دورية أكاديمية

Incidental diagnosis of cardiac fibroma in an infant with acute viral bronchiolitis.

التفاصيل البيبلوغرافية
العنوان: Incidental diagnosis of cardiac fibroma in an infant with acute viral bronchiolitis.
المؤلفون: Pigosso YG; Hospital Pequeno Príncipe (HPP), Curitiba, PR, Brasil., Fogiato IM; Hospital Pequeno Príncipe (HPP), Curitiba, PR, Brasil., Vieira GG; Hospital Pequeno Príncipe (HPP), Curitiba, PR, Brasil., Vaz A; Hospital Pequeno Príncipe (HPP), Curitiba, PR, Brasil., Percicote AP; Hospital Pequeno Príncipe (HPP), Curitiba, PR, Brasil., Silva BHS; Hospital Pequeno Príncipe (HPP), Curitiba, PR, Brasil., João PRD; Hospital Pequeno Príncipe (HPP), Curitiba, PR, Brasil.
المصدر: Revista paulista de pediatria : orgao oficial da Sociedade de Pediatria de Sao Paulo [Rev Paul Pediatr] 2024 May 27; Vol. 42, pp. e2022157. Date of Electronic Publication: 2024 May 27 (Print Publication: 2024).
نوع المنشور: Case Reports; Journal Article
اللغة: English
بيانات الدورية: Publisher: Sociedade De Pediatria De Sao Paulo Country of Publication: Brazil NLM ID: 9109353 Publication Model: eCollection Cited Medium: Internet ISSN: 1984-0462 (Electronic) Linking ISSN: 01030582 NLM ISO Abbreviation: Rev Paul Pediatr Subsets: MEDLINE
أسماء مطبوعة: Publication: 2017- : Sao Paulo : Sociedade De Pediatria De Sao Paulo
Original Publication: Sao Paulo : Sociedade De Pediatria De Sao Paulo
مواضيع طبية MeSH: Heart Neoplasms*/diagnosis , Heart Neoplasms*/complications , Fibroma*/diagnosis , Fibroma*/complications , Incidental Findings* , Bronchiolitis, Viral*/diagnosis, Humans ; Male ; Infant ; Acute Disease
مستخلص: Objective: Pediatric cardiac tumors are rare and, among them, 90% are benign. Cardiac fibroma is the second most frequent tumor, after rhabdomyoma. The objective of this study is to report a case of cardiac fibroma diagnosed incidentally in a patient admitted with acute viral bronchiolitis.
Case Description: A 5-month-old male infant was admitted to the pediatric emergency department with acute viral bronchiolitis requiring hospitalization. He presented a detectable respiratory syncytial virus in oropharyngeal swab, blood test with lymphocytosis and a chest radiography revealed cardiomegaly. Further cardiologic testing was performed detecting elevation of cardiac biomarkers, an electrocardiogram with alteration of left ventricular repolarization and echocardiogram with a heterogeneous mass in the left ventricular, with areas of calcification. A chest angiotomography suggested rhabdomyosarcoma or cardiac fibroma and a magnetic resonance showed a mass, with characteristics suggesting fibroma. The final diagnosis was made after two cardiac catheterizations for biopsy of the lesion, confirming cardiac fibroma by anatomopathological examination. Because the patient had moderate to severe systolic dysfunction, he was submitted to heart transplant.
Comments: One third of cardiac fibromas are asymptomatic, generally diagnosed late through tests ordered for other reasons. The gold-standard test for definitive diagnosis is biopsy. Cardiac fibroma usually does not present spontaneous regression and, in most cases, partial or total surgical resection is necessary. When tumors are unresectable, heart transplantation should be indicated. It is essential to have detailed characterization of the cardiac mass to establish the most appropriate therapeutic approach for each patient.
References: Pediatr Cardiol. 2000 Jul-Aug;21(4):317-23. (PMID: 10865004)
Asian Cardiovasc Thorac Ann. 2017 Mar;25(3):207-209. (PMID: 26542780)
Ann Pediatr Cardiol. 2021 Apr-Jun;14(2):224-227. (PMID: 34103866)
Arq Bras Cardiol. 2013 Feb;100(2):120-6. (PMID: 23503820)
Rev Port Cardiol. 2011 Oct;30(10):795-7. (PMID: 22118131)
Paediatr Drugs. 2019 Jun;21(3):185-193. (PMID: 31124053)
Eur J Pediatr. 2017 Feb;176(2):253-260. (PMID: 28074279)
Cardiovasc Pathol. 2008 Jul-Aug;17(4):193-8. (PMID: 18402818)
تواريخ الأحداث: Date Created: 20240529 Date Completed: 20240529 Latest Revision: 20240531
رمز التحديث: 20240531
مُعرف محوري في PubMed: PMC11135903
DOI: 10.1590/1984-0462/2024/42/2022157
PMID: 38808864
قاعدة البيانات: MEDLINE
الوصف
تدمد:1984-0462
DOI:10.1590/1984-0462/2024/42/2022157