever, Pigmentation disorders, Dermatology, RL1-803 |
الوصف: | Abstract: Amyloidosis cutis dyschromica is a rare type of primary cutaneous amyloidosis characterized by reticulate hyper-pigmentation with discrete hypopigmented macules. Up to date, about 50 cases of amyloidosis cutis dyschromica have been reported and the majority are familial cases of Asian ethnicity. Various diseases, particularly autoimmune diseases such as systemic sclerosis and systemic lupus erythematosus, have been associated with amyloidosis cutis dyschromica. Herein, we report a case of amyloidosis cutis dyschromica accompanying familial Mediterranean fever with a delayed diagnosis of 40 years. To the best of our knowledge, this is the first report of the association of amyloidosis cutis dyschromica and familial mediterranean fever. |
نوع الوثيقة: | article |
وصف الملف: | electronic resource |
اللغة: | English Portuguese |
تدمد: | 0365-0596 1806-4841 |
Relation: | http://www.scielo.br/pdf/abd/v92n5s1/0365-0596-abd-92-05-s1-0021.pdf; http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017001100021&tlng=en; https://doaj.org/toc/0365-0596 |
DOI: | 10.1590/abd1806-4841.20176114 |
URL الوصول: | https://doaj.org/article/47e2bad26f9047abb68e340905c24d4e |
رقم الأكسشن: | edsdoj.47e2bad26f9047abb68e340905c24d4e |
قاعدة البيانات: | Directory of Open Access Journals |
تدمد: | 03650596 18064841 |
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DOI: | 10.1590/abd1806-4841.20176114 |