دورية أكاديمية
Left Ventricular Non-Compaction Spectrum in Adults and Children: From a Morphological Trait to a Structural Muscular Disease
العنوان: | Left Ventricular Non-Compaction Spectrum in Adults and Children: From a Morphological Trait to a Structural Muscular Disease |
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المؤلفون: | Flavia Fusco, Nunzia Borrelli, Rosaria Barracano, Giovanni Domenico Ciriello, Federica Verrillo, Giancarlo Scognamiglio, Berardo Sarubbi |
المصدر: | Cardiogenetics, Vol 12, Iss 2, Pp 170-184 (2022) |
بيانات النشر: | MDPI AG, 2022. |
سنة النشر: | 2022 |
المجموعة: | LCC:Diseases of the circulatory (Cardiovascular) system |
مصطلحات موضوعية: | left ventricular non-compaction, LVNC, hypertrabeculated left ventricle, cardiomyopathy, reversible, Diseases of the circulatory (Cardiovascular) system, RC666-701 |
الوصف: | Left ventricular non-compaction (LVNC) is an extremely heterogeneous disorder with a highly variable clinical presentation, morphologic appearance at imaging testing, and prognosis. It is still unclear whether LVNC should be classified as a separate cardiomyopathy or if it is a mere morphological trait shared by many phenotypically distinct cardiomyopathies. Moreover, the hypertrabeculated phenotype may be reversible in some cases, possibly reflecting the left ventricular physiological response of the cardiac muscle to chronic overload. The current diagnostic criteria have several limitations, leaving many patients in a grey area. Here, we review the available literature on LVNC in order to provide an overview of the current knowledge on this complex disorder. |
نوع الوثيقة: | article |
وصف الملف: | electronic resource |
اللغة: | English |
تدمد: | 2035-8148 2035-8253 |
Relation: | https://www.mdpi.com/2035-8148/12/2/16; https://doaj.org/toc/2035-8253; https://doaj.org/toc/2035-8148 |
DOI: | 10.3390/cardiogenetics12020016 |
URL الوصول: | https://doaj.org/article/c721133f872e4b5c917148ee65ec7e69 |
رقم الأكسشن: | edsdoj.721133f872e4b5c917148ee65ec7e69 |
قاعدة البيانات: | Directory of Open Access Journals |
تدمد: | 20358148 20358253 |
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DOI: | 10.3390/cardiogenetics12020016 |