دورية أكاديمية
أعرض في EDS

Behçet's Disease-related Budd-Chiari Syndrome Successfully Managed with anti-TNF Antibody: A Case Report and Review of the Literature.

التفاصيل البيبلوغرافية
العنوان: Behçet's Disease-related Budd-Chiari Syndrome Successfully Managed with anti-TNF Antibody: A Case Report and Review of the Literature.
المؤلفون: Erul E; Department of Internal Medicine, Faculty of Medicine, Hacettepe University, Ankara, Turkey., Uzun GS; Division of Rheumatology, Department of Internal Medicine, Faculty of Medicine, Hacettepe University, Ankara, Turkey., Koksal D; Department of Pulmonary Diseases, Faculty of Medicine, Hacettepe University, Ankara, Turkey., Keskin O; Department of Gastroenterology, Faculty of Medicine, Hacettepe University, Ankara, Turkey., Uysal S; Department of Thoracic Surgery, Faculty of Medicine, Hacettepe University, Ankara, Turkey., Inkaya AC; Department of Infectious Diseases, Faculty of Medicine, Hacettepe University, Ankara, Turkey., Kalyoncu U; Division of Rheumatology, Department of Internal Medicine, Faculty of Medicine, Hacettepe University, Ankara, Turkey.
المصدر: European journal of case reports in internal medicine [Eur J Case Rep Intern Med] 2022 Aug 25; Vol. 9 (8), pp. 003515. Date of Electronic Publication: 2022 Aug 25 (Print Publication: 2022).
نوع المنشور: Journal Article
اللغة: English
بيانات الدورية: Publisher: SMC Media Country of Publication: Italy NLM ID: 101648453 Publication Model: eCollection Cited Medium: Internet ISSN: 2284-2594 (Electronic) Linking ISSN: 22842594 NLM ISO Abbreviation: Eur J Case Rep Intern Med Subsets: PubMed not MEDLINE
أسماء مطبوعة: Original Publication: Milano : SMC Media, [2014]-
مستخلص: Behçet's disease (BD) is multisystemic vasculitis with heterogeneous clinical manifestations. We describe the case of a 26-year-old man who presented with Budd-Chiari syndrome (BCS) related to BD. The patient received infliximab (IFX) due to the severity of vascular involvement. Subsequently, after IFX therapy, hospital-acquired pneumonia, trapped lung, and fungal infection of the lung and central nervous system developed as complications. The patient benefited from a second course of IFX and clinical remission was achieved following early identification and treatment of complications. Data on the presentation and prognosis of BCS related to BD are extremely limited. Our case report supports the growing evidence that anti-TNF antibody is a promising treatment for BD-related BCS.
Learning Points: Behçet's disease-related Budd-Chiari syndrome is a rare form of vascular involvement that severely affects mortality.Behçet's disease-related Budd-Chiari syndrome is frequently confused with idiopathic thrombosis and may be underdiagnosed.Infliximab could be a therapeutic option for refractory Behçet's disease with major vascular involvement, but the increased risk of opportunistic infections should be kept in mind.
Competing Interests: Conflicts of Interests: The authors declare there are no competing interests.
(© EFIM 2022.)
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فهرسة مساهمة: Keywords: Behçet’s disease; Budd-Chiari syndrome; bronchopleural fistula; infliximab; vascular involvement
تواريخ الأحداث: Date Created: 20220912 Latest Revision: 20220913
رمز التحديث: 20240628
مُعرف محوري في PubMed: PMC9451515
DOI: 10.12890/2022_003515
PMID: 36093305
قاعدة البيانات: MEDLINE
الوصف
تدمد:2284-2594
DOI:10.12890/2022_003515