دورية أكاديمية

Extraosseous Ewing Sarcoma in a Pelvic Region: A Case Report

التفاصيل البيبلوغرافية
العنوان: Extraosseous Ewing Sarcoma in a Pelvic Region: A Case Report
المؤلفون: Sushma Gurung, Sagun Thapa, Shristi Gautam
المصدر: Journal of Nepal Medical Association, Vol 60, Iss 251 (2022)
بيانات النشر: Nepal Medical Association, 2022.
سنة النشر: 2022
المجموعة: LCC:Medicine (General)
مصطلحات موضوعية: Ewing sarcoma, neoadjuvant chemotherapy, radiation therapy., Medicine (General), R5-920
الوصف: Ewing sarcoma is the second most common malignant bone tumour in children. It rarely originates from extraskeletal soft tissue sites such as the upper thigh, buttocks, upper arm and shoulder. Primary extraosseous Ewing sarcoma located in the pelvic region is rare. We report a 17-year-female who had gradual onset of progressive lower abdominal mass and pain. A computed tomography scan revealed well defined lobulated heterogeneously enhancing lesion noted in the pelvic region measuring approximately 12.9 x 9.8 x 9.3 cm. Incisional biopsy showed a small round blue cell tumour which was strongly positive for Cluster of Differentiation 99, vimentin, Friend Leukaemia Integration 1 with 40% Ki-67. Following treatment with chemotherapy, surgery and radiotherapy, there was complete resolution of the tumour. Although extraosseous Ewing sarcoma is rare, it can occur virtually in any soft tissue site. Therefore, clinicians need to distinguish it from soft tissue sarcoma because rapid progression, early diagnosis and timely treatment are crucial for a favourable prognosis.
نوع الوثيقة: article
وصف الملف: electronic resource
اللغة: English
تدمد: 0028-2715
1815-672X
Relation: https://jnma.com.np/jnma/index.php/jnma/article/view/7523; https://doaj.org/toc/0028-2715; https://doaj.org/toc/1815-672X
DOI: 10.31729/jnma.7523
URL الوصول: https://doaj.org/article/12f7f20f2aa44a7fb099169a49556f02
رقم الأكسشن: edsdoj.12f7f20f2aa44a7fb099169a49556f02
قاعدة البيانات: Directory of Open Access Journals
الوصف
تدمد:00282715
1815672X
DOI:10.31729/jnma.7523