دورية أكاديمية
Severe cardiovascular system involvement in a patient with Marfan’s syndrome
العنوان: | Severe cardiovascular system involvement in a patient with Marfan’s syndrome |
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المؤلفون: | O. S. Groznova, E. P. Kalachanova, I. V. Leontyeva, P. E. Rzhevskaya |
المصدر: | Rossijskij Vestnik Perinatologii i Pediatrii, Vol 60, Iss 2, Pp 95-99 (2016) |
بيانات النشر: | Ltd. “The National Academy of Pediatric Science and Innovation”, 2016. |
سنة النشر: | 2016 |
المجموعة: | LCC:Pediatrics |
مصطلحات موضوعية: | дети, синдром марфана, кардиомиопатия, аорта, лозартан, диагностика, лечение, Pediatrics, RJ1-570 |
الوصف: | The given clinical case of a 14-year-old child with Marfan’s syndrome demonstrates the early severe cardiovascular system diseases, such as dilated cardiomyopathy and aortic root dilatation, that required surgical treatment when he was 9 years old, and grades 2 and 3 insufficiency of the mitral and aortic valves, respectively. The paper presents the modern view of the involvement of the heart and vessels in Marfan’s syndrome (cardiomyopathy as a new sign of the disease, arterial dissection). It shows new possibilities for treating cardiovascular disorders in children with this disease, such as pathogenetic therapy with losartan, anti-transforming growth factor-β antibodies. |
نوع الوثيقة: | article |
وصف الملف: | electronic resource |
اللغة: | Russian |
تدمد: | 1027-4065 2500-2228 |
Relation: | https://www.ped-perinatology.ru/jour/article/view/107; https://doaj.org/toc/1027-4065; https://doaj.org/toc/2500-2228 |
URL الوصول: | https://doaj.org/article/9971c3cf2ca2497687f02001737b8f56 |
رقم الأكسشن: | edsdoj.9971c3cf2ca2497687f02001737b8f56 |
قاعدة البيانات: | Directory of Open Access Journals |
تدمد: | 10274065 25002228 |
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