دورية أكاديمية

Severe cardiovascular system involvement in a patient with Marfan’s syndrome

التفاصيل البيبلوغرافية
العنوان: Severe cardiovascular system involvement in a patient with Marfan’s syndrome
المؤلفون: O. S. Groznova, E. P. Kalachanova, I. V. Leontyeva, P. E. Rzhevskaya
المصدر: Rossijskij Vestnik Perinatologii i Pediatrii, Vol 60, Iss 2, Pp 95-99 (2016)
بيانات النشر: Ltd. “The National Academy of Pediatric Science and Innovation”, 2016.
سنة النشر: 2016
المجموعة: LCC:Pediatrics
مصطلحات موضوعية: дети, синдром марфана, кардиомиопатия, аорта, лозартан, диагностика, лечение, Pediatrics, RJ1-570
الوصف: The given clinical case of a 14-year-old child with Marfan’s syndrome demonstrates the early severe cardiovascular system diseases, such as dilated cardiomyopathy and aortic root dilatation, that required surgical treatment when he was 9 years old, and grades 2 and 3 insufficiency of the mitral and aortic valves, respectively. The paper presents the modern view of the involvement of the heart and vessels in Marfan’s syndrome (cardiomyopathy as a new sign of the disease, arterial dissection). It shows new possibilities for treating cardiovascular disorders in children with this disease, such as pathogenetic therapy with losartan, anti-transforming growth factor-β antibodies.
نوع الوثيقة: article
وصف الملف: electronic resource
اللغة: Russian
تدمد: 1027-4065
2500-2228
Relation: https://www.ped-perinatology.ru/jour/article/view/107; https://doaj.org/toc/1027-4065; https://doaj.org/toc/2500-2228
URL الوصول: https://doaj.org/article/9971c3cf2ca2497687f02001737b8f56
رقم الأكسشن: edsdoj.9971c3cf2ca2497687f02001737b8f56
قاعدة البيانات: Directory of Open Access Journals