دورية أكاديمية
Cardiac involvement in children with neuro-muscular disorders
العنوان: | Cardiac involvement in children with neuro-muscular disorders |
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المؤلفون: | E. N. Arkhipova |
المصدر: | Нервно-мышечные болезни, Vol 5, Iss 4, Pp 10-15 (2015) |
بيانات النشر: | ABV-press, 2015. |
سنة النشر: | 2015 |
المجموعة: | LCC:Neurology. Diseases of the nervous system |
مصطلحات موضوعية: | нервно-мышечные болезни, мышечная дистрофия дюшенна, миотоническая дистрофия 1-го и 2-го типов, поясно-конечностная мышечная дистрофия, мышечная дистрофия эмери–дрейфуса, дилатационная кардиомиопатия, желудочковая аритмия, фибрилляция предсердия, нарушение атриовентрикулярной проводимости, нарушение внутрижелудочковой проводимости, внезапная кардиальная смерть, Neurology. Diseases of the nervous system, RC346-429 |
الوصف: | Many inherited neuromuscular disorders include cardiac involvement as a typical clinical feature. Among the most common of them is the group of muscular dystrophies. Dilated cardiomyopathy, ventricular arrhythmias, atrial fibrillations, atrioventricular and intraventricular conduction abnormalities, and sudden cardiac death are well known pathological findings in Duchenne muscular dystrophies, myotonic dystrophy type I and 2, Emery-Dreifuss muscular dystrophies and different types of limb-girdle muscular dystrophies and other disorders. Detection of cardiac pathology in patients with different muscular dystrophies is possible with ECG, echocardiography and cardiovascular magnetic resonance imaging, which are recommended for screening and early cardioprotective treatment. |
نوع الوثيقة: | article |
وصف الملف: | electronic resource |
اللغة: | Russian |
تدمد: | 2222-8721 2413-0443 |
Relation: | https://nmb.abvpress.ru/jour/article/view/127; https://doaj.org/toc/2222-8721; https://doaj.org/toc/2413-0443 |
DOI: | 10.17650/2222-8721-2015-5-4-10-15 |
URL الوصول: | https://doaj.org/article/720786215ec141a78b9cd643a04560a4 |
رقم الأكسشن: | edsdoj.720786215ec141a78b9cd643a04560a4 |
قاعدة البيانات: | Directory of Open Access Journals |
تدمد: | 22228721 24130443 |
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DOI: | 10.17650/2222-8721-2015-5-4-10-15 |