دورية أكاديمية
Isolated left ventricular non-compaction: Clinical characterisation of a teenage male.
| العنوان: | Isolated left ventricular non-compaction: Clinical characterisation of a teenage male. |
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| المؤلفون: | Khan J; Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan., Sohail H; Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan., Akhtar P; Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan., Memon AQ; Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan., Jalil B; Department of Adult Cardiology, National Institute of Cardiovascular Diseases, Karachi, Pakistan. |
| المصدر: | JPMA. The Journal of the Pakistan Medical Association [J Pak Med Assoc] 2024 Jun; Vol. 74 (6), pp. 1183-1186. |
| نوع المنشور: | Case Reports; Journal Article |
| اللغة: | English |
| بيانات الدورية: | Publisher: Pakistan Medical Association Country of Publication: Pakistan NLM ID: 7501162 Publication Model: Print Cited Medium: Internet ISSN: 0030-9982 (Print) Linking ISSN: 00309982 NLM ISO Abbreviation: J Pak Med Assoc Subsets: MEDLINE |
| أسماء مطبوعة: | Publication: Karachi : Pakistan Medical Association Original Publication: Karachi. |
| مواضيع طبية MeSH: | Defibrillators, Implantable* , Isolated Noncompaction of the Ventricular Myocardium*/therapy , Isolated Noncompaction of the Ventricular Myocardium*/diagnosis , Echocardiography*, Humans ; Male ; Adolescent ; Dyspnea/etiology ; Dizziness/etiology |
| مستخلص: | Isolated Left Ventricular Non-compaction (LVNC) is a type of cardiomyopathy that usually has a genetic origin. Its diagnosis is based on finding such as deep intertrabecular recesses or sinusoids and ventricular trabeculations communicating with the left ventricular cavity. LVNC was first clinically recognised almost four decades ago, yet its diagnostic and management challenges persist. In this report, we present the case of an 18-year-old boy, who presented at the National Institute of Cardiovascular Diseases, Karachi, in March 2023, with complaints of dizziness, pedal oedema, and shortness of breath. Echocardiography revealed signs suggestive of LVNC, which were confirmed conclusively on Cardiovascular Magnetic Resonance (CMR) (NC/C ratio>2.4). The patient underwent implantable cardioverter defibrillator (ICD) placement, was discharged after a smooth post-procedure recovery, and is doing well on follow-ups. Hence, ICD and guideline-directed medical therapy as a combination have turned out to have satisfactory outcomes in decreasing morbidity and providing mortality benefits for such patients. |
| فهرسة مساهمة: | Keywords: Left ventricular non-compaction, Isolated noncompaction of left ventricular myocardium, Left ventricular dysfunction. |
| تواريخ الأحداث: | Date Created: 20240701 Date Completed: 20240701 Latest Revision: 20240701 |
| رمز التحديث: | 20240701 |
| DOI: | 10.47391/JPMA.10034 |
| PMID: | 38948997 |
| قاعدة البيانات: | MEDLINE |
Full Text Finder | تدمد: | 0030-9982 |
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| DOI: | 10.47391/JPMA.10034 |