دورية أكاديمية
[Eosinophilic granulomatosis with polyangiitis].
العنوان: | [Eosinophilic granulomatosis with polyangiitis]. |
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عنوان ترانسليتريتد: | Granulomatosis eosinofílica con poliangeítis. |
المؤلفون: | Romero Gómez C; Internal Medicine Department, Regional University Hospital of Málaga, Biomedical Research Institute of Málaga (IBIMA), University of Málaga (UMA), Málaga, España. Electronic address: carlosrg1968@gmail.com., Hernández Negrín H; Internal Medicine Department, Regional University Hospital of Málaga, Biomedical Research Institute of Málaga (IBIMA), University of Málaga (UMA), Málaga, España., Ayala Gutiérrez MDM; Internal Medicine Department, Regional University Hospital of Málaga, Biomedical Research Institute of Málaga (IBIMA), University of Málaga (UMA), Málaga, España. |
المصدر: | Medicina clinica [Med Clin (Barc)] 2023 Apr 06; Vol. 160 (7), pp. 310-317. Date of Electronic Publication: 2023 Feb 09. |
نوع المنشور: | Journal Article; Review |
اللغة: | English; Spanish; Castilian |
بيانات الدورية: | Publisher: Elsevier España Country of Publication: Spain NLM ID: 0376377 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1578-8989 (Electronic) Linking ISSN: 00257753 NLM ISO Abbreviation: Med Clin (Barc) Subsets: MEDLINE |
أسماء مطبوعة: | Publication: <2009- > : Madrid : Elsevier España Original Publication: Barcelona : Ediciones Doyma, S.A. |
مواضيع طبية MeSH: | Granulomatosis with Polyangiitis*/complications , Granulomatosis with Polyangiitis*/diagnosis , Granulomatosis with Polyangiitis*/drug therapy , Churg-Strauss Syndrome*/complications , Churg-Strauss Syndrome*/diagnosis , Churg-Strauss Syndrome*/drug therapy , Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis*/complications , Eosinophilia*/etiology , Eosinophilia*/complications , Asthma*/complications, Humans ; Antibodies, Antineutrophil Cytoplasmic |
مستخلص: | Eosinophilic granulomatosis with polyangiitis (EGPA) is a systemic vasculitis characterized by the presence of asthma associated with eosinophilia, eosinophilic infiltration of different organs, and vasculitis of small and medium-sized vessels. Although classified as anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis, it occurs in less than half of the patients. The disease is infrequent, typically appearing in patients with asthma and affecting multiple organs such as lung, skin and peripheral nervous system. Treatment has been based on the use of glucocorticoids and immunosuppressants. In recent years, progress has been made in the knowledge of the pathophysiology, in treatment with the inclusion of biologic agents, the classification criteria have been revised and new therapeutic recommendations have been published. (Copyright © 2023 Elsevier España, S.L.U. All rights reserved.) |
التعليقات: | Comment in: Med Clin (Barc). 2024 Feb 9;162(3):140. (PMID: 37567822) |
فهرسة مساهمة: | Keywords: Eosinofilia; Eosinophilia; Eosinophilic granulomatosis with polyangiitis; Granulomatosis eosinofílica con poliangeítis; Systemic vasculitis; Vasculitis sistémica |
المشرفين على المادة: | 0 (Antibodies, Antineutrophil Cytoplasmic) |
تواريخ الأحداث: | Date Created: 20230211 Date Completed: 20230324 Latest Revision: 20240326 |
رمز التحديث: | 20240327 |
DOI: | 10.1016/j.medcli.2023.01.003 |
PMID: | 36774291 |
قاعدة البيانات: | MEDLINE |
تدمد: | 1578-8989 |
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DOI: | 10.1016/j.medcli.2023.01.003 |