دورية أكاديمية
Pancreatic Agenesis with Congenital Diaphragmatic Hernia and Congenital Heart Disease: A Case Report
| العنوان: | Pancreatic Agenesis with Congenital Diaphragmatic Hernia and Congenital Heart Disease: A Case Report |
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| المؤلفون: | Atsushi Nakao, Tomohiro Takeda, Yoshiya Hisaeda, Atsushi Hirota, Syusuke Amagata, Yuko Sakurai, Tadashi Kawakami |
| المصدر: | American Journal of Perinatology Reports, Vol 03, Iss 02, Pp 119-122 (2013) |
| بيانات النشر: | Thieme Medical Publishers, Inc., 2013. |
| سنة النشر: | 2013 |
| المجموعة: | LCC:Gynecology and obstetrics |
| مصطلحات موضوعية: | pancreatic agenesis, congenital diaphragmatic hernia, congenital heart disease, therapy, Gynecology and obstetrics, RG1-991 |
| الوصف: | Abstract Pancreatic agenesis is a rare disease that causes neonatal diabetes mellitus and exocrine pancreatic insufficiency. We report the case of a very low birth weight infant with congenital diaphragmatic hernia, and congenital heart disease (ventricular septal defect and patent ductus arteriosus). Failure to gain weight, despite well-managed respiratory and heart failure, was improved by infusion of subcutaneous insulin, administration of pancreatic enzyme, and nutrition of medium-chain-triglyceride -enriched formula. This is the first case of pancreatic agenesis with both malformations where the patient is discharged from the hospital. Early diagnosis and adequate treatments to compensate pancreatic function may prevent mortality and improve growth. |
| نوع الوثيقة: | article |
| وصف الملف: | electronic resource |
| اللغة: | English |
| تدمد: | 2157-6998 2157-7005 |
| Relation: | https://doaj.org/toc/2157-6998; https://doaj.org/toc/2157-7005 |
| DOI: | 10.1055/s-0033-1353388 |
| URL الوصول: | https://doaj.org/article/feacb7371dae4cc0ac3db1390ca527d9 |
| رقم الأكسشن: | edsdoj.feacb7371dae4cc0ac3db1390ca527d9 |
| قاعدة البيانات: | Directory of Open Access Journals |
Full Text Finder | تدمد: | 21576998 21577005 |
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| DOI: | 10.1055/s-0033-1353388 |