Sarcomatoid Renal Cell Carcinoma in an Adolescent with Sickle Cell Anaemia.

التفاصيل البيبلوغرافية
العنوان: Sarcomatoid Renal Cell Carcinoma in an Adolescent with Sickle Cell Anaemia.
المؤلفون: Ahmad HR; Haematology/Oncology Unit, Department of Paediatrics, Ahmadu Bello University/Teaching Hospital, Zaria, Nigeria., Faruk JA; Haematology/Oncology Unit, Department of Paediatrics, Ahmadu Bello University/Teaching Hospital, Zaria, Nigeria., Bugaje MA; Nephrology Unit, Department of Paediatrics, Ahmadu Bello University/Teaching Hospital, Zaria, Nigeria., Solomon A; Haematology/Oncology Unit, Department of Paediatrics, Ahmadu Bello University/Teaching Hospital, Zaria, Nigeria., Samaila MOA; Department of Pathology, Ahmadu Bello University/Teaching Hospital, Zaria, Nigeria., Akuse RM; Nephrology Unit, Department of Paediatrics, Ahmadu Bello University/Teaching Hospital, Zaria, Nigeria.
المصدر: Case reports in oncological medicine [Case Rep Oncol Med] 2017; Vol. 2017, pp. 2129450. Date of Electronic Publication: 2017 Oct 31.
نوع المنشور: Case Reports
اللغة: English
بيانات الدورية: Publisher: Hindawi Pub. Corp Country of Publication: United States NLM ID: 101581035 Publication Model: Print-Electronic Cited Medium: Print ISSN: 2090-6706 (Print) NLM ISO Abbreviation: Case Rep Oncol Med Subsets: PubMed not MEDLINE
أسماء مطبوعة: Original Publication: New York, NY : Hindawi Pub. Corp.
مستخلص: Malignancies have been reported to occur in people with sickle cell disease. Renal medullary carcinoma (RMC), also tagged seventh sickle cell nephropathy, is an aggressive cancer seen almost exclusively in people with sickle cell disease with more than 160 cases reported worldwide, but only few cases were reported in patients with sickle cell anaemia (HBSS) and from Nigeria. Sarcomatoid renal cell carcinoma is a renal tumour of any histologic variant containing foci of high-grade malignant spindle cells. We report an adolescent girl with sickle cell anaemia (HBSS) who presented with left renal tumour, histology of which confirmed a diagnosis of sarcomatoid renal cell carcinoma (sRCC). Surgical debulking and palliative care with chemotherapy were given, and she demised 10 months after. The rarity of the case and challenges of managing a cancer in the background of a chronic haematologic disorder are highlighted.
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تواريخ الأحداث: Date Created: 20171212 Latest Revision: 20201001
رمز التحديث: 20240628
مُعرف محوري في PubMed: PMC5684584
DOI: 10.1155/2017/2129450
PMID: 29225982
قاعدة البيانات: MEDLINE
الوصف
تدمد:2090-6706
DOI:10.1155/2017/2129450