Malignant rhabdoid tumor in a solitary kidney arising in an adult patient with chronic obstructive renal calculi
| العنوان: | Malignant rhabdoid tumor in a solitary kidney arising in an adult patient with chronic obstructive renal calculi |
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| المؤلفون: | Y. Nouira, S. Ben Rhouma, Y. Ayari, M. Krarti, Myriam Jrad, H. Boussaffa, L. Charfi |
| المصدر: | International Journal of Surgery Case Reports |
| بيانات النشر: | Elsevier BV, 2019. |
| سنة النشر: | 2019 |
| مصطلحات موضوعية: | Adult, medicine.medical_specialty, Renal calculi, Malignant rhabdoid tumor, medicine.medical_treatment, Solitary kidney, Autopsy, Hydronephrosis, urologic and male genital diseases, Inferior vena cava, Article, 03 medical and health sciences, 0302 clinical medicine, Medicine, Sampling (medicine), Renal, Malignant, Kidney, business.industry, medicine.disease, Nephrectomy, medicine.anatomical_structure, medicine.vein, 030220 oncology & carcinogenesis, 030211 gastroenterology & hepatology, Surgery, Radiology, Rhabdoid tumor, business |
| الوصف: | Highlights • Malignant rhabdoid tumor of the kidney in adult patients are extremely rare and have the worst prognosis of all renal tumors. • The histological features and immunohistochemical staining may aid in confirming the diagnosis of these tumors. • It is necessary to consider this entity in front of renal masses when such type of renal tumor is encountered in adult patients. Introduction Malignant rhabdoid tumor (MRT) is one of the most aggressive and lethal malignancies in pediatric oncology, MRT of the kidney is an uncommon renal tumor in children and it’s extremely rare in adult patients. With only seven previously reported adult cases in the English-literature, to our knowledge this is the first case that is associated with renal calculi. Presentation of case We present the case of a 65-year-old man with an MRT arising in a solitary kidney with multiple enlarged lymph nodes that compressing the inferior vena cava. Discussion Malignant rhabdoid tumor of the kidney was originally described as a “rhabdomyosarcomatoid” variant of Wilm’s tumor due to the resemblance of cells to rhabdomyoblasts, now this type of tumor is recognized as distant and unique malignant renal tumor. It affects usually children before the age of 2 years. Tumor tissue sampling is required to make the diagnosis of MRTK, based on either nephrectomy, core biopsy, or autopsy specimens. There is no established standard of care due to the paucity of cases. Surgery is considered to be the first choice of treatment if possible. Conclusion This case report reinforces the importance of recognizing this entity in the adult population, and discuss the possible treatment options of this rare and highly aggressive tumor. |
| تدمد: | 2210-2612 |
| URL الوصول: | https://explore.openaire.eu/search/publication?articleId=doi_dedup___::bf6bede29d225fdc96541bdebf01438c https://doi.org/10.1016/j.ijscr.2019.04.021 |
| حقوق: | OPEN |
| رقم الأكسشن: | edsair.doi.dedup.....bf6bede29d225fdc96541bdebf01438c |
| قاعدة البيانات: | OpenAIRE |
Full Text via ClinicalKey | تدمد: | 22102612 |
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