دورية أكاديمية

Hypohidrotic (Anhidrotic) Ectodermal dysplasia - A rare cause of childhood Atrophic Rhinitis".

التفاصيل البيبلوغرافية
العنوان: Hypohidrotic (Anhidrotic) Ectodermal dysplasia - A rare cause of childhood Atrophic Rhinitis".
المؤلفون: Das Gupta S; Department of Otorhinolaryngology, Shri Vasantrao Naik Government Medical College, Yavatmal., Joshi SV, Lanjewar K, Murkey N
المصدر: Indian journal of otolaryngology and head and neck surgery : official publication of the Association of Otolaryngologists of India [Indian J Otolaryngol Head Neck Surg] 2006 Apr; Vol. 58 (2), pp. 202-4.
نوع المنشور: Journal Article
اللغة: English
بيانات الدورية: Publisher: Springer Country of Publication: India NLM ID: 9422551 Publication Model: Print Cited Medium: Print ISSN: 2231-3796 (Print) Linking ISSN: 22313796 NLM ISO Abbreviation: Indian J Otolaryngol Head Neck Surg Subsets: PubMed not MEDLINE
أسماء مطبوعة: Publication: <2007>- : New Delhi : Springer
Original Publication: Calcutta : B.K. Roy Chaudhuri, [1993-
مستخلص: Hypohydrotic (Anhidrotic) Ectodermal dysplasia is a rare hereditary genodermatosis characterized by a triad of defects including hypohidrosis hypotrichosis and anomalous dentition. Mainly ectodermal structures are involved such as epidermis and its annexes (hair & nails), although non-ecotodermal tissue may also became involved(1). ENT involvement in such cases is a consequence of the defect involving the eccrine and sebaceous glands. A case of a 3 years old female child suffering from hypohidrotic ectodermal dysplasia with features of Atrophic Rhinitis from infancy & early childhood is reported here. Management of these patients is mainly supportive and otolaryngologist is a vital component of the health care team managing such patients.
التعليقات: Erratum in: Indian J Otolaryngol Head Neck Surg. 2006 Dec;58(4):351. Dasgupta, K S [corrected to Das Gupta, S]; Lanjewar, Kanchan [added]; Murkey, Neeraj [added]; Gawarle, Surendra H [removed]; Murkey, N S N [removed]; Avad, Atul [removed].
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فهرسة مساهمة: Keywords: Atrophic Rhinitis; Hypohidrotic Ectodermal Dysplasia
تواريخ الأحداث: Date Created: 20121103 Date Completed: 20121105 Latest Revision: 20211021
رمز التحديث: 20231215
مُعرف محوري في PubMed: PMC3450788
DOI: 10.1007/BF03050792
PMID: 23120289
قاعدة البيانات: MEDLINE
الوصف
تدمد:2231-3796
DOI:10.1007/BF03050792