دورية أكاديمية
Treatment of thrombotic thrombocytopenic purpura
العنوان: | Treatment of thrombotic thrombocytopenic purpura |
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المؤلفون: | Gennadii M. Galstyan, Alexei A. Maschan, Elizaveta E. Klebanova, Irina I. Kalinina |
المصدر: | Терапевтический архив, Vol 93, Iss 7, Pp 826-829 (2021) |
بيانات النشر: | "Consilium Medicum" Publishing house, 2021. |
سنة النشر: | 2021 |
المجموعة: | LCC:Medicine |
مصطلحات موضوعية: | adamts13, thrombotic thrombocytopenic purpura, upshaw–schulman syndrome, pregnancy, therapeutic plasma exchange, recombinant adamts13, Medicine |
الوصف: | The review discusses approaches to treatment of congenital thrombotic thrombocytopenic purpura (TTP) or Upshaw-Schulman syndrome. In congenital TTP, plasma transfusions are sufficient. Such treatment options as plasma exchange, administration of clotting factor VIII concentrate, recombinant ADAMTS13, are also used. Separately discussed issues of management of patients with TTP during pregnancy, and pediatric patients with TTP. |
نوع الوثيقة: | article |
وصف الملف: | electronic resource |
اللغة: | Russian |
تدمد: | 0040-3660 2309-5342 00403660 |
Relation: | https://ter-arkhiv.ru/0040-3660/article/viewFile/76363/56962; https://doaj.org/toc/0040-3660; https://doaj.org/toc/2309-5342 |
DOI: | 10.26442/00403660.2021.07.200914 |
URL الوصول: | https://doaj.org/article/a9298776924844eb84312f7678190568 |
رقم الأكسشن: | edsdoj.9298776924844eb84312f7678190568 |
قاعدة البيانات: | Directory of Open Access Journals |
تدمد: | 00403660 23095342 |
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DOI: | 10.26442/00403660.2021.07.200914 |