Dysplasia Epiphysealis Hemimelica (DEH) or Trevor's disease is a rare skeletal condition that forms osteochondroma like lesions in the epiphysis of long bones. This occurs mainly in pediatric patients with a predilection for the lower extremities. The knee and the ankle joint are most commonly affected in a hemimelic distribution meaning that either the medial or the lateral part of the center of ossification is affected. We report a rare case of Dysplasia Epiphysealis Hemimelica in an active pediatric patient involving multiple tarsal bones around the left ankle that was surgically excised after using a medial malleolar osteotomy for exposure. At over four years of follow up, our patient is pain free, has no growth arrest and continues to engage in normal activities.
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