How strict is galactose restriction in adults with galactosaemia? International practice
| العنوان: | How strict is galactose restriction in adults with galactosaemia? International practice |
|---|---|
| المؤلفون: | Karen Corthouts, P. Portnoi, M. Heddrich-Ellerbrok, Isidro Vitoria, U. Meyer, S.M. Bernabei, A. Micciche, M. Robert, Louise Robertson, Carina Heidenborg, S. Dawson, Alessandro P. Burlina, Suzanne Ford, S. Rosenbaum-Fabian, K. Luyten, S. Boocock, S. Schultz, A. van Teeffelen-Heithoff, T. Coote, K. Sahm, Katharina Dokoupil, I. Fasan, J. Wenz, G. Gallo, C. Timmer, C. Ferguson, S. Defourny, M. Diels, Sarah C. Grünert, Kath Singleton, M. Van Driessche, J. Wildgoose, L. Stoelen, L. van der Ploeg, S. Donald, Y. Devlin, M. Forga, M. van Rijn, S. Ripley, E. Sjoqvist, S. Bollhalder, S. Adam, R. Akroyd, Jaime Dalmau, Anita MacDonald, K. Vande Kerckhove, M. Westbrook, H. Zweers, A. De Meyer, E. Müller, Sharon Evans, An Desloovere, C. Voillot, A. Terry, C. Jonkers, S. Thompson, K. Lefebure |
| المساهمون: | Extramural researchers, Endocrinology |
| المصدر: | Molecular Genetics and Metabolism, 115(1), 23. Academic Press Inc. Molecular Genetics and Metabolism, 115, 23-6 Molecular Genetics and Metabolism, 115(1), 23-26. ACADEMIC PRESS INC ELSEVIER SCIENCE Molecular genetics and metabolism MOLECULAR GENETICS AND METABOLISM r-IIS La Fe. Repositorio Institucional de Producción Científica del Instituto de Investigación Sanitaria La Fe instname Molecular genetics and metabolism, 115(1), 23-26. Academic Press Inc. Molecular Genetics and Metabolism, 115, 1, pp. 23-6 |
| بيانات النشر: | Elsevier BV, 2015. |
| سنة النشر: | 2015 |
| مصطلحات موضوعية: | Endocrinology, Diabetes and Metabolism, Galactose-1-phosphate, Lactose, PHENOTYPE, Biochemistry, chemistry.chemical_compound, Endocrinology, Galactosides, Surveys and Questionnaires, Vegetables, galactose restriction, vegetable, Food science, comparative study, questionnaire, Adult, dietitian, Chemistry, Galactosemia, Metabolic Disorders Radboud Institute for Molecular Life Sciences [Radboudumc 6], clinical trial, health survey, priority journal, disease severity, dietetics, CLASSICAL GALACTOSEMIA, Galactosaemia, diet restriction, Adult, Galactosemias, Monitoring, Diet therapy, food processing, Genetics, medicine, follow up, Humans, controlled study, human, Biology, Molecular Biology, galactosemia, Adult patients, questionnaire, food, Dietary management, Galactose, fruit, medicine.disease, major clinical study, Diet, multicenter study, diet therapy, Fruits and vegetables, Human medicine, dietary intake |
| الوصف: | Dietary management of 418 adult patients with galactosaemia (from 39 centres/12 countries) was compared. All centres advised lactose restriction, 6 restricted galactose from galactosides +/- fruits and vegetables and 12 offal. 38% (n = 15) relaxed diet by: 1) allowing traces of lactose in manufactured foods (n = 13) or 2) giving fruits, vegetables and galactosides (n = 2). Only 15% (n = 6) calculated dietary galactose. 32% of patients were lost to dietetic follow-up. In adult galactosaemia, there is limited diet relaxation. (C) 2015 Elsevier Inc. All rights reserved. |
| وصف الملف: | image/pdf; pdf |
| تدمد: | 1096-7192 |
| URL الوصول: | https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d7596e365883545a329953f3d1d84908 https://doi.org/10.1016/j.ymgme.2015.03.008 |
| حقوق: | OPEN |
| رقم الأكسشن: | edsair.doi.dedup.....d7596e365883545a329953f3d1d84908 |
| قاعدة البيانات: | OpenAIRE |
| تدمد: | 10967192 |
|---|