دورية أكاديمية
Anesthesia for a cesarean section on a pregnant patient with Cockayne syndrome: case report
| العنوان: | Anesthesia for a cesarean section on a pregnant patient with Cockayne syndrome: case report |
|---|---|
| المؤلفون: | Viviane Barrada Ribeiro, Leonardo Teixeira Ribeiro Alonso de Faria, Roberta de Lima Machado, Bruno Mendonça Barcellos, Marco Antonio Cardoso de Resende, Rogério Luiz da Rocha Videira |
| المصدر: | Revista Brasileira de Anestesiologia, Vol 70, Iss 1, Pp 51-54 (2020) |
| بيانات النشر: | Sociedade Brasileira de Anestesiologia, 2020. |
| سنة النشر: | 2020 |
| المجموعة: | LCC:Anesthesiology |
| مصطلحات موضوعية: | Cockayne syndrome, Difficult airway, Obsteric anesthesia, Pregnancy, Progeria, Anesthesiology, RD78.3-87.3 |
| الوصف: | Abstract Cockayne syndrome is an autosomal recessive multi-systemic disorder due to DNA repair failure. It was originally described in 1936 in children of small stature, retinal atrophy and deafness, characterized by dwarfism, cachexia, photosensitivity, premature aging and neurologic deficits. The most typical feature is described as birdlike facies: protruding maxilla, facial lipoatrophy, sunken eyes, large ears and thin nose. Difficult airway management with subglottic stenosis and risk of gastric content aspiration has been described. Although the clinical characteristics of Cockayne syndrome have been well described in pediatric publications, there is only one report in the literature on anesthesia for an obstetric patient. We report the case of a pregnant patient diagnosed with Cockayne syndrome, submitted successfully to spinal anesthesia for a cesarean section due to cephalopelvic disproportion. In view of the difficult decision between inducing general anesthesia in a patient with a likely difficult airway, or neuraxial anesthesia in a patient with cardiovascular, respiratory and neurocognitive limitations, we suggest tailored management to reach the best results for the mother and newborn. |
| نوع الوثيقة: | article |
| وصف الملف: | electronic resource |
| اللغة: | English Spanish; Castilian Portuguese |
| تدمد: | 1806-907X |
| Relation: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0034-70942020000100051&tlng=pt; http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0034-70942020000100051&tlng=en; http://www.scielo.br/pdf/rba/v70n1/pt_0034-7094-rba-70-01-0051.pdf; http://www.scielo.br/pdf/rba/v70n1/0034-7094-rba-70-01-0051.pdf; https://doaj.org/toc/1806-907X |
| DOI: | 10.1016/j.bjane.2020.02.006 |
| URL الوصول: | https://doaj.org/article/6c18d43ea82740d2ba2dfaab469d9927 |
| رقم الأكسشن: | edsdoj.6c18d43ea82740d2ba2dfaab469d9927 |
| قاعدة البيانات: | Directory of Open Access Journals |
Full Text via ClinicalKey 
Full Text Finder | تدمد: | 1806907X |
|---|---|
| DOI: | 10.1016/j.bjane.2020.02.006 |