دورية أكاديمية
أعرض في EDS

Femur fracture in a paediatric patient with hereditary hyaline fibromatosis syndrome.

التفاصيل البيبلوغرافية
العنوان: Femur fracture in a paediatric patient with hereditary hyaline fibromatosis syndrome.
المؤلفون: Morley HL; Trauma and Orthopaedics, Bradford Royal Infirmary, Bradford, UK hannah.morley1@nhs.net., Shaw DL; Trauma and Orthopaedics, Bradford Royal Infirmary, Bradford, UK., Hannant G; Trauma and Orthopaedics, Bradford Royal Infirmary, Bradford, UK.
المصدر: BMJ case reports [BMJ Case Rep] 2022 Apr 05; Vol. 15 (4). Date of Electronic Publication: 2022 Apr 05.
نوع المنشور: Case Reports; Journal Article
اللغة: English
بيانات الدورية: Publisher: BMJ Pub. Group Country of Publication: England NLM ID: 101526291 Publication Model: Electronic Cited Medium: Internet ISSN: 1757-790X (Electronic) Linking ISSN: 1757790X NLM ISO Abbreviation: BMJ Case Rep Subsets: MEDLINE
أسماء مطبوعة: Original Publication: London : BMJ Pub. Group
مواضيع طبية MeSH: Femoral Fractures*/surgery , Fracture Fixation, Intramedullary* , Hyaline Fibromatosis Syndrome*/complications, Child ; Female ; Femur ; Humans ; Infant ; Traction ; Treatment Outcome
مستخلص: An 18-month-old girl with hereditary hyaline fibromatosis syndrome (HHFS) and fixed flexion contractures presented with an oblique femur fracture, following a fall out of her mother's arms. The fracture was abutting intramedullary hyaline lesions. Due to her condition, balanced traction was impossible to apply. The authors report effective treatment of her injury using a non-operative approach in an early hip spica, over a 4-week period. There was no evidence of delayed osseous healing. Early spica application could be used as a definitive management option in children with femur fractures and fixed flexion contractures in future. This case emphasises the need for preventative measures to support bone health in patients with HHFS.
Competing Interests: Competing interests: None declared.
(© BMJ Publishing Group Limited 2022. No commercial re-use. See rights and permissions. Published by BMJ.)
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فهرسة مساهمة: Keywords: Congenital disorders; Orthopaedic and trauma surgery; Orthopaedics
تواريخ الأحداث: Date Created: 20220406 Date Completed: 20220407 Latest Revision: 20240405
رمز التحديث: 20240405
مُعرف محوري في PubMed: PMC8984057
DOI: 10.1136/bcr-2021-248447
PMID: 35383097
قاعدة البيانات: MEDLINE
الوصف
تدمد:1757-790X
DOI:10.1136/bcr-2021-248447