مراجعة

Crouzon's Syndrome with a Dominant Sinus Pericranii Draining Transverse Sinus: Report of a Rare Association and Review of Literature.

التفاصيل البيبلوغرافية
العنوان: Crouzon's Syndrome with a Dominant Sinus Pericranii Draining Transverse Sinus: Report of a Rare Association and Review of Literature.
المؤلفون: Kumari S; Department of Anatomy, School of Medical Sciences and Research, Sharda University, Greater Noida, India., Verma SK; Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India., Singh PK; Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi, India.
المصدر: Pediatric neurosurgery [Pediatr Neurosurg] 2022; Vol. 57 (3), pp. 196-201. Date of Electronic Publication: 2022 Mar 21.
نوع المنشور: Case Reports; Review
اللغة: English
بيانات الدورية: Publisher: S. Karger Country of Publication: Switzerland NLM ID: 9114967 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1423-0305 (Electronic) Linking ISSN: 10162291 NLM ISO Abbreviation: Pediatr Neurosurg Subsets: MEDLINE
أسماء مطبوعة: Original Publication: Basel ; New York : S. Karger, c1990-
مواضيع طبية MeSH: Craniofacial Dysostosis*/complications , Craniofacial Dysostosis*/diagnostic imaging , Craniofacial Dysostosis*/surgery , Craniosynostoses*/complications , Sinus Pericranii*/diagnostic imaging , Sinus Pericranii*/surgery , Transverse Sinuses*/diagnostic imaging , Transverse Sinuses*/surgery, Humans ; Superior Sagittal Sinus
مستخلص: Introduction: Crouzon's syndrome and sinus pericranii (SP) are rare entities. Only few cases having both the features are reported. SP most commonly drains in relation to superior sagittal sinus and their communication to major posterior dural sinuses is rare.
Case Report: We report a rare case of Crouzon's syndrome with SP at a suboccipital location with termination of left transverse sinus into the SP draining further through the extracranial suboccipital and extravertebral cervical venous plexi into external jugular veins. Distal transverse sinus and sigmoid sinus on the left side were absent.
Conclusion: Crouzon's syndrome with SP is an extremely rare entity. SP with communication to major posterior dural venous sinuses is also rare and mostly associated with multi-suture craniosynostosis. Management depends on the volume of venous blood they are draining. Most of them are dominant type and their occlusion is not feasible. Preoperative diagnosis of a dominant SP is essential for proper surgical planning as it needs to be preserved mandatorily to prevent cerebral venous infarction.
(© 2022 S. Karger AG, Basel.)
فهرسة مساهمة: Keywords: Craniosynostosis; Crouzon’s syndrome; Dominant type sinus pericranii; Suboccipital sinus pericranii
تواريخ الأحداث: Date Created: 20220320 Date Completed: 20220622 Latest Revision: 20220622
رمز التحديث: 20240628
DOI: 10.1159/000524134
PMID: 35306498
قاعدة البيانات: MEDLINE
الوصف
تدمد:1423-0305
DOI:10.1159/000524134