دورية أكاديمية
Surgical Management of Pachyonychia Congenita in a 3-Year-Old
| العنوان: | Surgical Management of Pachyonychia Congenita in a 3-Year-Old |
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| المؤلفون: | Jack D. Sudduth, Christopher Clinker, Matthew Holdaway, Jessica L. Marquez, Jacob Veith, Thomas Wright, W. Bradford Rockwell |
| المصدر: | Archives of Plastic Surgery, Vol 50, Iss 06, Pp 573-577 (2023) |
| بيانات النشر: | Thieme Medical Publishers, Inc., 2023. |
| سنة النشر: | 2023 |
| المجموعة: | LCC:Surgery |
| مصطلحات موضوعية: | pachyonychia congenita, germinal matrix excision, nail bed excision, surgical dermatology, congenital, Surgery, RD1-811 |
| الوصف: | Pachyonychia congenita is a rare genetic disorder characterized by hypertrophic nail plates, hyperkeratotic nail beds, and thickened hyponychium of the fingers and toes, impairing manual dexterity and resulting in poor aesthetics. The current body of literature describes various treatment modalities, but no singular approach has been defined as the gold standard. In this case, the authors employed different surgical techniques for treating pachyonychia congenita to evaluate the most effective approach. A 3-year-old boy presented with hypertrophic nail growth involving all digits of both hands and feet. Three surgical procedures were performed on the patient's fingers and toes using germinal matrix excision (GME) alone, GME plus partial sterile matrix excision (pSME), or GME plus complete sterile matrix excision (cSME). The digits treated with GME + cSME exhibited no recurrence of nail growth. Those treated with GME alone exhibited recurrence of hypertrophic nail growth, although their growth slowed. Excision of GME + cSME prevented recurrence of hypertrophic nails, while GME alone or with pSME led to slower-growing hypertrophic nails. Complete excision of the germinal and sterile matrices with skin graft closure may be a definitive treatment for pachyonychia congenita, but further studies are needed to validate these findings. |
| نوع الوثيقة: | article |
| وصف الملف: | electronic resource |
| اللغة: | English |
| تدمد: | 2234-6163 2234-6171 |
| Relation: | https://doaj.org/toc/2234-6163; https://doaj.org/toc/2234-6171 |
| DOI: | 10.1055/s-0043-1771520 |
| URL الوصول: | https://doaj.org/article/f0c0a7117e2640a3a895a6d7593c62bd |
| رقم الأكسشن: | edsdoj.f0c0a7117e2640a3a895a6d7593c62bd |
| قاعدة البيانات: | Directory of Open Access Journals |
Full Text Finder | تدمد: | 22346163 22346171 |
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| DOI: | 10.1055/s-0043-1771520 |