تقرير
أعرض في EDS

Vacterl syndrome: Medical and stomatological considerations for comprehensive patient management.

التفاصيل البيبلوغرافية
العنوان: Vacterl syndrome: Medical and stomatological considerations for comprehensive patient management.
المؤلفون: Do Amaral COF; Faculty of Dentistry, University of Oeste Paulista - Unoeste, São Paulo, Brazil., Souza AFFB; Dentistry - University of Western Sao Paulo - Unoeste, São Paulo, Brazil., Carlucci GP; Dentistry - University of Western Sao Paulo - Unoeste, São Paulo, Brazil., Lima LDS; Dentistry - University of Western Sao Paulo - Unoeste, São Paulo, Brazil., Amaral MOFD; Medical School, University of West São Paulo, São Paulo, Brazil., Straioto FG; Department of Prosthodontics and Geriatic Dentistry, Dental School, University of Western Sao Paulo, São Paulo, Brazil.
المصدر: Special care in dentistry : official publication of the American Association of Hospital Dentists, the Academy of Dentistry for the Handicapped, and the American Society for Geriatric Dentistry [Spec Care Dentist] 2024 May 02. Date of Electronic Publication: 2024 May 02.
Publication Model: Ahead of Print
نوع المنشور: Case Reports
اللغة: English
بيانات الدورية: Publisher: American Dental Association Country of Publication: United States NLM ID: 8103755 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1754-4505 (Electronic) Linking ISSN: 02751879 NLM ISO Abbreviation: Spec Care Dentist Subsets: MEDLINE
أسماء مطبوعة: Original Publication: [Chicago : American Dental Association, c1981-
مستخلص: Aim: The VACTERL association or Syndrome consists of Vertebral, Anorectal, Cardiac, Tracheo-Esophageal, Renal, and Limb defects. The diagnosis relies on the presence of at least three of these structural abnormalities. This study reports a single case of a patient with VACTERL Syndrome (VS), aiming to assist dentists in recognizing the general aspects, systemic changes, and oral care related to this condition.
Case Report: A 14-year-old female patient medically diagnosed with VS. The study evaluated the presence of systemic alterations, medication use, behavioral deviations, cognitive development, and oral aspects. The patient exhibited cardiovascular alterations including a ventricular septal defect (C), anal atresia (A), polydactyly (considered limb alteration-L), and scoliosis (a possible indication of vertebral anomalies-V). In the intraoral examination, findings included tooth crowding, enamel hypomineralization in several teeth, a deep and atretic palate, generalized gingivitis, bleeding, gingival hyperplasia, Class III malocclusion, and a right unilateral crossbite.
Conclusion: Patients diagnosed with VACTERL syndrome experience significant systemic impairments. The research subject presented compromised oral health, challenges in dental management, delays in neuropsychomotor development, though these are not inherent to the syndrome. It is crucial to prevent oral diseases and provide early dental care for these patients to avoid the need for complex and invasive dental treatments due to systemic impairments.
(© 2024 Special Care Dentistry Association and Wiley Periodicals LLC.)
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فهرسة مساهمة: Keywords: congenital abnormalities; multiple abnormalities; oral health; syndrome
تواريخ الأحداث: Date Created: 20240502 Latest Revision: 20240502
رمز التحديث: 20240502
DOI: 10.1111/scd.13006
PMID: 38693821
قاعدة البيانات: MEDLINE
الوصف
تدمد:1754-4505
DOI:10.1111/scd.13006