دورية أكاديمية
Best management in isolated right ventricular hypoplasia with septal defects in adults
العنوان: | Best management in isolated right ventricular hypoplasia with septal defects in adults |
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المؤلفون: | Zahra Khajali, Maedeh Arabian, Maryam Aliramezany |
المصدر: | Journal of Cardiovascular and Thoracic Research, Vol 12, Iss 3, Pp 237-243 (2020) |
بيانات النشر: | Tabriz University of Medical Sciences, 2020. |
سنة النشر: | 2020 |
المجموعة: | LCC:Diseases of the circulatory (Cardiovascular) system |
مصطلحات موضوعية: | right ventricular hypoplasia, adult congenital heart disease, cyanosis, atrial septal defect, Diseases of the circulatory (Cardiovascular) system, RC666-701 |
الوصف: | Hypoplastic right ventricle is a rare congenital disease usually associated with pulmonary atresia or tricuspid atresia. Isolated right ventricular hypoplasia is a rare anomaly without important valvular abnormalities. It is associated with inter atrial septal defects leading to the right-to-left shunting of blood. Patients with isolated right ventricular hypoplasia usually have different and variable courses. In some patients, it is recognized in the perinatal period and necessitates prompt intervention; nonetheless, there are some reports of this anomaly in old age with no significant symptoms. In this report, we describe the clinical data and management of 6 adult cases with isolated right ventricular hypoplasia treated medically or surgically based on the severity of the disease and symptoms and then offer an in-depth discussion regarding this rare anomaly. |
نوع الوثيقة: | article |
وصف الملف: | electronic resource |
اللغة: | English |
تدمد: | 2008-5117 2008-6830 |
Relation: | https://jcvtr.tbzmed.ac.ir/PDF/jcvtr-12-237.pdf; https://doaj.org/toc/2008-5117; https://doaj.org/toc/2008-6830 |
DOI: | 10.34172/jcvtr.2020.36 |
URL الوصول: | https://doaj.org/article/062c137acf374887b58b4f5924c1173a |
رقم الأكسشن: | edsdoj.062c137acf374887b58b4f5924c1173a |
قاعدة البيانات: | Directory of Open Access Journals |
تدمد: | 20085117 20086830 |
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DOI: | 10.34172/jcvtr.2020.36 |