دورية أكاديمية
Vessel wall imaging in the diagnosis of antiphospholipid syndrome presenting as Moyamoya syndrome-A case report.
| العنوان: | Vessel wall imaging in the diagnosis of antiphospholipid syndrome presenting as Moyamoya syndrome-A case report. |
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| المؤلفون: | Yang DL; Perelman School of Medicine, University of Pennsylvania, USA., Thomas R; Department of Neurology, University of Pennsylvania, USA., Ford AF; Department of Neurology, University of Pennsylvania, USA., Cucchiara BL; Department of Neurology, University of Pennsylvania, USA., George DK; Department of Neurology, University of Pennsylvania, USA., Song JW; Department of Radiology, University of Pennsylvania, USA. |
| المصدر: | The neuroradiology journal [Neuroradiol J] 2024 Apr 15, pp. 19714009241247469. Date of Electronic Publication: 2024 Apr 15. |
| Publication Model: | Ahead of Print |
| نوع المنشور: | Journal Article |
| اللغة: | English |
| بيانات الدورية: | Publisher: Sage Publications Country of Publication: United States NLM ID: 101295103 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 2385-1996 (Electronic) Linking ISSN: 19714009 NLM ISO Abbreviation: Neuroradiol J Subsets: MEDLINE |
| أسماء مطبوعة: | Publication: 2015- : Thousand Oaks, CA : Sage Publications Original Publication: Bologna : Centauro |
| مستخلص: | Objectives: We describe a case of anti-phospholipid syndrome (APLS) vasculopathy presenting with Moyamoya syndrome (MMS) and show the associated intracranial vessel wall MRI (VWI) findings. Methods: A 37-year-old-woman presented with acute onset dizziness and left-sided weakness. Neurologic exam revealed a left facial droop and left hemiparesis. She underwent a comprehensive laboratory work-up for stroke. Neuroimaging included a CT head, CT angiogram, VWI, and digital subtraction angiography. Results: Work-up revealed a triple-positive APLS antibody profile. CT of the head showed an acute right basal ganglia infarction and right frontal subarachnoid hemorrhage. CT angiogram revealed severe stenosis of the right internal carotid artery terminus in a Moyamoya pattern. Intracranial VWI showed long-segment concentric vessel wall thickening and homogeneous vessel wall enhancement and T2-hyperintense wall edema of the stenotic right ICA terminus, M1 middle cerebral artery, and A1 anterior cerebral artery. She was treated with long-term anticoagulation with warfarin and a right superficial temporal artery to middle cerebral artery bypass. Discussion: We present intracranial VWI features of vessel wall pathology in a patient with primary APLS presenting with MMS. Competing Interests: Declaration of conflicting interestsThe author(s) declared no potential conflicts of interest with respect to the research, authorship, and/or publication of this article. |
| فهرسة مساهمة: | Keywords: Anti-phospholipid syndrome; central nervous system vasculopathy; moyamoya; proliferative vasculopathy; vessel wall magnetic resonance imaging |
| تواريخ الأحداث: | Date Created: 20240415 Latest Revision: 20240415 |
| رمز التحديث: | 20240416 |
| DOI: | 10.1177/19714009241247469 |
| PMID: | 38621702 |
| قاعدة البيانات: | MEDLINE |
Full Text Finder | تدمد: | 2385-1996 |
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| DOI: | 10.1177/19714009241247469 |