Persistent Müllerian Ducts Syndrome: A Case Report
| العنوان: | Persistent Müllerian Ducts Syndrome: A Case Report |
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| المؤلفون: | F. Z. El Argubi, A. Mdaghri Alaoui, Y. Kriouile, Z. Imane, A. Gaouzi |
| المصدر: | Scholars Journal of Medical Case Reports. 10:1061-1062 |
| بيانات النشر: | SASPR Edu International Pvt. Ltd, 2022. |
| سنة النشر: | 2022 |
| مصطلحات موضوعية: | General Medicine |
| الوصف: | We report the case of a 6 years old child, admitted for management of testicular ectopia, the clinical examination found an empty scrotum, a normal looking penis and a urethral meatus in place. The scrotal ultrasound showed an intra-abdominal testicle (left illiac fossa) of homogeneous echostructure on the left side, while the right testicle was not visualized. The gonadotropins LH and FSH levels were low, as well as the level of testosterone, the secretion of which is stimulated after administration of Pregnyl. Laparoscopy revealed 2 gonadal formations on the same side, 2 tubes and a median formation reminiscent of the uterus. The karyotype of the patient was male 46XY, the dosage of anti Müllerian hormone (AMH) was high, confirming an abnormality of its receptors, which explains the persistence of the Müllerian ducts in this child. The child underwent a left gonadectomy with bilateral hysterectomy and adnexectomy, associated with a lowering of the right testicle. At 9 years, pubertal development was classified as T3P4 according to Tanner's classification, scrotal ultrasound showed a free left testicular compartment with testicular calcifications classified as grade 3, and tumor marker levels were normal. |
| تدمد: | 2347-6559 2347-9507 |
| URL الوصول: | https://explore.openaire.eu/search/publication?articleId=doi_________::a7ed98ac8b17c2a5c0d4945af13d56da https://doi.org/10.36347/sjmcr.2022.v10i10.018 |
| حقوق: | OPEN |
| رقم الأكسشن: | edsair.doi...........a7ed98ac8b17c2a5c0d4945af13d56da |
| قاعدة البيانات: | OpenAIRE |
| تدمد: | 23476559 23479507 |
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