دورية أكاديمية

L1077P CFTR pathogenic variant function rescue by Elexacaftor–Tezacaftor–Ivacaftor in cystic fibrosis patient-derived air–liquid interface (ALI) cultures and organoids: in vitro guided personalized therapy of non-F508del patients

التفاصيل البيبلوغرافية
العنوان: L1077P CFTR pathogenic variant function rescue by Elexacaftor–Tezacaftor–Ivacaftor in cystic fibrosis patient-derived air–liquid interface (ALI) cultures and organoids: in vitro guided personalized therapy of non-F508del patients
المؤلفون: Lo Cicero, Stefania, Castelli, Germana, Blaconà, Giovanna, Bruno, Sabina Maria, Sette, Giovanni, Pigliucci, Riccardo, Villella, Valeria RachelaAff3, Aff4, Esposito, SperanzaAff3, Aff4, Zollo, ImmacolataAff3, Aff4, Spadaro, Francesca, Maria, Ruggero DeAff6, Aff7, Biffoni, Mauro, Cimino, Giuseppe, Amato, FeliceAff3, Aff4, Lucarelli, MarcoAff2, Aff9, Eramo, AdrianaAff1, IDs12931023025160_cor16
المصدر: Respiratory Research. 24(1)
قاعدة البيانات: Springer Nature Journals
الوصف
تدمد:1465993X
DOI:10.1186/s12931-023-02516-0