دورية أكاديمية
Hydrops and congenital diaphragmatic hernia: reported incidence and postnatal outcomes. Analysis of the congenital diaphragmatic hernia study group registry.
| العنوان: | Hydrops and congenital diaphragmatic hernia: reported incidence and postnatal outcomes. Analysis of the congenital diaphragmatic hernia study group registry. |
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| المؤلفون: | Mesas Burgos C; Department of Pediatric Surgery, Karolinska University Hospital and Karolinska Institute, Stockholm, Sweden. carmen.mesas.burgos@ki.se., Ebanks AH; Department of Pediatric Surgery, McGovern Medical School at UT Health and Children's Memorial Hermann Hospital, Houston, TX, USA., Löf-Granström A; Department of Pediatric Surgery, Karolinska University Hospital and Karolinska Institute, Stockholm, Sweden., Holden KI; Department of Pediatric Surgery, McGovern Medical School at UT Health and Children's Memorial Hermann Hospital, Houston, TX, USA., Johnson A; The Fetal Center, Children's Memorial Hermann Hospital, University of Texas Health Science Center, Houston, TX, USA., Conner P; Center for Fetal Medicine, Karolinska University Hospital and Karolinska Institute, Stockholm, Sweden., Harting MT; Department of Pediatric Surgery, McGovern Medical School at UT Health and Children's Memorial Hermann Hospital, Houston, TX, USA. |
| مؤلفون مشاركون: | Congenital Diaphragmatic Hernia Study Group |
| المصدر: | Journal of perinatology : official journal of the California Perinatal Association [J Perinatol] 2024 May 30. Date of Electronic Publication: 2024 May 30. |
| Publication Model: | Ahead of Print |
| نوع المنشور: | Journal Article |
| اللغة: | English |
| بيانات الدورية: | Publisher: Nature Publishing Group Country of Publication: United States NLM ID: 8501884 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1476-5543 (Electronic) Linking ISSN: 07438346 NLM ISO Abbreviation: J Perinatol Subsets: MEDLINE |
| أسماء مطبوعة: | Publication: 2001- : New York, NY : Nature Publishing Group Original Publication: [Philadelphia, Pa. : W.B. Saunders, c1984- |
| مستخلص: | Objective: Congenital Diaphragmatic Hernia (CDH) associated with hydrops is rare. The aim of this study was to describe the incidence of this combination of anomalies and the postnatal outcomes from a large database for CDH. Study Design: Data from the multicenter, multinational database on infants with prenatally diagnosed CDH (CDHSG Registry) born from 2015 to 2021 were analyzed. Results: A total of 3985 patients were entered in the registry during the study period, 3156 were prenatally diagnosed and 88 were reported to have associated fluid in at least 1 compartment, representing 2.8% of all prenatally diagnosed CDH cases in the registry. The overall survival to discharge for CDH patients with hydrops was 43%. The hydropic CDH group had lower birth weight and gestational age at birth, and increased incidence of right-sided CDH (55%), and rate of non-repair (45%). However, the survival rate for hydropic infants with CDH undergoing surgical repair was 80%. Other associated anomalies were more common in hydropic CDH (50% vs 37%, p = 0.001). Conclusion: Hydropic CDH is rare, only 2.8% of all prenatally diagnosed cases, and more commonly occurring in right-sided CDH. Survival rates are low, with higher rates of non-repair. However, decision-making regarding goals of care and an aggressive surgical approach in selected cases may result in survival rates comparable to non-hydropic cases. (© 2024. The Author(s).) |
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| تواريخ الأحداث: | Date Created: 20240530 Latest Revision: 20240530 |
| رمز التحديث: | 20240531 |
| DOI: | 10.1038/s41372-024-02010-5 |
| PMID: | 38816581 |
| قاعدة البيانات: | MEDLINE |
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Full Text Finder | تدمد: | 1476-5543 |
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| DOI: | 10.1038/s41372-024-02010-5 |