دورية أكاديمية
أعرض في EDS

A case report of pulmonary artery sling and situs inversus incompletes.

التفاصيل البيبلوغرافية
العنوان: A case report of pulmonary artery sling and situs inversus incompletes.
المؤلفون: Xu Y; Department of Pulmonology., Xu D; Department of Pulmonology., Cheng B; Department of Pulmonology., Tang L; Department of Pulmonology., Chen Z; Department of Pulmonology., Du L; Department of Neonatology, The Children's Hospital, Zhejiang University School of Medicine, National Clinical Research Center for Child Health, Hangzhou, Zhejiang Province, China.
المصدر: Medicine [Medicine (Baltimore)] 2021 Jan 22; Vol. 100 (3), pp. e24021.
نوع المنشور: Case Reports; Journal Article
اللغة: English
بيانات الدورية: Publisher: Lippincott Williams & Wilkins Country of Publication: United States NLM ID: 2985248R Publication Model: Print Cited Medium: Internet ISSN: 1536-5964 (Electronic) Linking ISSN: 00257974 NLM ISO Abbreviation: Medicine (Baltimore) Subsets: MEDLINE
أسماء مطبوعة: Original Publication: Hagerstown, Md : Lippincott Williams & Wilkins
مواضيع طبية MeSH: Aorta, Thoracic/*abnormalities , Heart Defects, Congenital/*complications , Lung/*abnormalities , Pulmonary Artery/*abnormalities , Situs Inversus/*complications , Tracheal Stenosis/*congenital, Abnormalities, Multiple/surgery ; Child ; Female ; Humans
مستخلص: Rationale: Pulmonary artery sling (PAS) is a rare congenital anomaly. Associated airway anomalies and/or those of the cardiovascular system are present in about half the patients. Situs inversus is a rare disease in which organs of the chest and/or abdomen are arranged in a mirror image reversal of their normal position. Herein, we report a rare case of pulmonary artery sling and situs inversus incompletus, which has not yet been reported.
Patient Concerns: A 10-year-old girl was admitted because of heart murmur for more than 9 years. On physical examination, the second heart sound was prominent, and a grade 2/6 systolic murmur was heard at the left mid-sternal border. Echocardiography revealed PAS and atrial septal defect (8.6 mm). A chest computer tomography angiograph demonstrated that she had lung inversus, right aortic arch, and right lung hypoplasia in addition to PAS, with a normal positioning of the heart. The PAS intersected and twisted across the bronchus, which was obviously narrowed. The PAS was type II B, since the carina was at the T6 level without a separate right upper lobe bronchus.
Diagnoses: Her final diagnosis was that of PAS, tracheal stenosis, situs inversus incompletus, right lung hypoplasia, right aortic arch, ASD and PDA.
Interventions: She underwent one-stage total correction for her initial cardiovascular defects through median sternotomy under cardiopulmonary bypass support.
Outcomes: She had an uneventful recovery and completely healthy following the procedure.
Lessons: A thorough examination before PAS surgery was essential in discovering and carefully evaluating complicated heart and lung anomalies.
Competing Interests: The authors declare that they have no conflict of interest.
(Copyright © 2021 the Author(s). Published by Wolters Kluwer Health, Inc.)
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معلومات مُعتمدة: NO.LQ14H010001 the Zhejiang Provincial Natural Science Foundation, China
تواريخ الأحداث: Date Created: 20210206 Date Completed: 20210216 Latest Revision: 20220420
رمز التحديث: 20231215
مُعرف محوري في PubMed: PMC7837816
DOI: 10.1097/MD.0000000000024021
PMID: 33545997
قاعدة البيانات: MEDLINE
الوصف
تدمد:1536-5964
DOI:10.1097/MD.0000000000024021